Medium-chain acyl-CoA dehydrogenase deficiency: Two novel ACADM mutations identified in a retrospective screening (original) (raw)

Medium-chain acyl-CoA dehydrogenase deficiency: Two novel ACADM mutations identified in a retrospective screening

Urh Groselj

Journal of International Medical Research, 2018

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Blood acylcarnitine levels in normal newborns and heterozygotes for medium-chain acyl-CoA dehydrogenase deficiency: A relationship between genotype and biochemical phenotype?

C. Rockman-Greenberg

Journal of Inherited Metabolic Disease, 2000

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Medium-Chain Acyl-CoA Dehydrogenase (MCAD) Mutations Identified by MS/MS-Based Prospective Screening of Newborns Differ from Those Observed in Patients with Clinical Symptoms: Identification and Characterization of a New, Prevalent Mutation That Results in Mild MCAD Deficiency*

Szabolcs Udvari

The American Journal of Human Genetics, 2001

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Maternal medium-chain acyl-CoA dehydrogenase deficiency identified by newborn screening

Julie Neidich

Molecular Genetics and Metabolism, 2011

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Pitfalls of neonatal screening for very-long-chain acyl-CoA dehydrogenase deficiency using tandem mass spectrometry

Ronald Wanders

The Journal of Pediatrics, 2006

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Four Years' Experience in the Diagnosis of Very Long-Chain Acyl-CoA Dehydrogenase Deficiency in Infants Detected in Three Spanish Newborn Screening Centers

Ana Morais

JIMD reports, 2017

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Neonatal Screening for Very Long-Chain Acyl-CoA Dehydrogenase Deficiency: Enzymatic and Molecular Evaluation of Neonates With Elevated C14:1-Carnitine Levels

Jos Ruiter

PEDIATRICS, 2006

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Multiple acyl-coenzyme A dehydrogenase deficiency: Diagnosis by acyl-carnitine analysis of a 12-year-old newborn screening card

Ida Di Giacinto

The Journal of Pediatrics, 1999

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Neonatal onset of medium-chain Acyl-CoA dehydrogenase deficiency in two siblings

Fumio Endo

Brain and Development, 1988

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Evaluation of newborn screening for medium chain acyl-CoA dehydrogenase deficiency in 275 000 babies

Veronica Wiley

Archives of Disease in Childhood - Fetal and Neonatal Edition, 2001

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Urinary acylcarnitines in a patient with neonatal multiple acyl-CoA dehydrogenation deficiency, quantified by a carboxylic acid analyzer with a reversed-phase column

Kiyofumi Asai

Clinica Chimica Acta, 1988

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Development of a newborn screening follow-up algorithm for the diagnosis of isobutyryl-CoA dehydrogenase deficiency

Barbara Burton

Genetics in Medicine, 2007

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Compound heterozygous mutations of ACADS gene in newborn with short chain acyl-CoA dehydrogenase deficiency: case report and literatures review

Gu-Hwan Kim

Korean journal of pediatrics, 2016

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Biochemical, molecular, and clinical characteristics of children with short chain acyl-CoA dehydrogenase deficiency detected by newborn screening in California

Julie Neidich

Molecular genetics and metabolism, 2012

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DNA analysis for detection of medium-chain acyl-CoA dehydrogenase deficiency in a Manitoba newborn population

Atilano Lacson

Screening, 1995

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Pseudo-glutarylcarnitinaemia in medium-chain acyl-CoA dehydrogenase deficiency detected by tandem mass spectrometry newborn screening

Veronica Wiley

Journal of Inherited Metabolic Disease, 2000

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The first three years of screening for medium chain acyl-CoA dehydrogenase deficiency (MCADD) by newborn screening ontario

Jennifer Milburn

BMC Pediatrics, 2010

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A severe genotype with favourable outcome in very long chain acyl-CoA dehydrogenase deficiency

Mohamed Rashed

Archives of Disease in Childhood, 2001

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A case report of short-chain acyl-CoA dehydrogenase deficiency (SCADD)

Tadej Battelino

Biochemia Medica, 2015

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MS/MS-based newborn and family screening detects asymptomatic patients with very-long-chain acyl-CoA dehydrogenase deficiency

Ronald Wanders

The Journal of Pediatrics, 2003

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Relevance of expanded neonatal screening of medium-chain acyl co-a dehydrogenase deficiency: outcome of a decade in galicia (Spain)

Dulce Quelhas

2011

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Reduced incidence of severe metabolic crisis or death in children with medium chain acyl-CoA dehydrogenase deficiency homozygous for c.985A>G identified by neonatal screening

Hans-Beat Hadorn

Molecular Genetics and Metabolism, 2005

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Medium-Chain Acyl-CoA Deficiency: Outlines from Newborn Screening, In Silico Predictions, and Molecular Studies

Catia Cavicchi

The Scientific World Journal, 2013

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The A985G mutation in the medium‐chain acyl‐CoA dehydrogenase gene: high prevalence in the swiss population resident in Geneva

D. Belin

Journal of Inherited Metabolic Disease, 1995

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Incidence of medium-chain acyl-CoA dehydrogenase deficiency in Canada using the Canadian Paediatric Surveillance Program: Role of newborn screening

Kathy Speechley

Paediatrics & Child Health, 2012

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221 newborn-screened neonates with medium-chain acyl-coenzyme A dehydrogenase deficiency: Findings from the Inborn Errors of Metabolism Collaborative

Adrya Stembridge

Molecular Genetics and Metabolism, 2016

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The natural history of medium-chain acyl CoA dehydrogenase deficiency in the Netherlands: Clinical presentation and outcome

Dirk-jan Reijngoud

The Journal of Pediatrics, 2006

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A Novel Tandem Mass Spectrometry Method for Rapid Confirmation of Medium- and Very Long-Chain acyl-CoA Dehydrogenase Deficiency in Newborns

Frank Veld

PLoS ONE, 2009

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