Combined Percutaneous Procedure in Patient with Lutembacher Syndrome: A Case Report and Real-World Experience Review (original) (raw)
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Successful percutaneous management of Lutembacher syndrome
Indian heart journal
The surgical management of Lutembacher syndrome is straight forward but percutaneous management, though technically demanding, is always desirable. A 17 year old unmarried female presented with severe Mitral stenosis and a 19 mm almost circular Ostium secundum ASD with moderate pulmonary artery hypertension and dilated right sided chambers. She was managed in a staged manner. Percutaneous trans mitral commissurotomy (PTMC) was done first, using a 26 mm Inoue balloon catheter set, and after 48 h, ASD was closed with a 20 mm Cocoon Septal Occluder. The mitral valve area increased after PTMC from 0.8 cm2 to 2.1 cm2 and QP/QS decreased from 4.9 to 2. ASD was successfully closed under echocardiographic and fluoroscopic guidance. Percutaneous management of the Lutembacher syndrome (PTMC and ASD device closure) is an effective and low risk procedure and avoids considerable morbidity and mental trauma for the patients.
Clinical Medicine And Health Research Journal
Introduction: Lutembacher’s syndrome is a rare clinical entity. In 1916, French physician Rene Lutembacher described his first case of 61 years old woman with a combination of congenital ASD with acquired MS. But he attributed this mitral lesion to congenital mitral stenosis. The definition of this syndrome named after him has undergone many changes since then. The current consensus defines Lutembacher Syndrome (LS) as any combination of ASD (congenital or iatrogenic) and MS (congenital or acquired). The clinical presentation of LS is a result of the interplay between the size of ASD, the severity of MS, pulmonary vascular resistance and RV compliance. Financial constraints also add to the delayed diagnosis and adequate treatment in our part of the world. Here we have discussed a case of LS with severe TR and moderate PAH in congestive cardiac failure which was successfully treated by surgery thereby demonstrating cost-effective and successful surgical management of a rare cardiac d...
Surgical management of Lutembacher’s syndrome in congestive cardiac failure
Introduction: Lutembacher’s syndrome is rare clinical entity.In 1916, French physician Rene Lutembacher described his first case of 61 years old woman with a combination of congenital ASD with acquired MS. But he attributed this mitral lesion to congenital mitral stenosis. The definition of this syndrome named after him has undergone many changes since then. The current consensus defines Lutembacher Syndrome (LS) as any combination of ASD (congenital or iatrogenic) and MS (congenital or acquired). The clinical presentation of LS is a result of interplay between size of ASD, severity of MS, pulmonary vascular resistance and RV compliance. Financial constraints also add to the delayed diagnosis and adequate treatment in our part of the world.Here we have discussed a case of LS with severe TR and moderate PAH in congestive cardiac failure which was successfully treated by surgery.Case report: A 42 years old thin built, poorly nourished housewife presented with chest discomfort and fati...
Lutembacher’s Syndrome in a young female treated Surgically: A Case Report
Bangladesh Heart Journal
Lutembacher’s syndrome is a rare clinical condition presenting with a combination of congenital atrial septal defect (ASD) and acquired mitral stenosis (MS). Lutembacher’s syndrome is more prevalent in developing countries and its prevalence depends on the prevalence of rheumatic fever in that geographical area. The syndrome can present at any age but is usually more commonly observed in young female adults. Echocardiography remains the gold standard for diagnosis and evaluation of Lutembacher’s syndrome (LS). Now a days many treatment options are available for LS – either percutaneous intervention or surgical correction. But pericardial patch closure of atrial septal defect and prosthetic mitral valve replacement is the treatment of choice for Lutembacher’s syndrome. Bangladesh Heart Journal 2022; 37(2): 143-147
Transcatheter Device Closure of Secundum Atrial Septal Defect in Adult Patient
Acta Informatica Medica, 2021
Background: Atrial septal abnormalities are common congenital lesions remaining asymptomatic until adulthood in a great number of patients. The most frequent atrial septal defects in adults are ostium secundum atrial septal defect (ASD). Complications from untreated, hemodynamically significant ASD are atrial arrhythmia, paradoxical embolization, Eisenmenger's syndrome, pulmonary hypertension, and right ventricular failure. Objective: We present a case report of secundum ASD in adult female patient who underwent transcatheter device closure with Amplatzer occluder. Methods and Results: The case of female Bosnian patient 50 years old who lives in Belgium for 20 years ago and during her visit to Bosnia she came to our polyclinic for cardiological exam. Echocardiographic exam showed enlargement of left atrium (LAD 51mm), right atrium and ventricle (RAD 46mm, RVd 33mm), atrial septal defect 9mm with left right shunt Qp:Qs 2,3:1. Several months later transcatheter device closure with Amplatzer occluder was performed and subsequent symptomatic improvement reported after closure. Conclusion: Echocardiography has superior role for precise evaluation of ASD type secundum who are suitable for transcatheter device closure as primary treatment option. Transcatheter techniques has now become preferable to surgical repair and provide valid option of treatment for this type of CHD.
Severe Iatrogenic Lutembacher Syndrome in a Young Male: Case Report and Literature Review
2021
Iatrogenic Lutembacher's syndrome is a rare combination of acquired Atrial Septal Defect (ASD) after percutaneous mitral commissurotomy (PMC), and Mitral stenosis (MS) (usually of rheumatic nature). Here we discuss the case of a 46 years old male with MS who had undergone successful PMC seven years ago, who complained from gradually progressive exertional dyspnea, fatigue and palpitations. On detailed examination and investigation, he was found to be having Lutembacher's syndrome confirmed by echocardiography. After concertation with the heart team, the patient was managed by valvular surgery. Keeping in mind this syndrome rare occurrence, we are presenting an overview of this syndrome, through a literature review, including its various aspects and the challenges faced by the patients and the physicians in the context of developped countries.
Cardiovascular diagnosis and therapy, 2015
Lutembacher syndrome (LS) is a rare cardiac abnormality characterized by any combination of a congenital or iatrogenic atrial septal defect (ASD) and a congenital or acquired mitral stenosis (MS). Clinical features and hemodynamic effects of LS depend on the balance of effects of the MS and the ASD. Prognosis is influenced by several factors [pulmonary vascular resistance, right ventricle (RV) compliance, size of ASD and MS severity] but the occurrence of secondary pulmonary hypertension and congestive heart failure is commonly associated with poor outcome. Echocardiography remains the gold standard for diagnosis and evaluation of LS. Timely diagnosis is critical for modifying the natural course, by allowing patients to benefit from currently available percutaneous trans-catheter therapies with favorable effects on the outcomes. This article is a review of published literature on the current diagnostic and therapeutic modalities for LS, focusing on the pivotal role of echocardiograp...