A new, tenth subunit of TFIIH is responsible for the DNA repair syndrome trichothiodystrophy group A (original) (raw)

GTF2E2 Mutations Destabilize the General Transcription Factor Complex TFIIE in Individuals with DNA Repair-Proficient Trichothiodystrophy

laura baranello

The American Journal of Human Genetics, 2016

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Cloning and characterization of p52, the fifth subunit of the core of the transcription/DNA repair factor TFIIH

Wim Vermeulen, Richard Roy

The EMBO journal, 1997

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Reduced level of the repair/transcription factor TFIIH in trichothiodystrophy

Miria Stefanini

Human Molecular Genetics, 2002

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A history of TFIIH: Two decades of molecular biology on a pivotal transcription/repair factor

Frédéric Coin

DNA Repair, 2011

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Defective Transcription/Repair Factor IIH Recruitment to Specific UV Lesions in Trichothiodystrophy Syndrome

Alain Sarasin

Cancer Research, 2008

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Architecture of the Human and Yeast General Transcription and DNA Repair Factor TFIIH

Bong Kim

Molecular cell, 2015

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DNA repair deficiencies associated with mutations in genes encoding subunits of transcription initiation factor TFIIH in yeast

Kevin Sweder

Nucleic Acids Research, 1996

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Two Sides of the Same Coin: TFIIH Complexes in Transcription and DNA Repair

Valentyn Oksenych

The Scientific World JOURNAL, 2010

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Nucleotide excision repair of DNA with recombinant human proteins: definition of the minimal set of factors, active forms of TFIIH, and modulation by CAK

Sofia Araujo

Genes & Development, 2000

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p44 and p34 subunits of the BTF2/TFIIH transcription factor have homologies with SSL1, a yeast protein involved in DNA repair

Anneke Van Vuuren

The EMBO Journal, 1994

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A mutation in the XPB/ERCC3 DNA repair transcription gene, associated with trichothiodystrophy

Wim Vermeulen

The American Journal of Human Genetics, 1997

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Rare diseases provide rare insights into DNA repair pathways, TFIIH, aging and cancer

Miriam Sander

DNA Repair, 2005

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Slowly Progressing Nucleotide Excision Repair in Trichothiodystrophy Group A Patient Fibroblasts

Wim Vermeulen

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Recovery of Normal DNA Repair and Mutagenesis in Trichothiodystrophy Cells after Transduction of the XPD Human Gene

Alain Sarasin

Cancer Research, 1996

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Interactions of the transcription/DNA repair factor TFIIH and XP repair proteins with DNA lesions in a cell-free repair assay

Bernard Salles

Journal of Molecular Biology, 1998

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Mouse model for the DNA repair/basal transcription disorder trichothiodystrophy reveals cancer predisposition

J. Garssen

Cancer research, 1999

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A 3′→ 5′ XPB Helicase Defect in Repair/Transcription Factor TFIIH of Xeroderma Pigmentosum Group B Affects Both DNA Repair and Transcription

Anneke Van Vuuren

Journal of Biological Chemistry, 1996

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Molecular insights into the recruitment of TFIIH to sites of DNA damage

Valentyn Oksenych, Frédéric Coin, Jean-marc Egly

The EMBO Journal, 2009

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ARCH domain of XPD, an anchoring platform for CAK that conditions TFIIH DNA repair and transcription activities

Laura Radu

Proceedings of the National Academy of Sciences, 2013

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Unraveling DNA Repair in Human: Molecular Mechanisms and Consequences of Repair Defect

Renu Tuteja

Critical Reviews in Biochemistry and Molecular Biology, 2001

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Transcription-coupled DNA repair in yeast transcription factor IIE (TFIIE) mutants

Karen Becker

Nucleic acids research, 2000

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Lineage-specific control of TFIIH by MITF determines transcriptional homeostasis and DNA repair

David E Fisher

Oncogene, 2019

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Defects in the DNA repair and transcription gene ERCC2(XPD) in trichothiodystrophy

Larry Thompson

The American Journal of Human Genetics, 1996

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The intricate network between the p34 and p44 subunits is central to the activity of the transcription/DNA repair factor TFIIH

Laura Radu

Nucleic Acids Research

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Comparative study of nucleotide excision repair defects between XPD-mutated fibroblasts derived from trichothiodystrophy and xeroderma pigmentosum patients

Alain Sarasin

DNA Repair, 2008

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UV-damaged DNA-binding protein in the TFTC complex links DNA damage recognition to nucleosome acetylation

Jeffrey Dilworth

The EMBO Journal, 2001

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