Monogenic and Polygenic Models Detected in Steroid 21-Hydroxylase Deficiency-Related Paediatric Hyperandrogenism (original) (raw)

An Androgen Receptor Gene Mutation (E653K) in a Family with Congenital Adrenal Hyperplasia due to Steroid 21-Hydroxylase Deficiency as well as in Partial Androgen Insensitivity

Sten Ivarsson

The Journal of Clinical Endocrinology & Metabolism, 2002

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Genotype-phenotype correlations in children and adolescents with nonclassical congenital adrenal hyperplasia due to 21-hydroxylase deficiency

Karl Schwab

Molecular and Cellular Pediatrics, 2020

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The Genetics of Steroid 21-Hydroxylase Deficiency

Javier Aisenberg

The Endocrinologist, 2005

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Nonclassic Steroid 21-Hydroxylase Deficiency due to a Homozygous V281L Mutation in CYP21A2 Detected by the Neonatal Mass-Screening Program in Japan

Reiko Horikawa

Endocrine Journal, 2007

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Mutational spectrum of steroid 21-hydroxylase and the genotype-phenotype association in Middle European patients with congenital adrenal hyperplasia

Franz Waldhauser

European Journal of Endocrinology, 2005

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CYP21A2 Genotypes do not Predict the Severity of Hyperandrogenic Manifestations in the Nonclassical Form of Congenital Adrenal Hyperplasia

Berenice Mendonca

Hormone and Metabolic Research, 2013

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Steroid 21‐hydroxylase gene mutational spectrum in 454 Argentinean patients: genotype–phenotype correlation in a large cohort of patients with congenital adrenal hyperplasia

noura zouari

Clinical Endocrinology, 2011

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Disease expression and molecular genotype in congenital adrenal hyperplasia due to 21-hydroxylase deficiency

Phyllis Speiser

Journal of Clinical Investigation, 1992

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Adrenal 21-hydroxylase gene mutations in Slovenian hyperandrogenic women: evaluation of corticotrophin stimulation and HLA polymorphisms in screening for carrier status

Vita Dolzan

European Journal of Endocrinology, 1999

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Common Genetic Variants of the Human Steroid 21- Hydroxylase Gene (CYP21A2) Are Related to Differences in Circulating Hormone Levels

Klara Koncz, Marton Doleschall

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Clinical Role of CYP2C19 Polymorphisms in Patients with Congenital Adrenal Hyperplasia Due to 21-hydroxylase Deficiency

Tinka Hovnik

Acta Chimica Slovenica, 2016

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Genotype–phenotype correlation in 1,507 families with congenital adrenal hyperplasia owing to 21-hydroxylase deficiency

brian gonzalez

Proceedings of the National Academy of Sciences, 2013

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High Frequency of Nonclassical Steroid 21-Hydroxylase Deficiency

Phyllis Speiser

Obstetrical & Gynecological Survey, 1986

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Endocrine profile and phenotype-genotype correlation in unrelated patients with non-classical congenital adrenal hyperplasia

Leonidas Phylactou, Vassos Neocleous

Clinical Biochemistry, 2011

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Congenital Adrenal Hyperplasia - The Main Effect of 21-Hydroxylase Deficiency

Davide Carvalho

IntechOpen eBooks, 2022

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Limited Value of Serum Steroid Measurements in Identification of Mild Form of 21-Hydroxylase Deficiency

Miklós Garami

Experimental and Clinical Endocrinology & Diabetes, 2003

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Molecular diagnosis of congenital adrenal hyperplasia due to 21-hydroxylase deficiency: an update of new CYP21A2 mutations

mohammad Taghi Akbari

Clinical Chemistry and Laboratory Medicine, 2010

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HETEROGENEITY OF STEROID 21-HYDROXYLASE GENES IN CLASSICAL CONGENITAL ADRENAL HYPERPLASIA

Roger Dawkins

European Journal of Immunogenetics, 1987

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Identification of non-amplifying CYP21 genes when using PCR-based diagnosis of 21-hydroxylase deficiency in congenital adrenal hyperplasia (CAH) affected pedigrees

DJ Day, Phyllis Speiser

Human Molecular Genetics, 1996

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Mutational Characterization of Steroid 21Hydroxylase Gene in Portuguese patients with Congenital Adrenal Hyperplasia

Selma Fernandes

Experimental and Clinical Endocrinology & Diabetes, 2009

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Recent advances in biochemical and molecular analysis of congenital adrenal hyperplasia due to 21-hydroxylase deficiency

Gu-Hwan Kim

Annals of pediatric endocrinology & metabolism, 2016

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Molecular diagnosis of patients with congenital adrenal hyperplasia due to 21-hydroxylase deficiency

Henrik Falhammar

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Pharmacogenetics of glucocorticoid replacement could optimize the treatment of congenital adrenal hyperplasia due to 21-hydroxylase deficiency

Berenice Mendonca

Clinics (São Paulo, Brazil), 2011

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Screening for Mutations of 21-Hydroxylase Gene in Hungarian Patients with Congenital Adrenal Hyperplasia 1

Csaba Barta

The Journal of Clinical Endocrinology & Metabolism, 1999

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Research Article Variations in the 3′UTR of the CYP21A2 Gene in Heterozygous Females with Hyperandrogenaemia

Vassos Neocleous, Meropi Toumba

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Screening for Mutations of 21-Hydroxylase Gene in Hungarian Patients with Congenital Adrenal Hyperplasia

Miklós Garami

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Characterization of mutations on the rare duplicated C4/CYP21 haplotype in steroid 21-hydroxylase deficiency

Holger Luthman

Human Genetics, 1994

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Congenital Adrenal Hyperplasia (CAH) due to 21-Hydroxylase Deficiency: A Comprehensive Focus on 233 Pathogenic Variants of CYP21A2 Gene

Kim Thiên Nguyễn

Molecular Diagnosis & Therapy, 2018

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Comprehensive Genetic Analysis of 182 Unrelated Families with Congenital Adrenal Hyperplasia due to 21-Hydroxylase Deficiency

Gabriela Finkielstain

The Journal of Clinical Endocrinology & Metabolism, 2011

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