Superior Canal Dehiscence Syndrome – Case Report (original) (raw)
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Superior semicircular canal dehiscence (SSCD) is a rare entity recently described whose typical clinical symptomatology is represented by dizziness triggered by a variation of pressure. We reported a case of SSCD which was diagnosed thanks to computed tomography (CT) scan of the petrous bone conducted systematically in front of mixed deafness with normal eardrum. The SSCD was bilateral and was revealed by mixed deafness on the left side and perception deafness on the right with a normal eardrum without the notion of vertigo. The cervical vestibular evoked myogenic potential (cVEMP) and an ultra-high resolution CT scan of the petrous bones in coronal and sagittal sections allowed the diagnosis. The SSCD should be considered in the presence of any conductive or mixed hearing loss with a normal eardrum. The CT scan in coronal and sagittal submillimetric sections allows the diagnosis.
Journal of Vestibular Research
This paper describes the diagnostic criteria for superior semicircular canal dehiscence syndrome (SCDS) as put forth by the classification committee of the Bárány Society. In addition to the presence of a dehiscence of the superior semicircular canal on high resolution imaging, patients diagnosed with SCDS must also have symptoms and physiological tests that are both consistent with the pathophysiology of a ‘third mobile window’ syndrome and not better accounted for by another vestibular disease or disorder. The diagnosis of SCDS therefore requires a combination of A) at least one symptom consistent with SCDS and attributable to ‘third mobile window’ pathophysiology including 1) hyperacusis to bone conducted sound, 2) sound-induced vertigo and/or oscillopsia time-locked to the stimulus, 3) pressure-induced vertigo and/or oscillopsia time-locked to the stimulus, or 4) pulsatile tinnitus; B) at least 1 physiologic test or sign indicating that a ‘third mobile window’ is transmitting pr...
Atypical superior semicircular canal dehiscence case report
The Egyptian Journal of Otolaryngology, 2013
Superior canal dehiscence syndrome is a rare medical condition with many variants. In this case report, we present a 35-year-old patient who presented with atypical presentation of superior canal dehiscence syndrome. We discuss his audiological, vestibular, and radiological findings before and after surgery. We present a protocol to establish the diagnosis of a similar condition, especially those presenting atypically.
An Uncommon Case of Bilateral Posterior and Superior Semicircular Canal Dehiscence Syndrome
International Journal of Anatomy Radiology and Surgery, 2020
Semicircular Canal Dehiscences (SCD) are rare and involvement of Posterior Semicircular Canal (PSCC) and/or multiple dehiscences are even rarer. A dehiscence of any of the semicircular canals may produce various auditory or vestibular symptoms by creating an abnormal communication between the inner ear and nearby structures. We report a rare case of multiple dehiscence with intracranially protruding PSCC and Superior Semicircular Canal (SSCC) beyond the margins of temporal bone with bony roof defects in bilateral PSCCs and SSCCs in a patient with chief complaints of positional vertigo.
Posterior Semicircular Canal Dehiscence
Otology & Neurotology, 2014
To identify clinical, audiological, and vestibular characteristics of posterior semicircular canal dehiscence. Study Design: Retrospective case review. Setting: Tertiary referral center. Patients: Twelve patients aged 2 to 67 years identified with posterior semicircular canal dehiscence. Interventions: Patients identified by suspicious clinical history and examination, confirmed by high-resolution computed tomography. Audiological evaluation included air and bone audiometry, tympanometry, acoustic reflexes, and vestibular evoked myogenic potential testing. Results: Hearing loss was mixed in 9 patients, conductive in 2 patients, and sensorineural in 1 patient, with downward-sloping configuration being the most common. Imaging revealed that 7 of 12 patients had dehiscence into a high-riding jugular bulb and 1 patient had an enlarged vestibular aqueduct with a Mondini malformation. One patient had Apert syndrome and another patient had microtia/atresia.
Superior semicircular canal dehiscence syndrome
ENT SCHOLAR, 2013
This article discusses superior semicircular canal dehiscence syndrome. This syndrome has been identified in 1998 by Minor etal. This condition is caused due to dehiscence of bone overlying the superior semicircular canal. This causes vertigo, oscillopsia, dysequilibrium due to exposure to sound. Ultra high resolution CT scans help in identification of this condition. This dehiscence has been confirmed by surgical exploration of middle cranial fossa.
Superior semicircular canal dehiscence: Diagnosis and management
Journal of Clinical Neuroscience, 2018
The authors provide an update on the clinical manifestations, diagnosis and various approaches to the treatment of superior semicircular canal dehiscence (SSCD). SSCD is a rare condition where the bone overlying the superior semicircular canal thins or dehisces causing characteristic clinical findings. Since this was first reported in 1998 by Minor and colleagues, there has been much advancement made in terms of diagnosis and treatment. Signs and symptoms include a wide variation of both vestibular and auditory manifestations. Diagnosis made solely on clinical signs is difficult due to how varied the presentations can be and the overlap with other otologic pathologies. High-resolution CT temporal scans have been the standard in confirming superior semicircular canal dehiscence, however, MRI FIESTA scans have recently been used to image SSCD. Additionally, audiometry and vestibular evoked myogenic potential (VEMP) testing are useful screening tools. Currently, the middle fossa approach is the most common and standard surgical approach to repair SSCD. The transmastoid, endoscopic and transcanal or endaural approaches have also been recently utilized. Presently, there is no consensus as to the best approach, material or technique for repair of SSCD. As we learn more, newer and less invasive approaches and techniques are being used to treat SSCD. We present a comprehensive review of SSCD, including clinical symptoms and presentation, histopathology, diagnosis, treatment strategies and outcomes of intervention.