The utility of cortical-sparing adrenalectomy in pheochromocytomas associated with genetic syndromes - PubMed (original) (raw)
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The utility of cortical-sparing adrenalectomy in pheochromocytomas associated with genetic syndromes
Sara C Fallon et al. J Pediatr Surg. 2013 Jun.
Abstract
Management of pediatric patients with pheochromocytomas associated with genetic syndromes, such as Von Hippel-Lindau (VHL) disease, is complex owing to the need for continuous surveillance, high rates of recurrence, multiple operations during childhood, and the possibility of lifelong exogenous steroid replacement. We report the successful treatment of two siblings with VHL who underwent a total of six cortical-sparing procedures without requiring steroid therapy.
Keywords: Adrenal Tumors; Pediatrics; Pheochromocytoma; Von Hippel Lindau.
Copyright © 2013 Elsevier Inc. All rights reserved.
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