The case of Schnitzler syndrome in one single rheumatologic center (original) (raw)
2015, Pediatric Rheumatology
https://doi.org/10.1186/1546-0096-13-S1-P164
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Abstract
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Schnitzler syndrome is a rare disorder characterized by chronic urticaria, recurrent fever, arthralgia, and monoclonal IgM gammopathy, with an obscure pathogenesis possibly linked to immune complex formation. This case report details the instance of a 44-year-old male with symptoms starting at age 40, highlighting diagnostic challenges due to overlapping presentations with other disorders like Muckle-Wells syndrome. Treatment included NSAIDs and systemic steroids, providing partial relief.
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