Congenitally Corrected Transposition of the Great Arteries with Situs Solitus: Pacemaker Implantation in a Septuagenarian (original) (raw)
Pacemaker implantation in congenitally corrected transposition of the great arteries can be challenging due to distorted cardiac anatomy that in some cases it may be accompanied by other anomalies. The present report outlines a rare case of congenitally corrected transposition of the great arteries, asymptomatic until the seventh decade of life. Keywords: congenital heart disease, congenitally corrected transposition of the great arteries, double discordance, levocardia, permanent pacemaker, situs solitus
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Eplasty, 2013
Congenitally corrected transposition of great arteries (CCTGA) is characterized by atrioventricular and ventriculoarterial discordance. Characterizations of these anomalies are important because they may influence surgical approach and management. We present a case of newly diagnosed CCTGA at the age of 50. He presented with sudden onset of shortness of breath for the first time and was diagnosed with CCTGA. Echocardiogram, magnetic resonance imaging, and cardiac catheterization were utilized to elucidate the pathology. Intraoperatively, patient's CCTGA and ventricularization of the right ventricle were confirmed. The severe systemic atrioventricular valve regurgitation was replaced with a bioprosthetic valve (Medtronic Mosaic No. 29) with placement of epicardial ventricular leads for possible future placement of automatic implantable cardioverter defibrillators. Pathology report confirmed a degeneration of the systemic atrioventricular valve. Significant coronary artery anomali...
SUMMARY We describe the case of an 83-year-old asymptomatic man followed in our centre. Transoesophageal echocardiography disclosed congenitally corrected transposition of great arteries (CCTGA) with no associated anomalies and only mild aortic regurgitation. Cardiac MR confirmed the diagnosis and revealed preserved systemic ventricle systolic function with a normal perfusional pathway. This report is a demonstration that CCTGA without associated anomalies can reach older life in an asymptomatic condition. This is the oldest asymptomatic living patient with CCTGA ever described. BACKGROUND
Congenitally corrected transposition of the great arteries: the systemic right ventricle
Progress in Pediatric Cardiology, 1999
L-Transposition of the great arteries (L-TGA) is characterized by atrioventricular and ventriculoarterial discordance such that the morphologic right ventricle and tricuspid valve directly provide systemic cardiac output. The ability of the right ventricle to support the systemic circulation is often complicated by associated cardiac defects which provide numerous potential mechanisms for the development of ventricular dysfunction. Theoretical risk factors for
Bangladesh heart journal, 2022
Congenitally Corrected Transposition of Great Arteries (c-TGA) is an anomaly with atrioventricular and ventriculoarterial discordance where left atrium connects to right ventricle and right atrium to left ventricle. However in this case of double inversion, aorta carries saturated blood and pulmonary artery carries venous blood. So, normal physiological circulation is maintained. Our patient, a 38-years-old Bangladeshi male presented with palpitation, dizziness and effort intolerance (NYHAII) during exertion since childhood, which has recently become much worse. However, he had no history of central cyanosis, chest pain or syncope. We diagnosed him as a case of Corrected TGA and second-degree AV block with intermittent complete heart block. A Dual chamber permanent Pacemaker was inserted without any complications. No invasive treatment including corrective surgery was performed because patient's cardiac function was almost normal. Patient became totally asymptomatic after pacemaker implantation
Journal of Dr Behcet Uz Children s Hospital
Congenitally corrected transposition of the great arteries (cc-TGA), is also defined as double discordance and ventricular inversion. We conducted a retrospective evaluation of medical records of 79 patients diagnosed and followed-up with congenital transposition of great arteries between December 1993 and January 2014 at our pediatric cardiology department. Of 79 patients included in the study, 46 (58.2%) were male, mean age at diagnosis was 40±39.25 months and the mean follow-up time was 56±39.4 months. Thirteen (16.5%) patients had atrial situs inversus. The most common concomitant abnormality was found to be ventricular septal defet (29.1%). Fourty-five patients had pulmonary stenosis either in the form of valvular, subvalvular or both together. Twelve (15.2%) patients had pulmonary atresia. Systemic atrioventricular valve (AV) regurgitation was present in 51 (64.6%) patients, whereas 2 (2.5%) patients had severe systemic AV valve regurgitation. Ebstein-like AV valve was detected in 5 (6.3%) patients. Transcatheter interventions included ductal stent implantation (n=5; 6.3%), left ventriculopulmonary artery conduit angioplasty (n=2; 2.5%), RV-PA conduit angioplasty (n=1; 1.3%) and pulmonary balloon valvuloplasty (n=2; 2.5%). Eleven (13.9%) patients underwent interventional therapeutic cardiac catheterization. Glenn anastomosis was performed in 16 (20.3%) patients. Nine (11.4%) patients required a permanent pacemaker implantation. Individualization of treatments and managements for the patients is of prognostic importance for these patients needing lifelong follow-up due to the large number of accompanying anomalies and different degrees of abnormalities in cc-TGA patients.
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