ICD-10-CM Diagnosis Code G90.09 - Other idiopathic peripheral autonomic neuropathy (original) (raw)
ICD List 2025-2026 Edition
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- 2026 ICD-10-CM Code G90.09
Other idiopathic peripheral autonomic neuropathy
ICD-10-CM Code:
G90.09
ICD-10 Code for:
Other idiopathic peripheral autonomic neuropathy
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:
G90.09 is a billable diagnosis code used to specify a medical diagnosis of other idiopathic peripheral autonomic neuropathy. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2025 through September 30, 2026.
- Code Information
- Approximate Synonyms
- Clinical Classification
- Clinical Information
- Tabular List of Diseases and Injuries
- Index to Diseases and Injuries References
- Convert to ICD-9 Code
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- Other Codes Used Similar Conditions
- Code History
- Diseases of the nervous system
G00–G99
The following list of clinical terms are approximate synonyms, alternative descriptions, or common phrases that might be used by patients, healthcare providers, or medical coders to describe the same condition. These synonyms and related diagnosis terms are often used when searching for an ICD-10 code, especially when the exact medical terminology is unclear. Whether you're looking for lay terms, similar diagnosis names, or common language alternatives, this list can help guide you to the correct ICD-10 classification.
- Familial visceral neuropathy
- Familial visceral neuropathy
- Idiopathic peripheral autonomic neuropathy
- Intestinal autonomic neuropathy
- Paralysis of cervical sympathetic trunk
- Paroxysmal extreme pain disorder
- Sphenopalatine neuralgia
- Visceral neuropathy and brain anomaly with facial dysmorphism and developmental delay syndrome
Clinical Classifications group individual ICD-10-CM diagnosis codes into broader, clinically meaningful categories. These categories help simplify complex data by organizing related conditions under common clinical themes.
They are especially useful for data analysis, reporting, and clinical decision-making. Even when diagnosis codes differ, similar conditions can be grouped together based on their clinical relevance. Each category is assigned a unique CCSR code that represents a specific clinical concept, often tied to a body system or medical specialty.
CCSR Code: NVS006
Inpatient Default: Y - Yes, default inpatient assignment for principal diagnosis or first-listed diagnosis.
Outpatient Default: Y - Yes, default outpatient assignment for principal diagnosis or first-listed diagnosis.
Paroxysmal Extreme Pain Disorder
a very rare, autosomal dominant inherited disorder caused by mutations in the scn9a gene. it is characterized by skin redness and flushing and attacks of severe pain. the pain attacks usually last seconds to minutes.
The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).
- - Bradycardia (sinoatrial) (sinus) (vagal) - R00.1
- - reflex - G90.09
- - Faciocephalalgia, autonomic - See Also: Neuropathy, peripheral, autonomic; - G90.09
- - Insufficiency, insufficient
- - idiopathic autonomic - G90.09
- - Neuralgia, neuralgic (acute) - M79.2
- - sphenopalatine (ganglion) - G90.09
- - Neuropathy, neuropathic - G62.9
- - peripheral (nerve) - See Also: Polyneuropathy; - G62.9
* - autonomic - G90.9
* - idiopathic - G90.09
- - peripheral (nerve) - See Also: Polyneuropathy; - G62.9
- - Paralysis, paralytic (complete) (incomplete) - G83.9
- - cervical
* - sympathetic - G90.09 - - sympathetic - G90.89
* - cervical - G90.09
- - cervical
- - Sphenopalatine ganglion neuralgia - G90.09
- - Syndrome - See Also: Disease;
- - Charcot-Weiss-Baker - G90.09
- - Hilger's - G90.09
- - Weiss-Baker - G90.09
- - Weiss-Baker syndrome - G90.09
References found for this diagnosis code in the External Cause of Injuries Index:
- Bradycardia(sinoatrial) (sinus) (vagal)
- reflex
- Faciocephalalgia, autonomic
- Insufficiency, insufficient
- idiopathic autonomic
- Neuralgia, neuralgic(acute)
- sphenopalatine (ganglion)
- Neuropathy, neuropathic
- peripheral (nerve)
- autonomic
- idiopathic
- autonomic
- peripheral (nerve)
- Paralysis, paralytic(complete) (incomplete)
- cervical
- sympathetic
- cervical
- Paralysis, paralytic(complete) (incomplete)
- sympathetic
- cervical
- sympathetic
- Sphenopalatine ganglion neuralgia
- Syndrome
- Charcot-Weiss-Baker
- Syndrome
- Hilger's
- Syndrome
- Weiss-Baker
- Weiss-Baker syndrome
Below are the ICD-9 codes that most closely match this ICD-10 code, based on the General Equivalence Mappings (GEMs). This ICD-10 to ICD-9 crosswalk tool is helpful for coders who need to reference legacy diagnosis codes for audits, historical claims, or approximate code comparisons.
ICD-9-CM: 337.00
Approximate Flag - The approximate mapping means this ICD-10 code does not have an exact ICD-9 equivalent. The matched code is the closest available option, but it may not fully capture the original diagnosis or clinical intent.
ICD-9-CM: 337.09
Approximate Flag - The approximate mapping means this ICD-10 code does not have an exact ICD-9 equivalent. The matched code is the closest available option, but it may not fully capture the original diagnosis or clinical intent.
Autonomic Nervous System Disorders
Your autonomic nervous system is the part of your nervous system that controls involuntary actions, such as the beating of your heart and the widening or narrowing of your blood vessels. When something goes wrong in this system, it can cause serious problems, including:
- Blood pressure problems
- Heart problems
- Trouble with breathing and swallowing
- Erectile dysfunction in men
Autonomic nervous system disorders can occur alone or as the result of another disease, such as Parkinson's disease, alcoholism and diabetes. Problems can affect either part of the system, as in complex regional pain syndromes, or all of the system. Some types are temporary, but many worsen over time. When they affect your breathing or heart function, these disorders can be life-threatening.
Some autonomic nervous system disorders get better when an underlying disease is treated. Often, however, there is no cure. In that case, the goal of treatment is to improve symptoms.
NIH: National Institute of Neurological Disorders and Stroke
FY 2026 - No Change, effective from 10/1/2025 through 9/30/2026
FY 2025 - No Change, effective from 10/1/2024 through 9/30/2025
FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.
