Lutembacher’s Syndrome An Echocardiographic Assessment (original) (raw)
Related papers
Cardiovascular diagnosis and therapy, 2015
Lutembacher syndrome (LS) is a rare cardiac abnormality characterized by any combination of a congenital or iatrogenic atrial septal defect (ASD) and a congenital or acquired mitral stenosis (MS). Clinical features and hemodynamic effects of LS depend on the balance of effects of the MS and the ASD. Prognosis is influenced by several factors [pulmonary vascular resistance, right ventricle (RV) compliance, size of ASD and MS severity] but the occurrence of secondary pulmonary hypertension and congestive heart failure is commonly associated with poor outcome. Echocardiography remains the gold standard for diagnosis and evaluation of LS. Timely diagnosis is critical for modifying the natural course, by allowing patients to benefit from currently available percutaneous trans-catheter therapies with favorable effects on the outcomes. This article is a review of published literature on the current diagnostic and therapeutic modalities for LS, focusing on the pivotal role of echocardiograp...
A Forty Year Old Lady with Undiagnosed Lutembacher Syndrome - A Case Report
University Heart Journal, 2011
A forty years widow having four children presented with palpitation, shortness of breath on exertion and chest pain. Her sufferings progressively increase in course of time. Her ECG shows complete Right Bundle Branch Block. Transthoracic echocardiography showed atrial septal defect of secundum type. Both the leaflets of the mitral valve were thickened with mild degree of diastolic doming. Key Words: Lutembacher Syndrome; Mitral Stenosis. DOI: 10.3329/uhj.v6i1.7198University Heart Journal Vol.6(1) 2010 pp.51-54
Lutembacher's Syndrome" - A Case Report
Faridpur Medical College Journal, 2011
Lutembacher's Syndrome is a rare heart disease comprises ASD (congenital) secundum with Mitral stenosis (Rheumatic origin). The patient Md. Mosharraf Hossain, 72 years old man, non diabetic, non hypertensive, smoker admitted in FMCH on 10.10.2010 with the complaints of respiratory distress and chest pain for 10 days. He had a previous history of Rheumatic fever in early childhood. There was history of recurrent attack of Rheumatic fever. Subsequently he developed MS from Rheumatic carditis. ASD was congenital in origin. If diagnosis could be done earlier, surgical closure of ASD with replacement of mitral valve bears a good prognostic value. Our patient is in elderly age and already developed pulmonary hypertension, operative procedure is not suitable. So the patient should be kept in conservative treatment. Key words:…
Clinical Medicine And Health Research Journal
Introduction: Lutembacher’s syndrome is a rare clinical entity. In 1916, French physician Rene Lutembacher described his first case of 61 years old woman with a combination of congenital ASD with acquired MS. But he attributed this mitral lesion to congenital mitral stenosis. The definition of this syndrome named after him has undergone many changes since then. The current consensus defines Lutembacher Syndrome (LS) as any combination of ASD (congenital or iatrogenic) and MS (congenital or acquired). The clinical presentation of LS is a result of the interplay between the size of ASD, the severity of MS, pulmonary vascular resistance and RV compliance. Financial constraints also add to the delayed diagnosis and adequate treatment in our part of the world. Here we have discussed a case of LS with severe TR and moderate PAH in congestive cardiac failure which was successfully treated by surgery thereby demonstrating cost-effective and successful surgical management of a rare cardiac d...
Lutembacher’s Syndrome: A Rare Cause of Right Heart Failure
Journal of Cardiovascular Disease Research, 2016
An official publication of Scibiolmed.Org (www.scibiolmed.org), it is a double-blind peer-reviewed, open access international circulating professional journal led by a group of research scientists, vascular disease experts and cardiologists coming from North America, Asia and Europe etc. www.jcdronline.org
Lutembacher's syndrome: a study of 3 cases
International Surgery Journal, 2015
The mitral valve was replaced using TTK Chitra valve and posterior mitral leaflet preservation. ASD is repaired using pericardial patch.
Surgical management of Lutembacher’s syndrome in congestive cardiac failure
Introduction: Lutembacher’s syndrome is rare clinical entity.In 1916, French physician Rene Lutembacher described his first case of 61 years old woman with a combination of congenital ASD with acquired MS. But he attributed this mitral lesion to congenital mitral stenosis. The definition of this syndrome named after him has undergone many changes since then. The current consensus defines Lutembacher Syndrome (LS) as any combination of ASD (congenital or iatrogenic) and MS (congenital or acquired). The clinical presentation of LS is a result of interplay between size of ASD, severity of MS, pulmonary vascular resistance and RV compliance. Financial constraints also add to the delayed diagnosis and adequate treatment in our part of the world.Here we have discussed a case of LS with severe TR and moderate PAH in congestive cardiac failure which was successfully treated by surgery.Case report: A 42 years old thin built, poorly nourished housewife presented with chest discomfort and fati...
Lutembacher syndrome with mitral valve calcification in a 31-year old male
JPMA. The Journal of the Pakistan Medical Association, 2018
Lutembacher syndrome is characterized by a congenital ostium secundum atrial septal defect and an acquired mitral valve stenosis. We present a similar case in a 31-year old male who came in with orthopnoea, central cyanosis and pedal oedema. Examination revealed cardiac murmurs in tricuspid and apical regions. Chest x-ray showed signs of pulmonary congestion and ventricular enlargement. Electrocardiogaphy (ECG) revealed right axis deviation and right bundle branch block along with atrial fibrillation and Transthoracic Echocardiography (TTE) showed abnormal valves (mitral stenosis with calcification and tricuspid regurgitation) and dilated cardiac chambers. The patient was consequently treated with beta-blockers and diuretics and scheduled for valvular and septal repair via open heart surgery. The purpose of this case report is to assist cardiologists in diagnosing this syndrome accurately on the basis of symptoms and investigations.
Variant of Lutembacher's syndrome with intact atrial septum
American Heart Journal, 1994
Lutembacher's syndrome, a cardiac anomaly in which mitral stenosis coexists with an interatrial septal defect (ASD), was first described in 1916.' In this condition, despite significant obstruction to outflow, the left atrium is variably decompressed via a left-to-right shunt created by From the Texas Heart Institute and the Section of Adult Cardiology, St. Luke's Episcopal Hospital.
Severe Iatrogenic Lutembacher Syndrome in a Young Male: Case Report and Literature Review
2021
Iatrogenic Lutembacher's syndrome is a rare combination of acquired Atrial Septal Defect (ASD) after percutaneous mitral commissurotomy (PMC), and Mitral stenosis (MS) (usually of rheumatic nature). Here we discuss the case of a 46 years old male with MS who had undergone successful PMC seven years ago, who complained from gradually progressive exertional dyspnea, fatigue and palpitations. On detailed examination and investigation, he was found to be having Lutembacher's syndrome confirmed by echocardiography. After concertation with the heart team, the patient was managed by valvular surgery. Keeping in mind this syndrome rare occurrence, we are presenting an overview of this syndrome, through a literature review, including its various aspects and the challenges faced by the patients and the physicians in the context of developped countries.