A rare case report of fibrous dysplasia of maxillary bone causing progressive vision loss: Case report (original) (raw)

Fibrous Dysplasia of Maxilla: A Case Report

Oral Surgery, Oral Medicine, Oral Pathology and Oral Radiology, 2015

Fibrous dysplasia (FD) is classified as a fibro-osseous lesion, benign in nature which exhibits distinctive features like exchange of normal bone by fibro-osseous connective tissue with different degrees of osseous metaplasia. The craniofacial type of FD which can affect jaw bones is a rare entity. It may cause pain, deformities, and pathological fracture of bone. FD constitutes approximately 2-5% of all bone tumors and 7% of all benign tumors. Here, we are reporting a case of FD affecting maxilla. Diagnosis was based on clinical, radiographical, and histological findings. Differential diagnosis poses a great value in case of FD.

Fibrous dysplasia of maxilla: An unusual case report

International Journal of Medical and Dental Case Reports

Bone is a dense connective tissue which is being aff ected by many diseases and that is independent of any age limits. Fibro-osseous lesions consist of the normal bone is being substituted by benign fi brous tissue comprising varying amount of mineralization which characteristically aff ect jaws and the craniofacial bone pathology.

Radiographic Diagnosis of Fibrous Dysplasia in Maxilla

Cureus, 2018

Fibrous dysplasia is a rare bone disorder characterized by the replacement of normal bone by abnormal fibrous tissue. Here we present a 16-year-old female with a fibrous dysplasia in the maxilla and obliteration of the sinus in the same side. Cone beam computed tomography scan revealed a mixed radiopacity that extended from the alveolar crest of the right posterior teeth to the right orbital floor in the superior-inferior direction. The radiopaque areas had homogenous ground glass appearance. There is a loss of bone trabeculation, thinning of the cortical boundaries but still intact, and a loss of the lamina dura around the right posterior permanent teeth. The radiographical features of the lesion were indicative of fibrous dysplasia in the maxilla.

Fibrous dysplasia of maxilla – A rare case report

Indian Journal of Case Reports, 2021

Fibrous dysplasia (FD) is a skeletal developmental anomaly, which is non-hereditary in origin and idiopathic in nature. It is a benign fibro-osseous disease that affects one or more bones. It usually affects unilaterally and is seen in the posterior region. Approximately 0.5% of untreated cases show the malignant transformation. We report the case of a 35-year-old female patient with FD involving the maxilla. The clinical diagnostic approach, different imaging modalities, and histological examination methods for definitive diagnosis have been elaborated.

Monostotic Fibrous Dysplasia of Maxilla: A Case Report

Innovative Publication, 2016

Fibrous Dysplasia is a non-neoplastic developmental disease of bone, which manifest as a defect in osteoblastic differentiation and maturation. It represents with three forms namely monostotic (single bone involvement), polyostotic (multiple bone involvement) and craniofacial forms. Maxilla is affected most commonly twice as mandible, in the posterior region. This paper describes a case of 18 years old male who presented with swelling on right middle third of the face and intraoral swelling on right posterior maxilla since one year. The diagnosis was based on clinico-radiological and histopathological investigations. The appropriate management was done and he is under followup without any recurrence.

FIBROUS DYSPLASIA IN THE MAXILLO-MANDIBULAR REGION – case report

Journal of IMAB - Annual Proceeding (Scientific Papers), 2010

Craniofacial fibrous dysplasia is 1 of 3 types of fibrous dysplasia that can affect the bones of the craniofacial complex, including the mandible and maxilla. Fibrous displasia is a skeletal developmental disorder of the bone-forming mesenchyme that manifests as a defect in osteoblastic differentiation and maturation. It is a lesion of unknown etiology, uncertain pathogenesis, and diverse histopathology. Fibrous dysplasia represents about 2, 5% of all bone tumors and over 7% of all benign tumours. The aim of this article is to represent a rare case of bilateral fibrous dysplasia of the upper and lower jaws, in combination with Intellectual disability (previously called mental retardation). The clinical diagnostic approach including imaging studies: Orthopantomogram (OPG) and 3D tomography is described. Histological examination was also essential for obtaining a definitive diagnosis.

Monostotic Fibrous Dysplasia Presenting in Maxilla: A Case Report

Journal of Istanbul University Faculty of Dentistry, 2016

Fibrous dysplasia (FD) is a bone disorder in which fibrous tissue replaces normal bone. FD can be monostotic (10%-25%) or polyostotic (50-90%) and is typically diagnosed accidentally on radiographs. Craniofacial lesions are typically unilateral and are diagnosed by clinical assessment and radiographic evaluation. This report describes the case of a 50-yearold female patient who had presented with painless swelling of the right maxilla and was diagnosed with FD. Subsequent bone scintigraphy identified the lesion as monostotic. Based on the patient's age and the radiographic data, contour correction was performed. However, 1 year after surgery, the lesion regrew and the treatment was repeated.

Surgical Approach In Craniofacial Fibrous Dysplasia: Case Report And Integrative Review

International Archives of Medicine, 2016

Fibrous dysplasia is a benign and pseudoneoplasic osteopathy with slow progression, characterized by the replacement of normal bone by an excessive proliferation of fibrous connective tissue cell, interspersed with irregular bone trabeculae. In general, it affects 1 between 4,000 to 10,000 individuals living births. This is a not familiar, congenital disorder, which produces around 2.5% of all bone tumors and more than 7% of all non-malignant bone tumors. This article aims to report a clinical case of monostotic fibrous dysplasia in jaw, proceeding with its surgical correction and to make a review of literature, describing the most important features and the major controversies.

Craniofacial fibrous dysplasia (CFD) of the maxilla in an 11-year old boy: A case report

Journal of Cranio-Maxillofacial Surgery, 2012

We present the case of a surgically treated 11-year old boy with a diagnosis of craniomaxillofacial fibrous dysplasia (CFD) in the maxillary sinus. When first seen in the outpatient clinic of our department he had minimal symptoms. After initial radiological diagnostics by computed tomography scans (CT-scans) the patient was treated operatively by radical excision of the tumor. The radiographs showed the typical intramedullary located and well-defined lesions, which eroded the cortical bone with the typical appearance of fibrous dysplasia. The histopathology showed the typical curved extending fibrous trabeculae in C, O and Y-shape which were embedded in a moderately cellular morphologically inconspicuous stroma, confirming the initial suspicion of fibrous dysplasia of the maxillary bone. Cone beam tomography was a valuable tool in determining the re-ossification of bone at the affected side. Local resection can be curative in limited disease.