Osteochondromatosis: A rare clinical condition (original) (raw)

Osteochondromatosis, also known as hereditary multiple osteocartilagenous exostosis or Bessel-Hagen disease, is a rare autosomal dominant condition occurring in approximately 1 in 50,000 births. This clinical condition is characterized by the development of osteochondromas, with a notable risk of malignant transformation ranging from 1% to 15%. The current paper discusses a case involving a patient with sessile osteochondromas and highlights the incidence, presentation, and the importance of monitoring asymptomatic cases without familial history—occurring in a small percentage of affected individuals.