Prenatal and postnatal evaluation for syringomyelia in patients with spinal dysraphism (original) (raw)

Abstract

Syringomyelia can be diagnosed in isolation but is more commonly found in the presence of craniocervical junction anomalies or spinal dysraphism. The origin of syringomyelia has been hypothesized to be either congenital or acquired. The purpose of this study was to determine the incidence of syringomyelia within the fetal and postnatal population with neural tube defects (NTDs). A review was performed of the authors' fetal MRI database of pregnancies with imaging between March 2004 and November 2011 for evaluation of an intrauterine anomaly detected via prenatal ultrasonography. Those cases with an NTD were then selected and a chart review was performed of all prenatal and postnatal imaging as well as available clinical history. A total of 2362 fetal MRI examinations were performed, and 109 of these were patients with an NTD. Of the 2362 studies reviewed, 2 cases of fetal syringomyelia were identified. Both fetal syrinxes were identified in fetuses with CSF flow disturbances (1 ...

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  18. Manuscript submitted September 20, 2013. Accepted May 13, 2014. Portions of this work were presented in poster form as proceed- ings at the Society of Pediatric Radiology Conference, San Antonio, Texas, May 14-18, 2013. Please include this information when citing this paper: pub- lished online July 4, 2014; DOI: 10.3171/2014.5.PEDS13482. Address correspondence to: Ben Bixenmann, M.D., 260 Stetson St., Ste. 2200, Cincinnati, OH 45267. email: bbixenmann@yahoo. com.