Altered Ca2+ concentration, permeability and buffering in the myofibre Ca2+ store of a mouse model of malignant hyperthermia (original) (raw)

Malignant hyperthermia susceptibility arising from altered resting coupling between the skeletal muscle L-type Ca2+ channel and the type 1 ryanodine receptor

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Gene Dose Influences Cellular and Calcium Channel Dysregulation in Heterozygous and Homozygous T4826I-RYR1 Malignant Hyperthermia-susceptible Muscle

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Role of Malignant Hyperthermia Domain in the Regulation of Ca2+ Release Channel (Ryanodine Receptor) of Skeletal Muscle Sarcoplasmic Reticulum

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Intracellular calcium homeostasis in human primary muscle cells from malignant hyperthermia-susceptible and normal individuals. Effect Of overexpression of recombinant wild-type and Arg163Cys mutated ryanodine receptors

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Sarcoplasmic reticulum Ca2+ release and depletion fail to affect sarcolemmal ion channel activity in mouse skeletal muscle

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A possible role of sarcoplasmic Ca2+ release in modulating the slow Ca2+ current of skeletal muscle

D. Feldmeyer

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Evidence for a role of C-terminus in Ca2+ inactivation of skeletal muscle Ca2+ release channel (ryanodine receptor)

Daniel Pasek

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Sarcoplasmic reticulum lumenal Ca2+ has access to cytosolic activation and inactivation sites of skeletal muscle Ca2+ release channel

Ashutosh Tripathy

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Hypernitrosylated ryanodine receptor calcium release channels are leaky in dystrophic muscle

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Mechanism of chloride-dependent release of Ca2+ in the sarcoplasmic reticulum of rabbit skeletal muscle

Manana Sukhareva

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The CaV 1.2 Ca2+ channel is expressed in sarcolemma of type I and IIa myofibers of adult skeletal muscle

Zhen Yan

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Alteration of intracellular Ca2+ transients in COS-7 cells transfected with the cDNA encoding skeletal-muscle ryanodine receptor carrying a mutation associated with malignant hyperthermia

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Postulated role of interdomain interactions within the type 1 ryanodine receptor in the low gain of Ca2+-induced Ca2+ release activity of mammalian skeletal muscle sarcoplasmic reticulum

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Intracellular Ca2+ dynamics in malignant hyperthermia and central core disease: established concepts, new cellular mechanisms involved

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Ca2+ Signaling in HEK-293 and Skeletal Muscle Cells Expressing Recombinant Ryanodine Receptors Harboring Malignant Hyperthermia and Central Core Disease Mutations

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Selectively Suppressed Ca2+-induced Ca2+Release Activity of α-Ryanodine Receptor (α-RyR) in Frog Skeletal Muscle Sarcoplasmic Reticulum

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Enhanced dihydropyridine receptor calcium channel activity restores muscle strength in JP45/CASQ1 double knockout mice

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Comparison of properties of Ca2+ release channels between rabbit and frog skeletal muscles

Nagomi Kurebayashi

Muscle Physiology and Biochemistry, 1999

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Robyn Murphy

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Regulation of Ca2+ release from internal stores in cardiac and skeletal muscles

Antoni Wrzosek

Acta Biochimica Polonica, 2000

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Effect of Calstabin1 Depletion on Calcium Transients and Energy Utilization in Muscle Fibers and Treatment Opportunities with RyR1 Stabilizers

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