Variability of diagnostic criteria and treatment of idiopathic nephrotic syndrome across European countries - PubMed (original) (raw)
Multicenter Study
. 2017 May;176(5):647-654.
doi: 10.1007/s00431-017-2891-2. Epub 2017 Mar 16.
Collaborators, Affiliations
- PMID: 28303389
- DOI: 10.1007/s00431-017-2891-2
Free article
Multicenter Study
Variability of diagnostic criteria and treatment of idiopathic nephrotic syndrome across European countries
Georges Deschênes et al. Eur J Pediatr. 2017 May.
Free article
Abstract
The aim of the surveys conducted by the Idiopathic Nephrotic Syndrome Working Group of the ESPN was to study the possible variability of treatment in Europe at different stages of the disease by means of questionnaires sent to members of the Working Group. Four surveys have been completed: treatment of the first flare, treatment of the first relapse and the issue of steroid dependency, use of rituximab, and the management of steroid-resistant patients. A uniform treatment of the first flare was applied in only three countries, and ten additional centers have adopted one of the three main protocols. Reported treatment of the first relapse was relatively uniform, whereas the use of additional immunosuppressants in steroid dependency was widely variable. Rituximab had already been used in hundreds of patients, although the formal evidence of efficiency in steroid dependency was relatively recent at the time of the survey. The definition of steroid resistance was variable in the European centers, but strikingly, the first-line treatment was uniform throughout the centers and included the combination of prednisone plus calcineurin antagonists.
Conclusion: The variability in the approach of idiopathic nephrotic syndrome is unexpectedly large and affects treatment of the first flare, strategies in the case of steroid dependency, as well as the definitions of steroid resistance. What is Known: • Steroids and immunosuppressants are the universal treatment of idiopathic nephrotic syndrome. What is New: • The variability of treatments and strategy of treatment in European centers of pediatric nephrology.
Keywords: Guidelines; Prednisone; Proteinuria; Rituximab; Steroid dependency; Steroid resistance.
Similar articles
- Risk factors for relapse and long-term outcome in steroid-dependent nephrotic syndrome treated with rituximab.
Kamei K, Ogura M, Sato M, Sako M, Iijima K, Ito S. Kamei K, et al. Pediatr Nephrol. 2016 Jan;31(1):89-95. doi: 10.1007/s00467-015-3197-0. Epub 2015 Sep 4. Pediatr Nephrol. 2016. PMID: 26341251 - Rituximab is a safe and effective long-term treatment for children with steroid and calcineurin inhibitor-dependent idiopathic nephrotic syndrome.
Ravani P, Ponticelli A, Siciliano C, Fornoni A, Magnasco A, Sica F, Bodria M, Caridi G, Wei C, Belingheri M, Ghio L, Merscher-Gomez S, Edefonti A, Pasini A, Montini G, Murtas C, Wang X, Muruve D, Vaglio A, Martorana D, Pani A, Scolari F, Reiser J, Ghiggeri GM. Ravani P, et al. Kidney Int. 2013 Nov;84(5):1025-33. doi: 10.1038/ki.2013.211. Epub 2013 Jun 5. Kidney Int. 2013. PMID: 23739238 Free PMC article. - Treating the idiopathic nephrotic syndrome: are steroids the answer?
Deschênes G, Dossier C, Hogan J. Deschênes G, et al. Pediatr Nephrol. 2019 May;34(5):777-785. doi: 10.1007/s00467-018-3963-x. Epub 2018 Jun 4. Pediatr Nephrol. 2019. PMID: 29869116 Review. - [Multicenter survey of diagnostic and therapeutic status in Chinese childhood patients with steroid-sensitive, relaping/steroid-dependent nephrotic syndrome].
Working Group For National Survey On Status Of Diagnosis And Treatment Of Childhood Renal Diseases. Working Group For National Survey On Status Of Diagnosis And Treatment Of Childhood Renal Diseases. Zhonghua Er Ke Za Zhi. 2014 Mar;52(3):194-200. Zhonghua Er Ke Za Zhi. 2014. PMID: 24824389 Chinese. - New treatment strategies in idiopathic nephrotic syndrome.
Ulinski T, Aoun B. Ulinski T, et al. Minerva Pediatr. 2012 Apr;64(2):135-43. Minerva Pediatr. 2012. PMID: 22495188 Review.
Cited by
- Rituximab therapy for childhood onset idiopathic nephrotic syndrome: experience of a Portuguese tertiary center.
Gomes R, Mosca S, Bastos-Gomes M, Correia-Costa L, Rocha L, Teixeira A, Costa T, Sameiro-Faria M, Matos P, Mota C. Gomes R, et al. J Bras Nefrol. 2023 Jul-Sep;45(3):326-334. doi: 10.1590/2175-8239-JBN-2022-0056en. J Bras Nefrol. 2023. PMID: 36259942 Free PMC article. - Commentary on "Pediatric Idiopathic Steroid-sensitive Nephrotic Syndrome Diagnosis and Therapy - Short version of the updated German Best Practice Guideline (S2e)".
Ehren R, Benz MR, Brinkkötter PT, Dötsch J, Eberl WR, Gellermann J, Hoyer PF, Jordans I, Kamrath C, Kemper MJ, Latta K, Müller D, Oh J, Tönshoff B, Weber S, Weber LT; German Society for Pediatric Nephrology. Ehren R, et al. Pediatr Nephrol. 2021 Oct;36(10):2961-2966. doi: 10.1007/s00467-021-05136-2. Epub 2021 Jun 5. Pediatr Nephrol. 2021. PMID: 34091755 Free PMC article. No abstract available. - Steroid treatment for the first episode of childhood nephrotic syndrome: comparison of the 8 and 12 weeks regimen using an individual patient data meta-analysis.
Schijvens AM, Teeninga N, Dorresteijn EM, Teerenstra S, Webb NJ, Schreuder MF. Schijvens AM, et al. Eur J Pediatr. 2021 Sep;180(9):2849-2859. doi: 10.1007/s00431-021-04035-w. Epub 2021 Mar 28. Eur J Pediatr. 2021. PMID: 33774744 Free PMC article. - Update on the treatment of steroid-sensitive nephrotic syndrome.
Zotta F, Vivarelli M, Emma F. Zotta F, et al. Pediatr Nephrol. 2022 Feb;37(2):303-314. doi: 10.1007/s00467-021-04983-3. Epub 2021 Mar 5. Pediatr Nephrol. 2022. PMID: 33665752 Review. - Optimizing the corticosteroid dose in steroid-sensitive nephrotic syndrome.
Christian MT, Maxted AP. Christian MT, et al. Pediatr Nephrol. 2022 Jan;37(1):37-47. doi: 10.1007/s00467-021-04985-1. Epub 2021 Feb 20. Pediatr Nephrol. 2022. PMID: 33611671 Free PMC article. Review.
References
- Cochrane Database Syst Rev. 2007 Oct 17;(4):CD001533 - PubMed
- Am J Kidney Dis. 2003 Jun;41(6):1155-62 - PubMed
- J Bras Nefrol. 2013 Jul-Sep;35(3):191-9 - PubMed
- Pediatr Nephrol. 2011 Aug;26(8):1241-6 - PubMed
- Nephrol Ther. 2005 Jul;1(3):150-6 - PubMed
Publication types
MeSH terms
Substances
LinkOut - more resources
Full Text Sources
Other Literature Sources
Medical