ICD-10-CM Diagnosis Code Q89.8 - Other specified congenital malformations (original) (raw)

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ICD List 2025-2026 Edition

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Other specified congenital malformations

ICD-10-CM Code:

Q89.8

ICD-10 Code for:

Other specified congenital malformations

Is Billable?

Not Valid for Submission

Chronic Condition Indicator: [1]

Chronic

Code Navigator:

Q89.8 is a non-specific and non-billable diagnosis code code, consider using a code with a higher level of specificity from the list below for a diagnosis of other specified congenital malformations. The code is not specific and is NOT valid for the year 2026 for the submission of HIPAA-covered transactions. Category or Header define the heading of a category of codes that may be further subdivided by the use of 4th, 5th, 6th or 7th characters.

Non-specific codes like Q89.8 require more digits to indicate the appropriate level of specificity. Consider using any of the following billable codes with a higher level of specificity when coding for other specified congenital malformations:

Use Q89.81 for Kabuki syndrome

Use Q89.89 for Other specified congenital malformations

  1. Code Information
  2. Specific Coding
  3. Clinical Classification
  4. Clinical Information
  5. Replaced Code
  6. Tabular List of Diseases and Injuries
  7. Convert to ICD-9 Code
  8. Patient Education
  9. Other Codes Used Similar Conditions
  10. Code History

Clinical Classifications group individual ICD-10-CM diagnosis codes into broader, clinically meaningful categories. These categories help simplify complex data by organizing related conditions under common clinical themes.

They are especially useful for data analysis, reporting, and clinical decision-making. Even when diagnosis codes differ, similar conditions can be grouped together based on their clinical relevance. Each category is assigned a unique CCSR code that represents a specific clinical concept, often tied to a body system or medical specialty.

CCSR Code: MAL010

Inpatient Default: Y - Yes, default inpatient assignment for principal diagnosis or first-listed diagnosis.

Outpatient Default: Y - Yes, default outpatient assignment for principal diagnosis or first-listed diagnosis.

a rare autosomal dominant syndrome caused by mutations in the col11a1, col11a2, and col2a1 genes which affect the production of type ii and xi collagen. it is characterized by a range of signs and symptoms including cleft palate, large tongue, small lower jaw, hearing loss, myopia, glaucoma, retinal detachment, skeletal, and joint abnormalities.

stickler syndrome inherited in an autosomal dominant pattern, caused by mutation(s) in the col2a1 gene, encoding collagen alpha-1(ii) chain.

a rare autosomal dominant syndrome caused by mutations in the col11a1 gene. it is characterized by an abnormal ocular vitreous architecture (beaded vitreous phenotype). other signs and symptoms include retinal detachment, joint hypermobility, hearing loss, and midline clefting.

This code was replaced in the 2026 ICD-10-CM code set with the code(s) listed below. The National Center for Health Statistics (NCHS) has published an update to the ICD-10-CM diagnosis codes which became effective October 1, 2025. This code was replaced for the FY 2026 (October 1, 2025 - September 30, 2026).

Below are the ICD-9 codes that most closely match this ICD-10 code, based on the General Equivalence Mappings (GEMs). This ICD-10 to ICD-9 crosswalk tool is helpful for coders who need to reference legacy diagnosis codes for audits, historical claims, or approximate code comparisons.

ICD-9-CM: 759.89

Approximate Flag - The approximate mapping means this ICD-10 code does not have an exact ICD-9 equivalent. The matched code is the closest available option, but it may not fully capture the original diagnosis or clinical intent.

Birth Defects

What are birth defects?

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

A birth defect may affect how the body looks, works, or both. Some birth defects like cleft lip or neural tube defects are structural problems that can be easy to see. Others, like heart disease, are found using special tests. Birth defects can range from mild to severe. How a birth defect affects a child's life depends mostly on which organ or body part is involved and how severe the defect is.

What causes birth defects?

For some birth defects, researchers know the cause. But for many birth defects, the exact cause is unknown. Researchers think that most birth defects are caused by a complex mix of factors, which can include:

Who is at risk of having a baby with birth defects?

Certain factors may increase the chances of having a baby with a birth defect, such as:

How are birth defects diagnosed?

Health care providers can diagnose some birth defects during pregnancy, using prenatal testing. That's why it important to get regular prenatal care.

Other birth defects may not be found until after the baby is born. Providers may find them through newborn screening. Some defects, such as club foot, are obvious right away. Other times, the health care provider may not discover a defect until later in life, when the child has symptoms.

What are the treatments for birth defects?

Children with birth defects often need special care and treatments. Because the symptoms and problems caused by birth defects vary, the treatments also vary. Possible treatments may include surgery, medicines, assistive devices, physical therapy, and speech therapy.

Often, children with birth defects need a variety of services and may need to see several specialists. The primary health care provider can coordinate the special care that the child needs.

Can birth defects be prevented?

Not all birth defects can be prevented. But there are things you can do before and during pregnancy to increase your chance of having a healthy baby:

Centers for Disease Control and Prevention

[Learn More in MedlinePlus]