Hearing outcome after surgical intervention in fibrous dysplasia of temporal bone (original) (raw)
Related papers
Fibrous dysplasia of the temporal bone secondary to ear surgery: a case report
Journal of Medical Case Reports, 2015
Introduction: In this report, we describe the clinical course, diagnostic features and management of a patient with fibrous dysplasia of the temporal bone 7 years after middle ear surgery on the same side. Case presentation: A 16-year-old Caucasian girl presented to our hospital with a growing bone lesion in the roof of the left temporal bone. She had undergone a previous tympanoplasty at 7 years of age because of a cholesteatoma. At the time of that first surgery, no radiological or histological signs indicated a bone disorder. A computed tomographic scan of the temporal bone showed a lesion with rarefaction areas and lytic images inside that affected the roof of the cavity to the tegmen tympani without alterations in the inner ear. A surgical revision of the ear cavity was performed by resecting the lesion and regularizing the cavity. The histopathologic study confirmed fibrous dysplasia. The patient progressed satisfactorily after surgery with no evidence of recurrence. Conclusion: To the best of our knowledge, this is the first report of fibrous dysplasia of the temporal bone secondary to ear surgery.
External auditory canal stenosis due to isolated fibrous dysplasia of temporal bone: a case report
International Journal of Otorhinolaryngology and Head and Neck Surgery, 2019
Benign disease of bone marrow in which marrow is reorganize into fibrous tissue and immature woven bone, is known as fibrous dysplasia. Involvement of temporal bone is rare and can be isolated or in monostotic or polystotic form with various otologic manifestations. We are here reporting a case of fibrous dysplasia of the unilateral temporal bone who presented with hearing loss and stenosis of the external auditory canal. External auditory canal stenosis due to fibrous dysplasia was managed with canalplasty and patient was free of recurrence till last follow up. Fibrous dysplasia of isolated temporal bone is a rare entity which requires high grade of suspicion in a patient who presents with unusual bony swellings in the ear. Its management usually includes resection of the most affected part of temporal bone in order to achieve auditory canal patency and restoration of hearing. After surgery, a close follow up is warranted due to its propensity of recurrence.
A Case Report-Fibrous Dysplasia of Temporal Bone
Research in Medical & Engineering Sciences
We present a case of 35 year old female with monotonic fibrous dysplasia which presented to us with blocked sensation, impaired hearing, and Discharge right ear with mass in the right mastoid region for the last one year. Main complaint of the patient was decreased hearing and found to be conductive hearing loss. Computed tomography showed diffusely expanded right temporal bone/mastoid, petro us parts and EAC with increased bone density. Patient underwent surgery for contouring of bone and canalplasty which improved hearing status, blocking sensation and discharge completely. Although there was cosmetic deformity but patient was not concerned regarding that, which also improved. Patient is under regular follow-up with very good functional and cosmetic results. From his case report, we learn the importance of conservative surgery and regular follow up in few selective cases of temporal bone fibrous dysplasia.
Fibrous dysplasia: rare manifestation in the temporal bone
Brazilian Journal of Otorhinolaryngology, 2020
Introduction: Fibrous dysplasia is a benign disorder, in which normal bone is replaced by fibrosis and immature bone trabeculae, showing a similar distribution between the genders, and being more prevalent in the earlier decades of life. Fibrous dysplasia of the temporal bone is a rare condition, and there is no consensus as to whether it is more common in monostotic or polyostotic forms. External auditory meatus stenosis and conductive dysacusis are the most common manifestations, with cholesteatoma being a common complication, whereas the involvement of the otic capsule is an unusual one. Surgical treatment is indicated to control pain or dysacusis, otorrhea, cholesteatoma, and deformity. Objectives: To describe the clinical experience of a tertiary referral hospital with cases of fibrous dysplasia of the temporal bone. Methods: Sampling of patients diagnosed with fibrous dysplasia of the temporal bone, confirmed by tomography, treated at the pediatric otology and otorhinolaryngology outpatient clinics, between 2015 and 2018. The assessed variables were age, gender, laterality, external auditory meatus stenosis, deformity, hearing loss, presence of secondary cholesteatoma of the external auditory meatus, lesion extension and management. Results: Five patients were included, four females and one male, with age ranging from 13 to 34 years. Three had the polyostotic form and two the monostotic form of fibrous dysplasia of the temporal bone. Four patients had local deformity and external auditory meatus stenosis, two of which progressed to cholesteatoma. All patients showed some degree of hearing impairment. All had preserved otic capsule at the tomography. Two patients are currently undergoing clinical observation; two were submitted to tympanomastoidectomy due to secondary cholesteatoma; one was submitted to lesion resection, aiming to control the dysacusis progression.
American Journal of Roentgenology, 1994
Because of its superior visualization of bone detail, compared with that of MR imaging, CT commonly is used in patients who have had otomastoid or other forms of temporal bone surgery. The already complex anatomy of the temporal bone is distorted by the combination of surgical procedures and preexisting abnormalities, making proper identification of the postoperative Imaging studies difficult. The purpose of this essay is to familiarize radiologists with the more common neurootologic surgical procedures and the expected postoperative findings in patients who have had this type of surgery. Special emphasis is placed on the indications for the procedure and the distinguishing features associated with each procedure.
Indian Journal of Otolaryngology and Head & Neck Surgery, 2010
Suboccipital retrosigmoid craniotomy with removal of posterior wall of internal auditory canal is preferred by many surgeons operating on acoustic neuromas, as it is a simple and safe approach. To study the topographic landmarks of the posterior surface of the temporal bone. We studied the surgical anatomy of 224 dry adult human temporal bones, measured the various distances on posterior wall of petrous bone relevant for suboccipital surgical approach to internal auditory canal. The internal auditory canal (IAC) lies within 32-44 mm from posterior wall of sigmoid sulcus and within 3-8 mm from the superior border of petrous bone. The point corresponding to highest point of jugular bulb was found between 4 and 9 mm away from the inferior border of IAC. The maximum distance found between bony orifice of vestibular aqueduct and IAC was 14 mm and the minimum distance was 6 mm.The vertical diameter of IAC ranged between 3 and 7 mm. These parameters may help the surgeons for better exposure of internal auditory canal and for avoiding damage to vital surrounding structures.
Fibrous dysplasia of the temporal bone: report of a case and a review of its characteristics
Ear, nose, & throat journal, 2000
Fibrous dysplasia is an uncommon benign disorder of unknown etiology. It represents a disturbance of normal bone development--specifically a defect in osteoblastic differentiation and maturation that originates in the mesenchymal precursor of the bone. Because fibrous dysplasia shows a predilection for the facial and cranial bones, where it causes deformity and dysfunction, the disease is of particular interest to the otolaryngologist. In this paper, we report a case of fibrous dysplasia of the temporal bone, the first symptom of which was a mixed hearing loss. We discuss the characteristic features of this specific location of the disease, the differential diagnosis, and the treatment policy. We also address the issue of secondary sensorineural hearing loss.
High resolution computed tomography of temporal bone in the evaluation of otologic diseases
International Journal of Otorhinolaryngology and Head and Neck Surgery, 2017
HRCT is particularly helpful in evaluating the anatomy and pathology of external auditory canal, middle ear cavity, vestibular aqueduct, tegmen tympani, sigmoid sinus plate, vertical segment of facial nerve canal, sinodural angle, carotid canal, jugular fossa, infra and supralabrynthine air cells and temporomandibular joint; both soft tissue extension and significantly sensitive ABSTRACT Background: Conventional radiological methods like X-ray mastoid have limited ability to delineate the details of the complex temporal bone and cochlea-vestibular anatomy and disease pathology. This can be overcome by the use of High resolution computed tomography (HRCT) evaluation of the temporal bone. HRCT is helpful in evaluating the anatomy and pathology type and extent of disease, thereby helps in preoperative planning. Methods: The CT scan of forty five patients attending the outpatient department of otorhinolaryngology in a tertiary care centre between August 2014 to August 2017 was evaluated in this study. Each CT scan was interpreted by an otolaryngologist and a radiologist and interpretation was by consensus. The data collected was evaluated and results are reported as rates and proportions (%). Results: The study evaluated CT scan of 45 patients of which 35 were male patients and 10 were female patients with age ranging from 5 years to 75 years. Most of these patients belonged to the 21-30, 31-40 age groups [9 (20%) in each group]. Infections of middle ear cleft (all with cholesteatoma), fractures of the temporal bone, anomalies and tumors of the external auditory canal and middle ear were the pathologies observed in these CT scans with infection (otomastoiditis) [23 (51.1%)] being the most common pathology observed. Conclusions: Pre-operative CT scan may not only help in identifying the nature, extent of infectious disease including ossicular, bony erosions; it may also identify anomalies in the temporal bone and surrounding structures. Thus, HRCT temporal bone will help the surgeon in planning effective surgical strategy, reducing morbidity during the surgery.
Sensory neural hearing loss following Tympano-mastoid surgery
Objective: Generated acoustic trauma by suction and drill may cause sensorineural hearing loss after Tympanomastoid surgery. This study was carried out to determine the relationship of sensorineural hearing loss and chronic otitis media surgery at Ahvaz Jundishapur University of Medical Sciences in Iran. Material and Methods: This prospective study included 386 patients of chronic middle ear disease, which were surgically treated at the department of Otolaryngology of Imam Khomeini and Apadana hospitals in Ahvaz, fromMarch 2008 to March 2011. Drilling duration of tympanomastoid surgery was 26.1±15.5 minutes. The preoperative and postoperative bone conduction thresholds in frequencies 250 to 4000 HZ were obtained one day before and 6-8 weeks after the surgical procedure by one expert audiologist. Result: A total of 386 patients was included in this study. Among them 267 (69.17%) were female and 119(30.83%) of them were male. The patients ranged in age from 6 to 68 years with a mean of 26.15 years. Statistically significant deterioration in bone conduction thresholds was found only with radical mastoidectomy. There was no change in mean bone conduction thresholds in 319 (82.6%) of patients. A total of 38 (9.8%) patients showed worsening of postoperative bone conduction thresholds. Conclusion: Our study has shown that the middle ear surgery in chronic otitis media in majority of the patients does not affect bone conduction thresholds. It is suggested that all ENT surgeons should do chronic otitis media surgery without being worried, but must take all the precaution.