A controlled trial of long-term inhaled hypertonic saline in patients with cystic fibrosis - PubMed (original) (raw)
Randomized Controlled Trial
. 2006 Jan 19;354(3):229-40.
doi: 10.1056/NEJMoa043900.
Affiliations
- PMID: 16421364
- DOI: 10.1056/NEJMoa043900
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Randomized Controlled Trial
A controlled trial of long-term inhaled hypertonic saline in patients with cystic fibrosis
Mark R Elkins et al. N Engl J Med. 2006.
Free article
Abstract
Background: Inhaled hypertonic saline acutely increases mucociliary clearance and, in short-term trials, improves lung function in people with cystic fibrosis. We tested the safety and efficacy of inhaled hypertonic saline in a long-term trial.
Methods: In this double-blind, parallel-group trial, 164 patients with stable cystic fibrosis who were at least six years old were randomly assigned to inhale 4 ml of either 7 percent hypertonic saline or 0.9 percent (control) saline twice daily for 48 weeks, with quinine sulfate (0.25 mg per milliliter) added to each solution to mask the taste. A bronchodilator was given before each dose, and other standard therapies were continued during the trial.
Results: The primary outcome measure, the rate of change (slope) in lung function (reflected by the forced vital capacity [FVC], forced expiratory volume in one second [FEV1], and forced expiratory flow at 25 to 75 percent of FVC [FEF25-75]) during the 48 weeks of treatment, did not differ significantly between groups (P=0.79). However, the absolute difference in lung function between groups was significant (P=0.03) when averaged across all post-randomization visits in the 48-week treatment period. As compared with the control group, the hypertonic-saline group had significantly higher FVC (by 82 ml; 95 percent confidence interval, 12 to 153) and FEV1 (by 68 ml; 95 percent confidence interval, 3 to 132) values, but similar FEF25-75 values. The hypertonic-saline group also had significantly fewer pulmonary exacerbations (relative reduction, 56 percent; P=0.02) and a significantly higher percentage of patients without exacerbations (76 percent, as compared with 62 percent in the control group; P=0.03). Hypertonic saline was not associated with worsening bacterial infection or inflammation.
Conclusions: Hypertonic saline preceded by a bronchodilator is an inexpensive, safe, and effective additional therapy for patients with cystic fibrosis. (ClinicalTrials.gov number, NCT00271310.)
Copyright 2006 Massachusetts Medical Society.
Comment in
- Restoring airway surface liquid in cystic fibrosis.
Ratjen F. Ratjen F. N Engl J Med. 2006 Jan 19;354(3):291-3. doi: 10.1056/NEJMe058293. N Engl J Med. 2006. PMID: 16421371 No abstract available. - Hypertonic saline for cystic fibrosis.
Aziz I, Kastelik JA. Aziz I, et al. N Engl J Med. 2006 Apr 27;354(17):1848-51; author reply 1848-51. doi: 10.1056/NEJMc060351. N Engl J Med. 2006. PMID: 16641405 No abstract available. - Hypertonic saline for cystic fibrosis.
Kuver R, Lee SP. Kuver R, et al. N Engl J Med. 2006 Apr 27;354(17):1848-51; author reply 1848-51. N Engl J Med. 2006. PMID: 16642591 No abstract available. - Inhaled hypertonic saline produces small increases in lung function in patients with cystic fibrosis.
Ratjen F. Ratjen F. J Pediatr. 2006 Jul;149(1):142. doi: 10.1016/j.jpeds.2006.04.030. J Pediatr. 2006. PMID: 17243308 No abstract available.
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