Non-infantile variant of desmoplastic ganglioglioma: a report of 2 cases (original) (raw)

Abstract

Desmoplastic infantile gangliogliomas (DIGs) are uncommon supratentorial brain tumors with a usually good prognosis despite an aggressive radiological appearance. These tumors form part of a spectrum of desmoplastic infantile tumors that includes desmoplastic infantile astrocytomas. DIGs are classified as benign WHO grade I tumors of infancy. Non-infantile variants of this biologically benign intracranial neoplasm are rare, with only four previous case reports in the literature. We report two cases of non-infantile DIG diagnosed at our institution on the basis of clinical features, radiological appearance and histological findings.

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Editorial note added in proof.

In addition to the following list of references, authors are also referred to: Kesavadas C, Sonwalker H, Thomas B, et al. (2005) Atypical MRI appearance of desmoplastic infantile ganglioglioma. Pediatr Radiol 35:1024–1026

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Authors and Affiliations

  1. Department of CT and MRI, Jaslok Hospital and Research Centre, 15, Dr. G. Deshmukh Marg, Mumbai 400026, Maharashtra, India
    Karthik Ganesan & Shrinivas Desai
  2. Department of Neurology, Jaslok Hospital and Research Centre, Maharashtra, India
    Anaita Udwadia-Hegde

Authors

  1. Karthik Ganesan
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  2. Shrinivas Desai
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  3. Anaita Udwadia-Hegde
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Correspondence toKarthik Ganesan.

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Ganesan, K., Desai, S. & Udwadia-Hegde, A. Non-infantile variant of desmoplastic ganglioglioma: a report of 2 cases.Pediatr Radiol 36, 541–545 (2006). https://doi.org/10.1007/s00247-005-0095-9

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