Development and Characterization of a Conditional Mitochondrial Complex I Assembly System (original) (raw)

Species-specific and Mutant MWFE Proteins. THEIR EFFECT ON THE ASSEMBLY OF A FUNCTIONAL MAMMALIAN MITOCHONDRIAL COMPLEX I

Amina Bisevac, N. Yadava, Immo Scheffler

Journal of Biological Chemistry, 2002

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Analysis of the Assembly Profiles for Mitochondrial- and Nuclear-DNA-Encoded Subunits into Complex I

Akira Ohtake

Molecular and Cellular Biology, 2007

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The NDUFA1 gene product (MWFE protein) is essential for activity of complex I in mammalian mitochondria

Immo Scheffler

Proceedings of the National Academy of Sciences, 1999

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Modular biogenesis of mitochondrial respiratory complexes

Gavin McStay

Mitochondrion, 2020

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Identification of Mitochondrial Complex I Assembly Intermediates by Tracing Tagged NDUFS3 Demonstrates the Entry Point of Mitochondrial Subunits

Cindy Dieteren

Journal of Biological Chemistry, 2006

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Understanding mitochondrial complex I assembly in health and disease

João Daniel Arrabaça

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Human mitochondrial complex I assembly: A dynamic and versatile process

Rutger Vogel

Biochimica et Biophysica Acta (BBA) - Bioenergetics, 2007

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Mitochondrial Complex I: Structural and Functional Aspects

christian bergamini

… et Biophysica Acta (BBA …, 2006

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An Assembled Complex IV Maintains the Stability and Activity of Complex I in Mammalian Mitochondria

Giovanni Manfredi

Journal of Biological Chemistry, 2007

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Identification and Characterization of a Common Set of Complex I Assembly Intermediates in Mitochondria from Patients with Complex I Deficiency

Hana Antonicka

Journal of Biological Chemistry, 2003

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Human Mitochondrial Complex I in Health and Disease

J. Smeitink

The American Journal of Human Genetics, 1999

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Mitochondrial complex III stabilizes complex I in the absence of NDUFS4 to provide partial activity

J. Smeitink, Shane Kruse

Human Molecular Genetics, 2012

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Characterisation of the active/de-active transition of mitochondrial complex I

Amanda Birch

Biochimica et Biophysica Acta (BBA) - Bioenergetics, 2014

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Human mitochondrial complex I assembly is mediated by NDUFAF1

J. Smeitink, Richard Huijbens

FEBS Journal, 2005

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Evaluation of mitochondrial bioenergetics, dynamics, endoplasmic reticulum-mitochondria crosstalk, and reactive oxygen species in fibroblasts from patients with complex I deficiency

Al-Walid Mohsen

Scientific Reports, 2018

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Human mitochondrial complex I assembles through the combination of evolutionary conserved modules: a framework to interpret complex I deficiencies

J. Smeitink, Richard Huijbens

Human Molecular Genetics, 2004

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ND3, ND1 and 39kDa subunits are more exposed in the de-active form of bovine mitochondrial complex I

Amanda Birch

Biochimica et Biophysica Acta (BBA) - Bioenergetics, 2014

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cDNA sequence and chromosomal localization of the NDUFS8 human gene coding for the 23 kDa subunit of the mitochondrial complex I

Pascal Soularue

Biochimica et Biophysica Acta (BBA) - Gene Structure and Expression, 1997

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Mitochondrial complex I in the network of known and unknown facts

Peter Račay

General Physiology and Biophysics, 2010

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Mammalian complex I: A regulable and vulnerable pacemaker in mitochondrial respiratory function

Salvatore Scacco, Anna Sardanelli

Biochimica et Biophysica Acta (BBA) - Bioenergetics, 2008

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Mouse mitochondrial complex I in the active state

Hannah Bridges

2018

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The nuclear encoded subunits of complex I from bovine heart mitochondria

Judy Hirst

Biochimica et Biophysica Acta (BBA) - Bioenergetics, 2003

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Pharmacological targeting of mitochondrial complex I deficiency: The cellular level and beyond

Ganesh R Manjeri

Mitochondrion, 2012

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Induction of the Mitochondrial NDUFA4L2 Protein by HIF-1α Decreases Oxygen Consumption by Inhibiting Complex I Activity

Susana Cadenas

Cell Metabolism, 2011

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Mutation of C20orf7 Disrupts Complex I Assembly and Causes Lethal Neonatal Mitochondrial Disease

Wendy Hutchison

The American Journal of Human Genetics, 2008

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Activation of the cAMP cascade in human fibroblast cultures rescues the activity of oxidatively damaged complex I

tiziana cocco

Free Radical Biology and Medicine, 2012

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Subunit-specific Incorporation Efficiency and Kinetics in Mitochondrial Complex I Homeostasis

Rosalinde Masereeuw

Journal of Biological Chemistry, 2012

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Cellular and molecular mechanisms of mitochondrial function

Farooque Ali

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Phosphorylation pattern of the NDUFS4 subunit of complex I of the mammalian respiratory chain

Aldo Di Luccia

Mitochondrion, 2010

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A Mitochondrial Protein Compendium Elucidates Complex I Disease Biology

David Hill

Cell, 2008

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C6ORF66 Is an Assembly Factor of Mitochondrial Complex I

Haya Lorberboum-galski, Ann Saada

The American Journal of Human Genetics, 2008

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Molecular mechanism and physiological role of active–deactive transition of mitochondrial complex I

Ravi Manjithaya

Biochemical Society Transactions, 2013

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Studies on assembly and genetic variation in mitochondrial respiratory complex I

Polly Marino

2019

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