Rare Giant Angiokeratoma of Vulva: A Case Report (original) (raw)
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Angiokeratoma of Fordyce in man and woman — case reports
Central European Journal of Medicine, 2012
Angiokeratomas are papular vascular lesions characterized by marked ectasia of the superficial dermal blood vessels. Dermatological examination of angiokeratomas of Fordyce is characterized by papular keratotic lesions of erythematous-violet color. They are more common in the scrotum, and vulval involvement is rarely reported. This article reports the cases of angiokeratoma of Fordyce in a 25-year-old man and a 42-year-old woman. Diagnosis were made by history and physical examination. Dermoscopy has shown well-demarcated round dark lacunae in both patients. As the lesions were asymptomatic, the patients requested no further treatment.
Rare case of recurrent angiokeratoma of Fordyce on penile shaft
Urology, 2006
Angiokeratomas are benign cutaneous vascular lesions characterized by dilated thin-walled blood vessels lying in the upper part of the dermis, mostly associated with an epidermal reaction such as acanthosis and/or hyperkeratosis. Angiokeratomas of Fordyce are predominantly located on the scrotum and are only rarely found on the penis and then usually on the glans penis. We report a rare case of angiokeratoma of Fordyce located on the shaft of the penis and associated with two recurrences after appropriate surgical excision.
Multiple giant angiokeratoma of Fordyce on the shaft of the penis masquerading as keratoacanthoma
Anais Brasileiros de Dermatologia, 2015
The term 'angiokeratoma' includes a wide range of dermatological conditions of hyperkeratotic vascular disorders with a similar histologic combination of hyperkeratosis and superfi cial dermal vascular ectasia. Angiokeratomas can be classifi ed into localized and systemic forms. Angiokeratoma of Fordyce (AKF) is a localized form of angiokeratoma, clinically characterized by 1-to 6-mm, black, blue, or dark red, dome-shaped papules located on the scrotum, shaft of penis, labia majora, clitoris, inner thigh, and lower abdomen. We describe herein a case of giant angiokeratoma of Fordyce on shaft of the penis in an elderly man, clinically masquerading as keratoacanthoma.
Cureus, 2022
Angiokeratomas are benign vascular lesions that can occur anywhere in the body. Fordyce angiokeratomas, also known as genital angiokeratomas, often develop on the vulva in women and the scrotum in males. A subtype of genital angiokeratoma in males is called penile angiokeratoma (PEAKER). In females, clitoral angiokeratoma (CLANKER) is the embryologic equivalent. As a result of the underlying pathophysiology, these lesions are often bilateral. Unilateral Fordyce angiokeratoma instances are infrequent, and unilateral PEAKER cases have never been previously documented. We describe a case of Fordyce's unilateral angiokeratoma with unilateral PEAKER. To the best of our knowledge, such a variation in presentation of this rare disease has not been previously reported.
Angiokeratoma of Clitoris: a Rare Lesion In An Adolescent Girl
Urology, 2008
Angiokeratoma is a benign vascular lesion. It is the result of dilation of ectatic subdermal vessels and congested capillaries. Weakness of the vessel walls, either from acquired or congenital reasons, can cause formation of the lesion. Angiokeratoma is more common in males, in ...
Vulva tumors are generally rare disease entity encountered in clinical practice of gynecology, and it is especially so at a young age. The spectrum of tumors arising in the vulva may be attributable to inflammatory conditions, infections, dermatological conditions, vulva intraepithelial neoplasia and invasive cancer; thus many specialties in the medical field may be consulted for diagnosis and treatment. Definitive diagnosis requires biopsy (incisional or excision). Other tests may be ordered as supportive or to diagnose infectious or other systemic causes of Vulva swellings. Presented here is a case report and diagnostic challenges of a mysterious vulvar swelling in a 20 years old woman who presented to our Hospital with painless progressively enlarging bilateral vulvar tumor which evolved over a period of four years. INTRODUCTION Tumors of the vulva are rare, few published cases have reported about this condition [1]. Apart from malignant tumors, fibromas fall in the group of the ...
Spectrum of vulvar lesions: a clinicopathologic study of 170 cases
International Journal of Reproduction, Contraception, Obstetrics and Gynecology, 2014
Background: A wide range lesions may occur in the vulvar region. The clinician is often confronted with the challenge to draw a distinction between normal variants, benign entities and a potentially serious pathology. The aim of the present study is to have an insight into the diverse morphologic spectrum of vulvar lesions. Methods: The present retrospective study was carried out by compiling the data from archival records over a period of eight years from January 2005 to December 2012. The vulvar biopsies/vulvectomy specimens were studied for histomorphological features. The lesions were categorized as non neoplastic, neoplastic and inconclusive; neoplastic ones were further divided into benign, malignant and premalignant. Results: The age of the women ranged from 6 to 80 years (mean 38.2±6.4) with the maximum number of patients between 31 to 40 years of age. Most common clinical presentation was itching and white plaque on the vulva (85 cases; 50%). The commonest site of vulval lesions was labia majora (87 cases, 51.18%). Non neoplastic lesions were more common (n = 94; 55.29%) than the neoplastic lesions (n =50; 29.41%). There were 23 (46%) benign lesions while 27 cases (54%) were malignant or premalignant ones. In 26 cases, no definitive histologic diagnosis could be rendered. Conclusion: Early recognition of vulvar lesions and a prompt biopsy diagnosis for all lesions with suspicious changes is of great significance. The term leukoplakia is imprecise and should be replaced by a precise histological description.
A Giant Vulvar Mass: A Case Study of Cellular Angiofibroma
Case Reports in Obstetrics and Gynecology, 2016
Cellular angiofibroma is a mesenchymal tumor that affects both genders. Nucci et al. first described it in 1997. Cellular angiofibroma is generally a small and asymptomatic mass that primarily arises in the vulvar-vaginal region, although rare cases have been reported in the pelvic and extrapelvic regions. It affects women most often during the fifth decade of life. The treatment requires simple local excision due to low local recurrence and no chance of metastasization. The current study presents a case of angiofibroma in the vulvar region that measured approximately 20 cm.
Angiographic Embolization followed by Excision of Large Cellular Angiofibroma of the Vulva
Current opinion in gynecology and obstetrics, 2019
Introduction: Cellular angiofibroma is a rare benign mesenchymal tumor, occurring almost exclusively in the superficial soft tissues of the genital region. Some of these lesions presents as large, hypervascularized masses. There are no reports in the literature to date on the challenges of resection of hypervascularized vulvar masses, or of hypervascularized cellular angiofibroma. Materials and methods: We describe a case of a cellular angiofibroma of the vulva and the surgical approach with tumoral vessel embolization and posterior resection. Case: A 47-year-old women was referred to vulvar pathology section of Italian Hospital of Buenos Aires for evaluation of left vulvar mass. A pelvic angiography was performed 5 days prior to surgery. It showed a hypervascularized formation at the level of the left vulva at the expense mainly of branches of the left internal pudendal artery. A complete resection was performed afterwards at our institution. The histopathological diagnosis was compatible with cellular angiofibroma. Conclusion: We consider that surgical planning is essential and has to be performed with a multidisciplinary approach. Angiographic embolization should be taken into account as a valid resource when planning a surgery with a high risk of blood loss in order to decrease morbidity.