Fibrolipomatous hamartoma in the median nerve in the arm - an unusual location but with MR imaging characteristics: a case report (original) (raw)
Related papers
Journal of Evolution of medical and Dental Sciences, 2015
Fibrolipomatous hamartoma is an uncommon congenital disorder, which is characterized by disproportionate hyperplasia of adipose tissue infiltrating along the perineurium, the epineurium and the affected nerve trajectory.1 The median nerve and its branches are most commonly affected, followed by the radial nerve, ulnar nerve, nerves at the dorsal aspect of the foot, brachial plexus and cranial nerves.1,2 Magnetic resonance imaging demonstrated a typical fibrolipomatous hamartoma with high signal intensity of fat on both T1-weighted and T2-weighted images, characteristic coaxial cable appearance on axial images, and spaghetti appearance on sagittal images in two of our cases. Fibrolipomatous hamartoma (FLH) of nerve is a rare tumor-like condition in which mature fat infiltrates the neural sheath, with the majority of the lesions occurring in the median nerve.3 We present two cases of Fibrolipomatous hamartoma of median nerve at the wrist with an unusual proximal extension to the forea...
Fibrolipomatous Hamartoma of the Median Nerve
Radiology Case Reports, 2008
We present the case of a 33-year-old woman who presented with a slowly enlarging mass over the volar aspect of the wrist that had been present since infancy which for the previous year had been causing progressive pain. The lesion was proven to be a fibrolipomatous hamartoma, a rare benign tumor that most commonly affects the median nerve. We discuss the characteristic radiologic appearance of this entity that is often pathognomonic and allows a confident diagnosis without the need for biopsy. Although rare, fibrolipomatous hamartomas are an important entity to be familiar with because their imaging findings are pathognomonic and allow for confident radiologic diagnosis.
Fibrolipomatous hamartoma of the radial nerve: MR imaging findings
Skeletal Radiology, 1995
Clinical information This 34-year-old man presented with a mass involving the dorsal aspect of the right hand and wrist. The patient remembered having had the mass since he was a child and had noticed slow enlargement of the mass for severn years before the present examination.
Carpal Tunnel Syndrome due to Fibrolipomatous Hamartoma of the Median Nerve
HAND, 2010
Nervous lipofibromatous hamartoma is a rare tumor-like condition involving the peripheral nerves, whereby the epineurium and perineurium are enlarged and distorted by excess of fatty and fibrous tissues that infiltrate between and around nerve boundaries. The median nerve is much more likely to develop a hamartoma than other nerves with a predilection for the carpal tunnel. We present a case of carpal tunnel syndrome in an adult caused by fibrolipomatous hamartoma of the median nerve, successfully removed by excision of the fibrolipomatous tissue and decompression.
Carpal Tunnel Syndrome Caused by A Fibrolipomatous Hamartoma of the Median Nerve
BJR|case reports
Fibrolipomatous hamartoma (FLH) of the nerve (also known as perineural lipoma, neural fibrolipoma, or lipomatosis of the nerve) is a well-known, rare benign lesion that can affect any peripheral nerve, resulting in significant enlargement of the involved nerve with fibrofatty infiltration. Although it is most commonly involving the median nerve, other peripheral nerves can be also involved. Being familiar with the pathognomonic characteristics on different imaging modalities and the association of this entity with macrodactyly help reach the diagnosis, avoid putting the patient at risk of an invasive procedure, and can guide management. We present to you a rare case of a FLH of the median nerve that was diagnosed on MRI of an adult female who presented with carpal tunnel syndrome (CTS) and progressive swelling of the right hand and wrist.
Fibrolipomatous hamartoma of nerve arising in the brachial plexus
The Journal of Hand Surgery: Journal of the British Society for Surgery of the Hand, 1995
Fibrolipomatous hamartoma of nerve is a rare benign infiltrating condition of peripheral nerves leading to progressive functional loss. Previous descriptions have virtually all been confined to the distal part of the upper limb, with the median nerve being the commonest reported site. Most cases occur in the first 3 decades of life and a third are associated with macrodactyly. A case is described in a 63-year-old woman, involving the whole of the brachial plexus, a previously unreported site for this particular lesion.
The Canadian journal of plastic surgery = Journal canadien de chirurgie plastique, 2014
A three-year-old boy was investigated for inexplicable incessant crying. On examination, his left wrist was mildly swollen (three to four months) and sensitive. Exploration and carpal tunnel decompression of the left wrist with incisional biopsy was performed for the presence of a fusiform swelling intimately associated with the median nerve. Histopathology revealed the presence of enlarged nerve bundles admixed with mature fat cells and diffuse fibroblastic proliferation. Three months later, he underwent urgent contralateral carpal tunnel decompression for a similar presentation. The final diagnosis was bilateral fibrolipomatous hamartoma (FLH) of the median nerves causing acute bilateral compression neuropathy. FLH of the median nerve is an extremely unusual cause of acute bilateral carpal tunnel syndrome in a young child presenting with 'incessant crying'. A comprehensive review of FLH including epidemiology, etiology, clinical presentation, differential diagnosis, imagin...
A case of fibrolipomatous hamartoma of nerve arising from superficial peroneal nerve
Fibrolipomatous hamartoma of nerve (neural fibrolipoma) is a tumor-like lipomatous process principally involving young persons. The median nerve is most commonly affected. The lesion is characterized by a soft slowly growing mass surrounding and infiltrating major nerves and their branches. It may cause symptoms of compression neuropathy and is associated with macrodactyly in one third of cases. Here, we present a case of neural fibrolipoma in the ankle region and dorsum of foot of a young man arising from superficial peroneal nerve. KEY WORDS: Fibrolipomatous hamartoma, neural fibrolipoma, macrodactyly, superficial peroneal nerve.