Demography and etiology of congenital sensorineural hearing loss in children (original) (raw)
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PARIPEX INDIAN JOURNAL OF RESEARCH, 2023
Objective: Hearing dysfunction is the most common sensory deficit in children. If hearing is lost, especially in children's, it may have a huge impact on life, interfering with the acquisition of spoken language and social development. It is therefore important to detect any abnormalities at an early age. Patients with complaint of inability to hear since birth attending ENT OPD, M.Y.H Hospital, Indore and patients referred to M.Y.H hospital from district hospitals with inability to hear since birth were evaluated clinically and audiometry was done. Patients with SNHL fulfilling the inclusion criteria were considered and their radiological evaluation was done. High resolution computed tomography scan (HRCT) of temporal bone were used in radiological evaluation of patients with congenital sensorineural. SUBJECTS AND METHODS: The study was conducted at a tertiary care centre Maharaja Yashwantrao Holkar (MYH) hospital and Mahatma Gandhi Memorial Medical College (MGMMC), Indore in the Department of otorhinolaryngology and head & neck surgery. Cases with hearing loss from 1 to 16 years of age were selected. A detailed medical history with primary focus on inability to hear was obtained with emphasis on previous hospital stays, developmental delay, maternal history, family history. Complete ENT examination was done. Our study included a total 30 children. All children were Results: between 1-16 years of age with sensorineural hearing loss. Majority 11(36.67%) of the participated in the study were between 5-8 years of age. Cochlear anomaly was found in 03(10%) patients. Cochlea was found normal in 27(90%) on both the ears, 03(10%) child had hypoplastic cochlea bilaterally, none were with aplastic cochlea. Vestibular anomaly was seen normal in 28(93.33%) patients on bilateral side. 02(6.67%) patients were present with dysplastic vestibule. SSC was found dysplastic/malformed in 04(13.33%) patients who had dysplastic/malformed semicircular canal. Conclusion: The selection of candidates for hearing aid trials and cochlear implantation requires consideration of a variety of clinical, audiological and radiological factors. Imaging is a fundamental part of the preoperative workup, it provides the surgeon with details which will lead him to a successful cochlear implantation with no or minimal complications. HRCT temporal bone provided us the information about the presence of various inner ear malformations including cochlea, vestibule, SCC, IAC. Mastoid, pneumatization, variations in vascular anatomy which included forward lying sigmoid sinus and high riding jugular bulb. All these findings are important for a detection of cause of SNHL in patients.
Jurnal Ilmu Kesehatan, 2020
Sensorineural Hearing Disorder in children could give a significant impact on everyday life and would cause loneliness, isolation, and frustration on children. Perinatal risk factors are important to note because they could be detected from newborn and could be an indication for the baby to do the screening. The purpose of hearing screening in newborns is to find hearing loss as early as possible so that habilitation can be done immediately. The purpose of this study was to describe perinatal period as risk factors for Sensorineural Hearing Disorder in children. The subjects of this study were children who has done BERA examinations at the Otolaryngology (ENT) Polyclinic of Abdul Wahab Sjahranie Hospital in Samarinda from January 2017 – June 2019. The design of this study was observational descriptive with cross-sectional method. There were 65 children as sample which consisted of 39 (60%) boys and 26 (40%) girls. BERA examination age that was found in this study has not reached the...
Present Scenario of Childhood Deafness: A Tertiary Level Health Care Study
Bengal Journal of Otolaryngology and Head Neck Surgery, 2017
Introduction Hearing loss is the most common sensory deficit in humans today. Approximately 63 million people in India suffer from significant auditory impairment. Materials and Methods Fifty children of 0-7 years age group, presented to a tertiary level center in Kolkata were assessed by objective and behavioural audiological tests. Result Mean age of presentation was found to be 40.5 months. No risk factor could be identified in 72% of the cases. 47% fell into the profoundly deaf category. Discussion Numerous studies agree that half of the infants with sensorineural hearing loss have no risk factors at birth and thus would be missed by a targeted hearing screening. Conclusion India certainly faces a worse situation regarding childhood deafness. Implementation of universal neonatal hearing screening along with pre-school hearing assessment can certainly change the scenario.
Journal of the Medical Association of Thailand = Chotmaihet thangphaet
To determine incidence and risk factors associated with hearing loss in high-risk neonates in Srinagarind Hospital. Prospective cohort study. High-risk neonates were screened with TEOAE/AABR. All infants were followed for hearing and developmental evaluation until one year of age. Four hundred twenty five neonates underwent hearing screening tests. Nine infants (2.1%) had abnormal TEOAE, AABR and ABR tests. During follow-up, two of the nine infants that had abnormal initial hearing tests were found to have normal hearing at eight and nine months of age. Therefore, seven high-risk neonates (1.6%) had permanent hearing loss. Significant risk factors for permanent hearing loss were craniofacial anomalies, very low birth weight, low Apgar scores at 5 minute and mechanical ventilation usage for more than five days. Continuing evaluation of hearing and development during follow-up is important in children with abnormal hearing tests. Invasive procedures as early intervention during the fi...
The Potential Risk Factors and the Identification of Hearing Loss in Infants
Indian Journal of Otolaryngology and Head & Neck Surgery, 2011
To identify potential risk factors for hearing loss from the infant with high risk criteria as guided by the Joint Committee on Infant Hearing (JCIH, 2000). 490 infants with age range of 2 days to 6 months who had undergone detailed audiological evaluation during for the period of 3 years at Gauhati Medical College Hospital were taken for the study. The hearing screening was performed on each infant using Distortion Product Otoacoustic Emission (DPOAE) testing. The infants who failed DPO-AEs screening were followed up and Auditory Brainstem Response testing. Out of 490 high risk infants who had undergone detailed audiological evaluation 145 infants were found to be having hearing loss. Out of 145 infants 73 infants were male and 72 infants were female. The risk factor for hearing loss with the highest incidence was hyperbilirubenemia, Apgar scores of 0-4 at 1 min or 0-6 at 5 min was the second most prevalent risk factor, followed by TORCH infections. This study suggests the need for review of high risk register that is used along with the physiological and electrophysiological hearing test to screen the infants. The high risk register remains helpful in determining follow up plans so that children who may develop late onset of hearing loss will not be missed. Being aware of which risk factors are more likely to cause hearing loss in infants would be helpful to plan for follow up these children.
INTRODUCTION Interpersonal communication, day to day activities, learning language and acquiring grades in the school are important parts in the life of school going children. Unilateral or bilateral Loss of hearing affects education and the child feels handicapped socially, emotionally, and scholastically. Such children lose grades and retained in the same class affecting them emotionally. The present study was conducted in order to find out the various causes of unilateral Sensorineural Hearing Loss (USNHL) in children and to study role of various audiological findings in diagnosing the cause of impaired hearing in children.
Hearing status of children under five years old in Jatinangor district
2020
Background: Hearing is one of the most influential factors in children developmental process. The critical period of hearing and speech development begins in the first 6 months of life and continues until the age of 3 years. World Health Organization estimates that one to three in a thousand births have sensorineural hearing loss (SNHL). Early detection of hearing loss is substantial so that the diagnosis can be established and appropriate intervention can be done earlier. Purpose: To determine the hearing status in children under five years of age in Jatinangor. Method: A cross-sectional observational study with 240 subjects under the age of five in 12 Integrated Healthcare Center (Posyandu) in Jatinangor. Examinations included parental interviews, Behavioral Observation Audiometry (BOA), Otoacoustic Emissions (OAE), and tympanometry tests. Result: One child (0.4%) had moderate conductive hearing lossin the left ear, 1 child (0.4%) had bilateralsevere SNHL, and 7 children (2.9%) ha...
International Journal of Pediatric Otorhinolaryngology, 2009
Objective: To determine the characteristics of infants with sensorineural hearing loss (SNHL) and the relationship with place of birth. Methods: Subjects were drawn from hospital-based and community-based universal infant hearing screening programs concurrently conducted from May 2005 to April 2008 in Lagos, Nigeria. Maternal and infant characteristics of children born in hospitals and detected with SNHL were compared with those born outside hospitals. Each program consisted of a first-stage screening with transient-evoked otoacoustic emissions (TEOAE) followed by second-stage automated auditory brainstem response (AABR). Hearing status was confirmed by diagnostic auditory brainstem response, tympanometry and visual response audiometry. Results: A total of 4718 infants were screened under the hospital-based program out of which 12 (0.3%) infants were confirmed with SNHL whereas 71 (1.0%) of the 7179 infants screened under the community-based program were confirmed with SNHL. Of all infants with SNHL 39 (47.0%) were born in hospitals suggesting that 27 (38.0%) of infants under the community-based program were born in hospitals. Prevalence of SNHL ranged from 4.0 per 1000 among infants born in government hospitals to 23 per 1000 among those born in family homes. Mothers of those born outside hospitals were significantly likely to belong to the Yoruba tribe (p < 0.001), use herbal medications in pregnancy (p < 0.001), deliver vaginally (p = 0.004) but without skilled attendants at delivery (p < 0.001). There were no significant differences among the infants themselves except that those born outside hospitals were significantly likely to be detected in the first 3 months of life compared to those born in hospitals (p < 0.001). Conclusions: A significant proportion of infants with SNHL in many developing countries are likely to be born outside hospitals thus underscoring the need for community-oriented UNHS to facilitate early detection and intervention. Conventional risk factors for SNHL are unlikely to discriminate across places of birth. Pediatricians and otolaryngologists should consider a more active role in fostering communityoriented delivery of primary ear care services in this and similar settings in the developing world.
Syndromic Deafness- Prevalence, Distribution and Hearing management Protocol in Indian Scenario
Annals of Medicine and Surgery, 2015
Background: The estimated prevalence of Sensory Neural Hearing Loss (SNHL) in patients less than 18 years of age is 6 per 1000. Roughly 50% of cases of congenital SNHL can be linked to a genetic cause, with approximately 30% being syndromic and the remaining 70% being non-syndromic. The term "syndromic" implies the presence of other distinctive clinical features in addition to hearing loss. The aim of our study was to find the distribution of various Syndromic associations in patients with profound deafness, presented at Madras ENT Research foundation, Chennai and to formulate a management protocol for these patients and to discuss in detail about the clinical features of commonly encountered syndromic deafness. Materials and methods: Our retrospective study was aimed at describing the various Syndromic associations seen in patients with congenital profound deafness. Information was collected from the medical records. At our centre all patients undergo a comprehensive evaluation. The distribution, etiological factors and management protocol for various syndromes are here presented. Results: Out of 700 patients with congenital profound deafness all patients with Syndromic associations (n ¼ 35) were studied. 5% of profoundly deaf candidates were found to be syndromic. Most common syndrome in our series was found to be congenital rubella syndrome followed by Jervell and Lange-Nielsen syndrome. Conclusion: Congenital deafness is an associated feature of many syndromes. Detailed history taking with comprehensive evaluation is mandatory to rule out the associated syndromes. Diagnosis must be confirm by a genetic study. Multidisciplinary approach is essential for appropriate diagnosis and management.