Radiotherapy in congenital vulvar lymphangioma circumscriptum (original) (raw)

Lymphangioma circumscriptum of the vulva treated with radiofrequency ablation: case report

Mucosa, 2020

Lymphangioma circumscriptum (LC) is a rare benign skin disease involving hamartomatous lymphatic malformation of the deep dermal and subcutaneous lymphatic ducts. Upon occuring in uncommon areas such as axilla, shoulder, groin, and vulva, it is a therapeutic challenge for the dermatologist. Various methods such as surgical excision, lasers, and sclerotherapy have been used in the past to treat this unsightly skin condition. In this article we report the efficacy of a radiofrequency ablation in a female patient with vulvar LC. The treatment efficiency of radiofrequency was satisfactory in our patient without recurrence during the 6-month follow-up period. Based on previous studies, radiofrequency technique is a safe and cost-effective treatment for LC management, as in our case.

Congenital lymphangioma circumscriptum of the vulva

Indian Pediatrics, 2009

Lymphangioma circumscriptum of the vulva is a disorder of lymphatic channels involving deep dermal tissues. Most of these cases are confused with genital warts leading to improper diagnosis and treatment. We present a three years young female child who had multiple skin colored papular lesions over the genitals. Skin biopsy revealed features of lymphangioma circumscriptum.

Acquired vulvar lymphangioma circumscriptum: a comparison of 12 cases with Crohn's associated lesions or radiation therapy induced tumors

Journal of Cutaneous Pathology, 2010

Vulvar lymphangioma circumscriptum (LC) is a rare entity which may present as a painful, warty lesion. In contrast to the congenital form, which occurs in children, the acquired form arises in older adults and may be associated with infection, Crohn's disease, or prior pelvic/regional surgery. We present a case of acquired LC of the vulva in a 55-year-old woman who presented with a 3-4 year history of vulvar pain following chemotherapy, radiation, and brachytherapy for cervical cancer. Vulvar shave biopsies followed by excision revealed a thickened dermis with epidermal hyperkeratosis, parakeratosis, elongated rete ridges and dilated lymphatic channels containing eosinophilic material and scattered thrombi. The differential diagnosis for this unusual lesion includes more common conditions such as condyloma acuminatum, fungating squamous cell carcinoma and molluscum contagiosum. It is important to recognize the clinical presentation as well as the distinct histological appearance of this rare benign entity.

Report of 4 cases of vulvar lymphangioma: an update

Obstetrics & Gynecology International Journal

Vulvar Lymphangioma is an infrequent pathology. There are few cases published in the English literature. We present 4 new cases of vulvar lymphangioma (1 acquired and 3 congenital) treated at the vulvar section of Hospital Italiano de Buenos Aires. It represents a challenge for clinicians because of its rarity. The main differential diagnosis is genital warts. This disease has cosmetic and psychosexual implications in the patients; therefore surgery with a cosmetic approach is the recommended treatment. Labiaplasty of labia majora and laser CO2 vaporization have similar success and recurrence rates. Conservative management (observation) is a valid option if the patient is asymptomatic.

Lymphangioma circumscriptum of the vulva: Report of a rare case

Journal of Mid-life Health, 2015

Lymphangioma circumscriptum (LC) is a form of lymphangioma characterised by benign dilation of lymphatic channels, which affects the skin and subcutaneous tissues. The most common sites of LC are mucosa of mouth, tongue, groin, axilla, trunk and proximal region of extremities. Vulva is a rare site of LC. In this report, we are presenting a case of LC of vulva occurring in a 60-year-old female without any obvious reason. The patient presented with multiple genital wart-like papular lesions in the vulva. Biopsy of lesion reveals LC. She was treated with vulvectomy and showed no sign of recurrence till date.

Acquired Vulvar Lymphangioma Circumscriptum

Case Reports in Dermatological Medicine, 2013

Lymphangioma circumscriptum (LC) is a benign dilation of lymph channels localized to the skin and subcutaneous tissues. It is generally localized in mouth mucosa, tongue, proximal regions of arms and legs, groin, axilla, and trunk. Primary vulvar involvement is very rare. Vulvar involvement occurs in various clinical settings. Here, two uncommon cases with giant lymphangioma circumscriptum mimicking genital warts will be presented: a 55-year-old female patient with extensive lymphangiectasic lesions and genital wart-like papular lesions in the vulva secondary to diffuse scrofuloderma scars and a 60year-old female patient with verruca-like lesions secondary to chronic inflammation.

Acquired vulvar lymphangioma: Report of two cases

Journal of General-Procedural Dermatology & Venereology Indonesia, 2016

Vulvar lymphangioma is a rare case and often being misdiagnosed as genital wart. This acquired disorder manifests as dilatation of superficial lymph vessel due to obstruction. It is caused by urogenital infection and most often occurs following surgery and radiotherapy of cervical cancer. The diagnosis is established based on clinical and histopathological features. Treatment aimed to eliminate the cause of obstruction. This article reports two cases of vulvar lymphangioma found in our Hospital. Kelainan yang mendasari lesi kulit pada kedua kasus adalah dilatasi pembuluh limfe superfisial dermis vulva. Sumbatan pembuluh limfe akibat radiasi dan operasi kanker serviks pada kasus 1 dan sumbatan pada kelenjar getah bening inguinal pada kasus 2, menyebabkan peningkatan tekanan pembuluh limfatik dermis. Beberapa modalitas terapi untuk menghilangkan lesi diharapkan memberi hasil akhir yang baik secara kosmetis, mencegah kekambuhan, dan infeksi. Tatalaksana pada kedua kasus menggunakan bedah listrik memberikan respon baik, namun perlu waspada adanya kekambuhan.

Vulval lymphangiectasia: 2 case reports

International Journal of Reproduction, Contraception, Obstetrics and Gynecology, 2017

Vulval lymphangiectasia is a rare cutaneous condition of lymphatic channels in deep dermal and subcutaneous layers. It can be congenital condition or might develop secondary to tuberculosis, surgery, radiotherapy, crohn’s disease etc. Very few cases have been reported in the literature so far. Diagnosis is mainly clinical aided with histopathology. Various treatment modalities are available for this condition. Surgical treatment is the most commonly used method to treat vulvar lymphangiectasia and has offered promising results. In this report, we present 2 cases of vulval lymphangiectasia- one congenital case and other acquired after tuberculosis.