Partial anomalous pulmonary venous return: case report and review of the literature (original) (raw)

Partial Anomalous Pulmonary Venous Return20190814 43053 phdl5y

Turkiye Klinikleri J Cardiovasc Sci., 2019

Partial pulmonary venous return anomaly (PPVRA) is defined as one or more of the pulmonary veins drain into the right atrium or a systemic vein such as superior vena cava (SVC), inferior vena cava (IVC), azygos, hepatic or portal vein. Diagnosing of PPVRA is often clinical challenging. Onset clinical manifestation and progression of the disease vary significantly depending on the amount of the intra-cardiac shunt. Signs or symptoms may include dyspnea, atrial arrhythmia, right heart failure and pulmonary hypertension, transient ischemic attack (TIA), or stroke. In this article, we aimed to present a 39-year-old female patient who underwent Warden Procedure with the diagnosis of PPVDA.

Partial Anomalous Pulmonary Venous Return20190814 10645 1daf6po

Turkiye Klinikleri J Cardiovasc Sci., 2019

Partial pulmonary venous return anomaly (PPVRA) is defined as one or more of the pulmonary veins drain into the right atrium or a systemic vein such as superior vena cava (SVC), inferior vena cava (IVC), azygos, hepatic or portal vein. Diagnosing of PPVRA is often clinical challenging. Onset clinical manifestation and progression of the disease vary significantly depending on the amount of the intra-cardiac shunt. Signs or symptoms may include dyspnea, atrial arrhythmia, right heart failure and pulmonary hypertension, transient ischemic attack (TIA), or stroke. In this article, we aimed to present a 39-year-old female patient who underwent Warden Procedure with the diagnosis of PPVDA.

Anomalous Pulmonary Venous Return

Circulation, 1965

One hundred and thirteen selected anomalous pulmonary venous returns have been well documented anatomically. Twenty-seven variations were seen. With the use of simplified diagrams, these have been correlated with related cases in the literature. Emphasis has been placed on transitional forms with one anomaly shading off into the next, rather than upon a series of neat, compartmentalized, classic types of anomalous pulmonary venous return. It is hoped that the broad anatomic spectrum shown will promote additional understanding and interest.

Partial Anomalous Pulmonary Venous Return With Persistent Angina: Simulating Coronary Artery Disease

Partial anomalous pulmonary venous return (PAPVR) is an uncommon adult congenital heart disease caused by an abnormal return of one or more, but not all, of the pulmonary veins to the right atrium or indirectly through venous connections from the anomalous pulmonary vein. Presentations vary from incidental findings to severe heart failure and diagnosis could easily be missed. We report a case of PAPVR in a 51-year-old male with a history of coronary artery bypass surgery presenting with exertional dyspnea and chest discomfort which were initially interpreted as angina in light of patient’s known coronary disease and prior revascularization. Patient underwent surgical repair with redirection of the pulmonary connection to the left atrium. On follow-up, patient had symptomatic improvement and decrease in pulmonary artery pressures. Diagnosis of PAPVR may be particularly elusive when patient also has a more common diagnosis, such as coronary disease. Unexplained pulmonary hypertension should alert physicians to consider additional differential diagnoses including congenital heart disease despite the patient’s adult age. As evidenced in this patient, successful surgical repair can lead to gratifying results and improved prognosis.