The Hepatic Fibrocystic Diseases (original) (raw)

Clinics in Liver Disease, 2006

Abstract

The hepatic fibrocystic diseases present with variable intrahepatic biliary abnormalities, which range from portal tract enlargement and fibrosis to cystic formations. They may present as autosomal recessive or dominant polycystic kidney diseases, with associated dilatation of the renal collecting system, or as incompletely characterized cystic diseases. Symptoms from the liver disease often result from complications of fibrosis or dilated ducts/cyst (sludge, lithiasis, infection). The treatment is supportive, with careful attention to associated renal disease. Liver transplantation is an option in selected patients.

Frederick Suchy hasn't uploaded this paper.

Let Frederick know you want this paper to be uploaded.

Ask for this paper to be uploaded.