maciej karolczak | Medical University of Warsaw (original) (raw)

Papers by maciej karolczak

Research paper thumbnail of Analysis of selected risk factors for pulmonary complications in infants after cardiac surgery procedures Analiza wybranych czynników ryzyka powikłań płucnych u niemowląt po operacjach kardiochirurgicznych

BACKGROUND Postoperative disorders of the respiratory system in infants after cardiac surgical pr... more BACKGROUND Postoperative disorders of the respiratory system in infants after cardiac surgical procedures entail significant clinical problems, both because they are life threatening and due to their potential adverse effect on the final outcome of the treatment. The main causes of postoperative complications include significant changes in the vascular system, intrathoracic manipulation, potentially leading to the damage of anatomical structures, drainage of the pleural cavities, postoperative immobilization, mechanical respiration and post-perfusion syndrome. The basic clinical symptoms include changes in the pulmonary parenchyma and fluid in the pleural space. The identification of the type of changes and the risk factors related to postoperative pulmonary complications enables optimal adjustment of postoperative care strategies, including directed respiratory physiotherapy[1, 9]. The aim of the study was to identify the most common respiratory complications in patients after pediatric cardiac surgical procedures, to carry out a separate analysis of the group of infants with heart defects associated with Down syndrome and to evaluate the effect of extracorporeal circulation (ECC) time and aortic cross-clamp (ACC) time on pulmonary complications.

Research paper thumbnail of Editorial Comment on: H. Moczulska, K. Janiak, M. Słodki and M. Respondek-Liberska Ultrasound and echocardiographic findings obtained in the second and third trimesters of gestation in fetuses with normal karyotype and increased nuchal translucency

Journal of Ultrasonography, 2013

Non-invasive ultrasound examinations play a vital role in pregnancy care. Thanks to ultrasound sc... more Non-invasive ultrasound examinations play a vital role in pregnancy care. Thanks to ultrasound scanning, the detectability of developmental defects keeps improving but the assessment of the cardiovascular system still poses a challenge for obstetricians. The article by Moczulska et al. concerns one of the most urgent issues in prenatal care, i.e. searching for methods of early, reliable and non-invasive detection of fetal anomalies that are safe for the fetus(1).

Research paper thumbnail of Mixed partial anomalous pulmonary venous drainage coexistent with an aortic valve abnormality – analysis of ultrasound diagnostics in a 10-year-old girl with Turner syndrome

Journal of Ultrasonography, 2014

The authors present a case of echocardiographic diagnosis of a rare congenital cardiovascular ano... more The authors present a case of echocardiographic diagnosis of a rare congenital cardiovascular anomaly in the form of mixed partial anomalous pulmonary veins connection in a 10-year-old girl with Turner syndrome and congenital mild stenosis of insufficient bicuspid aortic valve, made while diagnosing the causes of intestinal tract bleeding. The article presents various diagnostic difficulties leading to the delayed determination of a correct diagnosis, resulting from the absence of symptoms of circulatory failure in the early stage of the disease and the occurrence of severe and dominant auscultatory phenomena typical for congenital aortic valve defect which effectively masked the syndromes of increased pulmonary flow. The authors discuss the role of the impact of phenotypic characteristics of the Turner syndrome, in particular a short webbed neck restricting the suprasternal echocardiographic access and the presence of psychological factors associated with a long-term illness. The i...

Research paper thumbnail of Intraoperative Macroscopic Lung Appearance in Premature Infants with Body Weights Less than 1000 G Undergoing Surgical Treatment for PDA

Polish Journal of Surgery, 2007

The aim of the study was to assess the relationship between intraoperatively observed macroscopic... more The aim of the study was to assess the relationship between intraoperatively observed macroscopic pathologic findings in the left lung and the chosen clinical factors. The factors analyzed in the study were the following: neonatal gestational age and body weight, the age of the neonate at the time of surgery, the history of intrauterine infection and/or presence of active infection in the neonate, the history of ibuprofen treatment, and intraoperative diameter of the arterial duct. Material and methods. The authors included a group of 126 preterm infants with body weight less than 1000 g undergoing surgical treatment for PDA in the 2 nd Department of Cardiac and General Pediatric Surgery between January 2000 and May 2006 and analyzed the macroscopic intraoperative left lung appearance. The average body weight of the neonates who participated in the study was 765.2 g, with the average gestational age 25.68 Hbd. According to the results of intraoperative macroscopic lung assessment, the neonates were classified into one of the following three groups: 0-normal lungs or partially stiff lungs with emphysema focuses, 1-limited macroscopic findings, focuses of limited atelectasis, lung congestion, 2-severe pathologic findings in the pulmonary tissue, pulmonary hematomas, bleeding pulmonary surface, disseminated atelectasis, liver-like pulmonary tissue. In the study, the statistical analysis of the relationship between pathological pulmonary findings (groups 0, 1, 2) and investigated factors was performed by the comparison of mean values (or median) of the investigated factor in the analyzed groups. The Kruskal-Wallis and the Mann-Whitney tests were used dependent of the analyzed factor. Additionally, for chosen factors (the infection presence and PDA diameter), their relationship with the lung macroscopic appearance was assessed with the use of the Spearman test. Results. The pathological findings in the lungs were observed in the majority of the neonates (54%). The statistical analysis did not show any relationship between the pulmonary disorders and the majority of investigated factors. Conclusions. 1. The authors found that a duct diameter of ³ 4 mm correlates with the development of more severe disorders in the pulmonary tissue. 2. The authors emphasized the good results of surgical treatment of PDA and the lack of death in the perioperative period in that group of patients.

Research paper thumbnail of Zwiotczenie prawej kopuły przepony i zespół wad wrodzonych serca u niemowlęcia z delecją terminalną 8p23.1

Research paper thumbnail of Zespół wad wrodzonych ze złożoną wadą serca i zaburzeniami krzepnięcia sugerujący spektrum oczno-uszno-kręgowe – opis przypadku

Pediatria Polska, 2015

Abstract Oculo-auriculo-vertebral spectrum (OAVS) is a multisystem developmental anomaly that aff... more Abstract Oculo-auriculo-vertebral spectrum (OAVS) is a multisystem developmental anomaly that affects one in every 5600–26,500 births. The case of a 13-month-old girl with typical symptoms of OAVS and successfully corrected coexistent double outlet right ventricle with outflow tract obstruction is presented. Additionally deficit of VII, IX and XII coagulation factors was diagnosed prior to surgery as well as hemiparesis, right kidney agenesis and cleft palate. The authors stress the need for detailed and extended coagulologic laboratory examinations to precisely calculate operative risk and to establish appropriate therapeutic protocol.

Research paper thumbnail of Cervical Thymic Cyst

Polish Journal of Surgery, 2007

Kierownik: prof. dr hab. M. A. Karolczak The Authors of this study present a case of a 13-month o... more Kierownik: prof. dr hab. M. A. Karolczak The Authors of this study present a case of a 13-month old child subjected to surgical intervention for a cervical thymic cyst. The origin of lesions in children is usually associated with remnants from the development of the fetal thymus gland. When the tumor attains significant size, especially in the presence of clinical symptoms, such as respiratory disturbances and problems with feeding, surgical management is required. In spite of the rarity of thymic cysts, it should be considered in cases of differential diagnosis for neck tumors in children. Proper diagnosis is usually possible after the histopathological evaluation of removed tissues. The cervical approach enables removal of the entire lesion, even if partially localized in the thoracic cavity.

Research paper thumbnail of Right-sided intrathoracic bypass graft for complex or recurrent coarctation of the aorta

European Journal of Cardio-Thoracic Surgery, 1989

A simple technique is described for the interposition of a tube graft between the ascending and d... more A simple technique is described for the interposition of a tube graft between the ascending and descending aorta in the right chest. Directing the graft posteriorly preserves the integrity of the pericardium and avoids potential damage to the prosthesis at a subsequent sternotomy for open heart surgery. This procedure was used successfully and without complication in an 18-month-old boy who had undergone two previous operations for coarctation of the aorta, and in a 20-year-old girl with William's syndrome and diffuse hypoplasia of the distal aortic arch.

Research paper thumbnail of Efficacy and safety of surgical treatment of PDA in VLBW neonates. Warsaw region multicenter collaboration

Early Human Development, 2008

Background and aim Purpose: to evaluate the value of echocardiographic exam for the diagnosis and... more Background and aim Purpose: to evaluate the value of echocardiographic exam for the diagnosis and follow up of perinatal posthypoxic myocardial injury in the newborn infant. Materials and methods Methods. Patients: 92 newborns aged 0 to 14 days, with normal birth weight, hospitalised in Neonatology Intensive Care of the Cuza Voda Maternity Iasi, with perinatal hypoxia and Apgar score 3-7 and receiving resuscitation. The patients were without major congenital heart defects. In all cases were performed: clinical exam, ECG, chest X-ray (Rx.CT), Doppler echocardiographic exam (Echo). Most of our patients were treated with spironolactone 1 mg/kg/day for 3-5 months and evaluated clinically and echo after 6 months. Results The patients had mainly signs of neurological post hypoxic suffering, without signs of severe cardiac involvement. The cardiac examination revealed: systolic murmur (78 cases) and signs of persistent pulmonary hypertension of newborn (PPHN) in 12 cases. Chest X-ray: cardiomegaly (41 cases). ECG: severe left ventricle (LV) repolarization disturbances and low voltage of QRS complexes (47 cases), without ischemic changes. Doppler echo exam performed at 2-7 days of life revealed: ⁎ the absence of other severe congenital cardiac anomaly; ⁎permeability of foramen ovalae (100% cases) to the forced foramen ovalae (gradient LA/RA > 8 mmHg); ⁎myocardial hypertrophy (62 cases) mainly interventricular septal (48 cases), signs of PPHN(12 cases) with mild to severe tricuspid insufficiency(48 cases) and right atrium dilation (31 cases); prolonged isovolumic relaxation period (35 cases), increased the values of myocardial performance index (49 cases), the systolic function normal (all cases) and severe LV diastolic dysfunction (E/A < 1) in 51 cases. Reevaluation at 6 months showed the reduction of the myocardial hypertrophy and of the tricuspid regurgitation, with a normal LV diastolic function. Conclusions The severe perinatal hypoxia can induce the apparition of a true posthypoxic cardiomypathy at more than 70% of patients, the signs of cardiovascular suffering missing often. Echocardiography is the main method for diagnosis and follow up of perinatal hypoxic cardiomyopathy and is necessary from the first week of life.

Research paper thumbnail of Staged and primary Yasui repair in infants with interrupted aortic arch

Research paper thumbnail of Wady wrodzone Unusual presentation of the right atrial thrombus formation in a child with acute lymphoblastic leukaemia: a case report

Research paper thumbnail of WADY WRODZONE Cor triatriatum sinister with partially anomalous left pulmonary

Research paper thumbnail of Repair of common arterial trunk type I after previous pulmonary artery banding: technical considerations

Omówiono wybrane aspekty operacji wspólnego pnia tętniczego typu I u niemowląt po uprzednim bandi... more Omówiono wybrane aspekty operacji wspólnego pnia tętniczego typu I u niemowląt po uprzednim bandingu pnia płucnego, koncentrując się na wykorzystaniu metody analogicznej do stosowanej w korekcji okienka aortalno-płucnego. Technika ta jako warta rozważenia alternatywa dla odcięcia pnia płucnego i rekonstrukcji ściany neoaorty została przez autorów szczegółowo opisana oraz zilustrowana. Słowa kluczowe: wspólny pień tętniczy, banding tętnicy płucnej. Summary

Research paper thumbnail of Cor triatriatum dexter with underdevelopment of the right ventricle– case report

... Obliteracja balonem otworu międzyprzedsionkowego może być metodą rozstrzygającą w procesie kw... more ... Obliteracja balonem otworu międzyprzedsionkowego może być metodą rozstrzygającą w procesie kwalifikowania do operacji kardiochirurgicznej. Piśmiennictwo. 1. Joe BN, Poustchi-Amin M,Woodard PK. Case 56: cor triatriatum dexter. Radiology 2003; 226: 701-705. ...

Research paper thumbnail of WADY WRODZONE Removal of an unstable Amplatzer occluder and surgical closure of ASD in a 10-year old girl – a case report

... Jacek Wieteska, Maciej Karolczak, Bożena Werner, Krzysztof Godlewski. ... nowego typu implant... more ... Jacek Wieteska, Maciej Karolczak, Bożena Werner, Krzysztof Godlewski. ... nowego typu implantu Amplatzera (AGA Medical Carporation, Golden Valley, Minnesota, USA) poprawiło wyniki leczenia i zmniejszyło liczbę powikłań [1]. Ostatnie doniesienia potwierdzają również dużą ...

Research paper thumbnail of WADY WRODZONE Anomalous low insertion of superior vena cava into right atrium in infant with partial anomalous drainage of left pulmonary veins

Anomalies of the localization of the upper cavoatrial junction are extremely rare. We present the... more Anomalies of the localization of the upper cavoatrial junction are extremely rare. We present the case of 9 months old boy with low insertion of superior vena cava to right atrium and coexistent partial anomalous drainage of left pulmonary veins.

Research paper thumbnail of Double-chambered right ventricle in a 16-year-old patient with Williams syndrome

Journal of Ultrasonography

We present a case of double-chambered right ventricle diagnosed during preparation for colonoscop... more We present a case of double-chambered right ventricle diagnosed during preparation for colonoscopy due to gastrointestinal bleeding in a 16-year-old, mentally disabled boy with Williams syndrome. The patient was previously diagnosed with ventricular septal defect and mild pulmonary stenosis. Echocardiography performed under general anesthesia revealed hypertrophied muscular bundles in the right ventricle with the maximum gradient of 100 mmHg, causing severe outflow obstruction. This type of defect is extremely rare in patients with Williams syndrome, with only one case, which was diagnosed during invasive angiocardiography, described in world literature. A successful total surgical correction was performed based on echocardiography data.

Research paper thumbnail of Coronary steal phenomenon following right ventricle decompression and revascularization of atretic left coronary ostium: case report

Journal of Cardiothoracic Surgery

Background Coronary steal phenomenon and myocardial ischemia is a complication following decompre... more Background Coronary steal phenomenon and myocardial ischemia is a complication following decompression of a hypertensive right ventricle in patients with left coronary-cameral fistulae. Case presentation We present a 12-year-old girl with a complex heart defect successfully operated on using a hybrid surgical-interventional approach to decompress the ventricle, embolize the fistula and reconstruct the atretic left coronary ostium. Conclusions A novel hybrid strategy is the best solution for coronary-cameral fistulas reliant on high ventricular pressure at high risk for coronary steal phenomenon.

Research paper thumbnail of Late diagnosis of total anomalous pulmonary venous drainage in a 5.5-month-old infant

Journal of Ultrasonography, Apr 3, 2019

Background Total anomalous pulmonary venous drainage (TAPVD) is a cyanotic heart defect. TAPVD ac... more Background Total anomalous pulmonary venous drainage (TAPVD) is a cyanotic heart defect. TAPVD accounts for around 1.5% of all congenital heart defects (1) (1:10 000 live births (2)). Depending on morphological variants of the pulmonary venous drainage to the heart, four types of the defect may be distinguished: supracardiac (the most common, around 45% of reported cases (1,3)), intracardiac, infracardiac and mixed. Cyanosis, which accompanies TAPVD, depends on the effectiveness of the collateral circulation, the diameter of the pulmonary veins and the vertical vein, as well as the size of the coexistent atrial septal defect (ASD) (the only way by which oxygenated blood can reach the left atrium). Signs and symptoms typically exacerbate during physical exercise. About 80% of patients with TAPVD die within the first year of life (1,4,5) if untreated, although the literature mentions oligosymptomatic cases with long-term survival (1,4,6). Common symptoms of TAPVD include shortness of breath, cyanosis, fatigue, somnolence and no weight gain. An open-heart surgery should be performed immediately after the diagnosis in the neonatal period (5) .

Research paper thumbnail of Non-invasive diagnosis of aortic arch anomalies in children – 15 years of own experience

Journal of Ultrasonography, Apr 3, 2019

Non-invasive diagnosis of aortic arch anomalies in children-15 years of own experience

Research paper thumbnail of Analysis of selected risk factors for pulmonary complications in infants after cardiac surgery procedures Analiza wybranych czynników ryzyka powikłań płucnych u niemowląt po operacjach kardiochirurgicznych

BACKGROUND Postoperative disorders of the respiratory system in infants after cardiac surgical pr... more BACKGROUND Postoperative disorders of the respiratory system in infants after cardiac surgical procedures entail significant clinical problems, both because they are life threatening and due to their potential adverse effect on the final outcome of the treatment. The main causes of postoperative complications include significant changes in the vascular system, intrathoracic manipulation, potentially leading to the damage of anatomical structures, drainage of the pleural cavities, postoperative immobilization, mechanical respiration and post-perfusion syndrome. The basic clinical symptoms include changes in the pulmonary parenchyma and fluid in the pleural space. The identification of the type of changes and the risk factors related to postoperative pulmonary complications enables optimal adjustment of postoperative care strategies, including directed respiratory physiotherapy[1, 9]. The aim of the study was to identify the most common respiratory complications in patients after pediatric cardiac surgical procedures, to carry out a separate analysis of the group of infants with heart defects associated with Down syndrome and to evaluate the effect of extracorporeal circulation (ECC) time and aortic cross-clamp (ACC) time on pulmonary complications.

Research paper thumbnail of Editorial Comment on: H. Moczulska, K. Janiak, M. Słodki and M. Respondek-Liberska Ultrasound and echocardiographic findings obtained in the second and third trimesters of gestation in fetuses with normal karyotype and increased nuchal translucency

Journal of Ultrasonography, 2013

Non-invasive ultrasound examinations play a vital role in pregnancy care. Thanks to ultrasound sc... more Non-invasive ultrasound examinations play a vital role in pregnancy care. Thanks to ultrasound scanning, the detectability of developmental defects keeps improving but the assessment of the cardiovascular system still poses a challenge for obstetricians. The article by Moczulska et al. concerns one of the most urgent issues in prenatal care, i.e. searching for methods of early, reliable and non-invasive detection of fetal anomalies that are safe for the fetus(1).

Research paper thumbnail of Mixed partial anomalous pulmonary venous drainage coexistent with an aortic valve abnormality – analysis of ultrasound diagnostics in a 10-year-old girl with Turner syndrome

Journal of Ultrasonography, 2014

The authors present a case of echocardiographic diagnosis of a rare congenital cardiovascular ano... more The authors present a case of echocardiographic diagnosis of a rare congenital cardiovascular anomaly in the form of mixed partial anomalous pulmonary veins connection in a 10-year-old girl with Turner syndrome and congenital mild stenosis of insufficient bicuspid aortic valve, made while diagnosing the causes of intestinal tract bleeding. The article presents various diagnostic difficulties leading to the delayed determination of a correct diagnosis, resulting from the absence of symptoms of circulatory failure in the early stage of the disease and the occurrence of severe and dominant auscultatory phenomena typical for congenital aortic valve defect which effectively masked the syndromes of increased pulmonary flow. The authors discuss the role of the impact of phenotypic characteristics of the Turner syndrome, in particular a short webbed neck restricting the suprasternal echocardiographic access and the presence of psychological factors associated with a long-term illness. The i...

Research paper thumbnail of Intraoperative Macroscopic Lung Appearance in Premature Infants with Body Weights Less than 1000 G Undergoing Surgical Treatment for PDA

Polish Journal of Surgery, 2007

The aim of the study was to assess the relationship between intraoperatively observed macroscopic... more The aim of the study was to assess the relationship between intraoperatively observed macroscopic pathologic findings in the left lung and the chosen clinical factors. The factors analyzed in the study were the following: neonatal gestational age and body weight, the age of the neonate at the time of surgery, the history of intrauterine infection and/or presence of active infection in the neonate, the history of ibuprofen treatment, and intraoperative diameter of the arterial duct. Material and methods. The authors included a group of 126 preterm infants with body weight less than 1000 g undergoing surgical treatment for PDA in the 2 nd Department of Cardiac and General Pediatric Surgery between January 2000 and May 2006 and analyzed the macroscopic intraoperative left lung appearance. The average body weight of the neonates who participated in the study was 765.2 g, with the average gestational age 25.68 Hbd. According to the results of intraoperative macroscopic lung assessment, the neonates were classified into one of the following three groups: 0-normal lungs or partially stiff lungs with emphysema focuses, 1-limited macroscopic findings, focuses of limited atelectasis, lung congestion, 2-severe pathologic findings in the pulmonary tissue, pulmonary hematomas, bleeding pulmonary surface, disseminated atelectasis, liver-like pulmonary tissue. In the study, the statistical analysis of the relationship between pathological pulmonary findings (groups 0, 1, 2) and investigated factors was performed by the comparison of mean values (or median) of the investigated factor in the analyzed groups. The Kruskal-Wallis and the Mann-Whitney tests were used dependent of the analyzed factor. Additionally, for chosen factors (the infection presence and PDA diameter), their relationship with the lung macroscopic appearance was assessed with the use of the Spearman test. Results. The pathological findings in the lungs were observed in the majority of the neonates (54%). The statistical analysis did not show any relationship between the pulmonary disorders and the majority of investigated factors. Conclusions. 1. The authors found that a duct diameter of ³ 4 mm correlates with the development of more severe disorders in the pulmonary tissue. 2. The authors emphasized the good results of surgical treatment of PDA and the lack of death in the perioperative period in that group of patients.

Research paper thumbnail of Zwiotczenie prawej kopuły przepony i zespół wad wrodzonych serca u niemowlęcia z delecją terminalną 8p23.1

Research paper thumbnail of Zespół wad wrodzonych ze złożoną wadą serca i zaburzeniami krzepnięcia sugerujący spektrum oczno-uszno-kręgowe – opis przypadku

Pediatria Polska, 2015

Abstract Oculo-auriculo-vertebral spectrum (OAVS) is a multisystem developmental anomaly that aff... more Abstract Oculo-auriculo-vertebral spectrum (OAVS) is a multisystem developmental anomaly that affects one in every 5600–26,500 births. The case of a 13-month-old girl with typical symptoms of OAVS and successfully corrected coexistent double outlet right ventricle with outflow tract obstruction is presented. Additionally deficit of VII, IX and XII coagulation factors was diagnosed prior to surgery as well as hemiparesis, right kidney agenesis and cleft palate. The authors stress the need for detailed and extended coagulologic laboratory examinations to precisely calculate operative risk and to establish appropriate therapeutic protocol.

Research paper thumbnail of Cervical Thymic Cyst

Polish Journal of Surgery, 2007

Kierownik: prof. dr hab. M. A. Karolczak The Authors of this study present a case of a 13-month o... more Kierownik: prof. dr hab. M. A. Karolczak The Authors of this study present a case of a 13-month old child subjected to surgical intervention for a cervical thymic cyst. The origin of lesions in children is usually associated with remnants from the development of the fetal thymus gland. When the tumor attains significant size, especially in the presence of clinical symptoms, such as respiratory disturbances and problems with feeding, surgical management is required. In spite of the rarity of thymic cysts, it should be considered in cases of differential diagnosis for neck tumors in children. Proper diagnosis is usually possible after the histopathological evaluation of removed tissues. The cervical approach enables removal of the entire lesion, even if partially localized in the thoracic cavity.

Research paper thumbnail of Right-sided intrathoracic bypass graft for complex or recurrent coarctation of the aorta

European Journal of Cardio-Thoracic Surgery, 1989

A simple technique is described for the interposition of a tube graft between the ascending and d... more A simple technique is described for the interposition of a tube graft between the ascending and descending aorta in the right chest. Directing the graft posteriorly preserves the integrity of the pericardium and avoids potential damage to the prosthesis at a subsequent sternotomy for open heart surgery. This procedure was used successfully and without complication in an 18-month-old boy who had undergone two previous operations for coarctation of the aorta, and in a 20-year-old girl with William&#39;s syndrome and diffuse hypoplasia of the distal aortic arch.

Research paper thumbnail of Efficacy and safety of surgical treatment of PDA in VLBW neonates. Warsaw region multicenter collaboration

Early Human Development, 2008

Background and aim Purpose: to evaluate the value of echocardiographic exam for the diagnosis and... more Background and aim Purpose: to evaluate the value of echocardiographic exam for the diagnosis and follow up of perinatal posthypoxic myocardial injury in the newborn infant. Materials and methods Methods. Patients: 92 newborns aged 0 to 14 days, with normal birth weight, hospitalised in Neonatology Intensive Care of the Cuza Voda Maternity Iasi, with perinatal hypoxia and Apgar score 3-7 and receiving resuscitation. The patients were without major congenital heart defects. In all cases were performed: clinical exam, ECG, chest X-ray (Rx.CT), Doppler echocardiographic exam (Echo). Most of our patients were treated with spironolactone 1 mg/kg/day for 3-5 months and evaluated clinically and echo after 6 months. Results The patients had mainly signs of neurological post hypoxic suffering, without signs of severe cardiac involvement. The cardiac examination revealed: systolic murmur (78 cases) and signs of persistent pulmonary hypertension of newborn (PPHN) in 12 cases. Chest X-ray: cardiomegaly (41 cases). ECG: severe left ventricle (LV) repolarization disturbances and low voltage of QRS complexes (47 cases), without ischemic changes. Doppler echo exam performed at 2-7 days of life revealed: ⁎ the absence of other severe congenital cardiac anomaly; ⁎permeability of foramen ovalae (100% cases) to the forced foramen ovalae (gradient LA/RA > 8 mmHg); ⁎myocardial hypertrophy (62 cases) mainly interventricular septal (48 cases), signs of PPHN(12 cases) with mild to severe tricuspid insufficiency(48 cases) and right atrium dilation (31 cases); prolonged isovolumic relaxation period (35 cases), increased the values of myocardial performance index (49 cases), the systolic function normal (all cases) and severe LV diastolic dysfunction (E/A < 1) in 51 cases. Reevaluation at 6 months showed the reduction of the myocardial hypertrophy and of the tricuspid regurgitation, with a normal LV diastolic function. Conclusions The severe perinatal hypoxia can induce the apparition of a true posthypoxic cardiomypathy at more than 70% of patients, the signs of cardiovascular suffering missing often. Echocardiography is the main method for diagnosis and follow up of perinatal hypoxic cardiomyopathy and is necessary from the first week of life.

Research paper thumbnail of Staged and primary Yasui repair in infants with interrupted aortic arch

Research paper thumbnail of Wady wrodzone Unusual presentation of the right atrial thrombus formation in a child with acute lymphoblastic leukaemia: a case report

Research paper thumbnail of WADY WRODZONE Cor triatriatum sinister with partially anomalous left pulmonary

Research paper thumbnail of Repair of common arterial trunk type I after previous pulmonary artery banding: technical considerations

Omówiono wybrane aspekty operacji wspólnego pnia tętniczego typu I u niemowląt po uprzednim bandi... more Omówiono wybrane aspekty operacji wspólnego pnia tętniczego typu I u niemowląt po uprzednim bandingu pnia płucnego, koncentrując się na wykorzystaniu metody analogicznej do stosowanej w korekcji okienka aortalno-płucnego. Technika ta jako warta rozważenia alternatywa dla odcięcia pnia płucnego i rekonstrukcji ściany neoaorty została przez autorów szczegółowo opisana oraz zilustrowana. Słowa kluczowe: wspólny pień tętniczy, banding tętnicy płucnej. Summary

Research paper thumbnail of Cor triatriatum dexter with underdevelopment of the right ventricle– case report

... Obliteracja balonem otworu międzyprzedsionkowego może być metodą rozstrzygającą w procesie kw... more ... Obliteracja balonem otworu międzyprzedsionkowego może być metodą rozstrzygającą w procesie kwalifikowania do operacji kardiochirurgicznej. Piśmiennictwo. 1. Joe BN, Poustchi-Amin M,Woodard PK. Case 56: cor triatriatum dexter. Radiology 2003; 226: 701-705. ...

Research paper thumbnail of WADY WRODZONE Removal of an unstable Amplatzer occluder and surgical closure of ASD in a 10-year old girl – a case report

... Jacek Wieteska, Maciej Karolczak, Bożena Werner, Krzysztof Godlewski. ... nowego typu implant... more ... Jacek Wieteska, Maciej Karolczak, Bożena Werner, Krzysztof Godlewski. ... nowego typu implantu Amplatzera (AGA Medical Carporation, Golden Valley, Minnesota, USA) poprawiło wyniki leczenia i zmniejszyło liczbę powikłań [1]. Ostatnie doniesienia potwierdzają również dużą ...

Research paper thumbnail of WADY WRODZONE Anomalous low insertion of superior vena cava into right atrium in infant with partial anomalous drainage of left pulmonary veins

Anomalies of the localization of the upper cavoatrial junction are extremely rare. We present the... more Anomalies of the localization of the upper cavoatrial junction are extremely rare. We present the case of 9 months old boy with low insertion of superior vena cava to right atrium and coexistent partial anomalous drainage of left pulmonary veins.

Research paper thumbnail of Double-chambered right ventricle in a 16-year-old patient with Williams syndrome

Journal of Ultrasonography

We present a case of double-chambered right ventricle diagnosed during preparation for colonoscop... more We present a case of double-chambered right ventricle diagnosed during preparation for colonoscopy due to gastrointestinal bleeding in a 16-year-old, mentally disabled boy with Williams syndrome. The patient was previously diagnosed with ventricular septal defect and mild pulmonary stenosis. Echocardiography performed under general anesthesia revealed hypertrophied muscular bundles in the right ventricle with the maximum gradient of 100 mmHg, causing severe outflow obstruction. This type of defect is extremely rare in patients with Williams syndrome, with only one case, which was diagnosed during invasive angiocardiography, described in world literature. A successful total surgical correction was performed based on echocardiography data.

Research paper thumbnail of Coronary steal phenomenon following right ventricle decompression and revascularization of atretic left coronary ostium: case report

Journal of Cardiothoracic Surgery

Background Coronary steal phenomenon and myocardial ischemia is a complication following decompre... more Background Coronary steal phenomenon and myocardial ischemia is a complication following decompression of a hypertensive right ventricle in patients with left coronary-cameral fistulae. Case presentation We present a 12-year-old girl with a complex heart defect successfully operated on using a hybrid surgical-interventional approach to decompress the ventricle, embolize the fistula and reconstruct the atretic left coronary ostium. Conclusions A novel hybrid strategy is the best solution for coronary-cameral fistulas reliant on high ventricular pressure at high risk for coronary steal phenomenon.

Research paper thumbnail of Late diagnosis of total anomalous pulmonary venous drainage in a 5.5-month-old infant

Journal of Ultrasonography, Apr 3, 2019

Background Total anomalous pulmonary venous drainage (TAPVD) is a cyanotic heart defect. TAPVD ac... more Background Total anomalous pulmonary venous drainage (TAPVD) is a cyanotic heart defect. TAPVD accounts for around 1.5% of all congenital heart defects (1) (1:10 000 live births (2)). Depending on morphological variants of the pulmonary venous drainage to the heart, four types of the defect may be distinguished: supracardiac (the most common, around 45% of reported cases (1,3)), intracardiac, infracardiac and mixed. Cyanosis, which accompanies TAPVD, depends on the effectiveness of the collateral circulation, the diameter of the pulmonary veins and the vertical vein, as well as the size of the coexistent atrial septal defect (ASD) (the only way by which oxygenated blood can reach the left atrium). Signs and symptoms typically exacerbate during physical exercise. About 80% of patients with TAPVD die within the first year of life (1,4,5) if untreated, although the literature mentions oligosymptomatic cases with long-term survival (1,4,6). Common symptoms of TAPVD include shortness of breath, cyanosis, fatigue, somnolence and no weight gain. An open-heart surgery should be performed immediately after the diagnosis in the neonatal period (5) .

Research paper thumbnail of Non-invasive diagnosis of aortic arch anomalies in children – 15 years of own experience

Journal of Ultrasonography, Apr 3, 2019

Non-invasive diagnosis of aortic arch anomalies in children-15 years of own experience