The Fifth Chamber of the Heart: Congenital Aneurysm of the Atrial Appendage (original) (raw)

Five chambered heart: case of a huge left atrial appendage aneurysm

Cardiovascular pathology : the official journal of the Society for Cardiovascular Pathology

Aneurysmal enlargement of the left atrial appendage is an extremely rare pathology and can predispose to adverse events, including cardiac arrest, respiratory distress, arrhythmia, heart failure, systemic thromboembolism, or rupture. It is usually diagnosed incidentally or after the occurrence of atrial tachyarrhythmias or thrombotic events in the second to fourth decades of life. We describe a rare case of a symptomatic giant congenital left atrial appendage aneurysm (LAAA) in a 26-year-old man presenting with neurologic event, in whom surgical resection of the aneurysm was successfully performed. This is the largest LAAA reported in the literature so far.

Five chambered heart or large atrial appendage aneurysm: A report of two cases

ARYA atherosclerosis, 2013

Isolated intrapericardial LAA aneurysm is a rare cardiac anomaly which manifests with angina, dyspnea on exertion (DOE), systemic embolization, arrhythmia, and congestive heart failure. A 30-year-old female and a 46-year-old male were referred for evaluation of abnormal cardiac contour on chest radiograph and echocardiographic findings and non-specific symptoms. Transesophageal echocardiography suggested left atrial appendage (LAA) mass filled with clots. The mass had no compression on cardiac chambers and global ejection fraction was within normal limits. The intraoperative diagnosis was isolated congenital LAA aneurysm. After confirmation of the diagnosis, it was resected. She was discharged with uneventful postoperative course. At follow-up she was asymptomatic. These cases demonstrate the role of on-time surgical approaches in the prevention of fatal complication of this rare cardiac anomaly.

Asymptomatic giant congenital left atrial aneurysm

Turkish Journal of Pediatrics, 2019

Congenital aneurysm of the left atrial appendage can be caused by congenital dysplasia of the pectinate muscles and may be accompanied by a congenital absence of the pericardium. Symptoms generally manifest after two decades and the most common symptom is atrial arrhythmia in the form of atrial fibrillation / flutter. A four year-old patient with no symptoms underwent an echocardiographic examination for the investigation of a heart murmur. Echocardiographic examination revealed a large cystic lesion occupying the left hemithorax and compressing the left ventricle. The patient was referred to our center. The lesion caused displacement of the heart rightward behind the sternum which made the examination difficult. We aimed to present this rare case of giant left atrial appendage aneurysm in the light of current literature.

Congenital Aneurysm of the Left Atrial Appendage with Left Superior Vena Cava

Clinical Medicine Insights: Therapeutics, 2011

A 32-year-old man underwent excision of an aneurysm of the left atrial appendage which had been causing palpitation and supraventricular tachyarrhythmia. Various techniques are useful for making the diagnosis and allowing differential diagnosis between this and other pathologies. In this report, the diagnosis was based on transthoracic and transesophageal echocardiography, and the patient was treated by surgical resection of the aneurysm on cardiopulmonary bypass. There were no postoperative complications. Four months later, the patient remained asymptomatic and in sinus rhythm.

Left Atrial Appendage Giant Aneurysm- A Case Report

Bangladesh heart journal, 2022

Aneyrysm of left Atrial appendage (LAAA) is a rare cardiac anomaly. It was first identified in 1960. 1 As severe complications like thromboembolic events, rhythm disorders and CCF surgical management is recommended. The authors presented a 24 years old boy who was hospitalized with a LAAA. It was detected incidentally by CT Scan of the chest. The patient underwent operation with removal of aneurysm under cardiopulmonary bypass. Case Presentation Masum Billah of 21 years boy was attended in outpatient department with non specific presentation. A Thoracic Xray was done and suspected as a case of posterior mediastinal mass. A contrast CT scan was done and diagnosed as a case of giant LAAA (90 mm × 75 mm). For Cardiac evaluation Echocardiography was done and revealed large 90 mm x 70 mm LAAA enlarged compressing the left ventricle. The other findings of Echocardiography was within normal limit. Doing all necessary investigations the patient was scheduled to undergo surgery on 04/10/2020.

Aneurysm of the Right Atrial Appendage

Arquivos Brasileiros De Cardiologia, 2002

Atrial aneurysms involving the free wall or atrial appendage are rare entities in cardiology practice and may be associated with atrial arrhythmias or embolic phenomena. We review the literature and report a case of aneurysm of the right atrial appendage in a young adult, whose diagnosis was established with echocardiography after an episode of paroxysmal atrial flutter.

Aneurysm left atrial appendage

Cardiometry, 2017

Aneurysms of the atrial appendages are rare and extremely rare clinical entities. It can be confused with pericardial cyst, coronary artery aneurysm, left ventricular pseudoaneurysm and partial or complete congenital absence of the pericardium. Usually clinically asymptomatic, diagnosed as incidental finding by the presence of heart murmur or cardiomegaly on chest radiograph, it can also manifest in the presence of supraventricular arrhythmias or systemic embolism. The treatment of this pathology makes aneurysmectomy. For 3year preschool heart murmur and echocardiographic finding of insufficiency Mitral and aneurysmal dilation of the left atrial appendage it is presented.

Left Atrial Appendage Aneurysm in a Two Month Old Infant: A Case report

Life Science Journal 2014;11(10), 2014

Congenital aneurysm of the left atrial appendage is a rare anomaly caused by congenital dysplasia of the atrial muscles. The major manifestations of these aneurysms are cardiomegaly in the x-ray, supraventricular tachycardia, and systemic embolism. The case reported is a two month old infant who was evaluated because of respiratory symptoms and signs of cardiomegaly in Chest X-Ray. A large cystic mass communicating with the left atrium was seen on echocardiography. The diagnosis was based on echocardiography and was confirmed by computed tomography angiocardiography. Pathological examination after surgical excision confirmed its nature as an aneurysm of the left atrial appendage. Up to our knowledge, this case is so far the first case reported in Saudi Arabia having this presentation in infancy.