Influence of ATM function on telomere metabolism (original) (raw)
- Original Paper
- Published: 27 November 1997
Oncogene volume 15, pages 2659–2665 (1997)Cite this article
Abstract
The ATM gene product, which is defective in the cancer-prone disorder ataxia telangiectasia, has been implicated in mitogenic signal transduction, chromosome condensation, meiotic recombination and cell cycle control. The ATM gene has homology with the TEL1 gene of yeast, mutations of which lead to shortened telomeres. To test the hypothesis that the ATM gene product is involved in telomere metabolism, we examined telomeric associations (TA), telomere length, and telomerase activity in human cells expressing either dominant-negative or complementing fragments of the ATM gene. The phenotype of RKO colorectal tumor cells expressing ATM fragments containing a leucine zipper (LZ) motif mimics that of ataxia telangiectasia (A-T) cells. These transfected RKO cells relative to transfected controls had a higher frequency of cells with TA and shortened telomeres, but no detectable change in telomerase activity. In addition, the percentage of cells with TA after gamma irradiation was higher in the transfected RKO cells with dominant negative activity of the ATM gene, compared to control cells. SV40 transformed fibroblasts derived from an A-T patient and transfected with a complementing carboxyl terminal kinase region of the ATM gene had a reduced frequency of cells with TA, with no effect on the telomere length or telomerase activity. The present studies using isogenic cells with manipulated ATM function demonstrate a role for the ATM gene product in telomere metabolism.
This is a preview of subscription content, access via your institution
Access options
Subscribe to this journal
Receive 50 print issues and online access
$259.00 per year
only $5.18 per issue
Buy this article
- Purchase on SpringerLink
- Instant access to full article PDF
Prices may be subject to local taxes which are calculated during checkout
Additional access options:
Similar content being viewed by others
Author information
Authors and Affiliations
- Center for Radiological Research, College of Physicians and Surgeons, Columbia University, New York, 10032, NY, USA
Lubomir B Smilenov, Satin G Sawant & Tej K Pandita - The Johns Hopkins Oncology Center, Baltimore, 21205, Maryland, USA
Susan E Morgan & Michael B Kastan
Authors
- Lubomir B Smilenov
You can also search for this author inPubMed Google Scholar - Susan E Morgan
You can also search for this author inPubMed Google Scholar - Satin G Sawant
You can also search for this author inPubMed Google Scholar - Michael B Kastan
You can also search for this author inPubMed Google Scholar - Tej K Pandita
You can also search for this author inPubMed Google Scholar
Rights and permissions
About this article
Cite this article
Smilenov, L., Morgan, S., Sawant, S. et al. Influence of ATM function on telomere metabolism.Oncogene 15, 2659–2665 (1997). https://doi.org/10.1038/sj.onc.1201449
- Received: 10 June 1997
- Revised: 23 July 1997
- Accepted: 24 July 1997
- Issue Date: 27 November 1997
- DOI: https://doi.org/10.1038/sj.onc.1201449
Keywords
This article is cited by
Telomeres and telomerase: three decades of progress
- Jerry W. Shay
- Woodring E. Wright
Nature Reviews Genetics (2019)
Genetic analyses of aplastic anemia and idiopathic pulmonary fibrosis patients with short telomeres, possible implication of DNA-repair genes
- Elena G. Arias-Salgado
- Eva Galvez
- Leandro Sastre
Orphanet Journal of Rare Diseases (2019)
Inflammation, a significant player of Ataxia–Telangiectasia pathogenesis?
- Majid Zaki-Dizaji
- Seyed Mohammad Akrami
- Asghar Aghamohammadi
Inflammation Research (2018)
DNA damage checkpoints in stem cells, ageing and cancer
- Tobias Sperka
- Jianwei Wang
- K. Lenhard Rudolph
Nature Reviews Molecular Cell Biology (2012)
From the Rarest to the Most Common: Insights from Progeroid Syndromes into Skin Cancer and Aging
- Brian C. Capell
- Brook E. Tlougan
- Seth J. Orlow
Journal of Investigative Dermatology (2009)