Lutembacher’s Syndrome An Echocardiographic Assessment (original) (raw)

Lu�e�bac�er'ssyndro�e (L�), consis�ed o� A�rial �ep�al �e�ec� (A��) and Mi�ral ��enosis (M�), is a very rare �or� o� cardiac ano�aly. �ene Lu�e�bac�er's�irs� described ��is syndro�ein 1916. Curren�ly, any co�-bina�ion o� A��, congeni�al or ia�rogenic and M�, acquired or congeni�al is re�erred as L�. By using ec�ocardiograp�y, ��e �e�odyna�ic o� L� could be assesed. �a��op�ysiologically, ��e �e�odyna�ic o� A�� is rela�ed�o ��e �agni�ude and direc�ion o� s�un�ing across ��e in�era�rial co��unica�ion.T�e de-�er�inan�s o���e a�oun� o� s�un�ing are ��e de�ec� size and ��even�ricles rela�ive resis�ance �o in�low. In M�, ��e res�ric�ed in�low leads �o increased dias�olic pressures in ��e le�� ven�ricle.T�is resul�ed in �ar�ed accen�ua�ion o� ��e le��-�o-rig��s�un�. We repor�ed a case o� a 34 years old �e�ale, �irs� ca�e �o Harapan Ki�a Na�ional Cardiac Cen�er, in 2010. ��e was diagnosed wi�� L�, and was planned �o �ave A�� closure and �i�ral valve repair by surgery. However, s�e re�used �o under�a�e ��e procedure. In su��ary, �o illus�ra�e ��e in�erac�ions be�ween A�� and M�, ��e presence o� A�� underes�i�a�ed ��e severi�y o� M�; �eanw�ile ��e exis�ence o� M� �agni�ied ��e le�� �o rig�� s�un� in pa�ien�s wi�� A��.