Pseudosequestration of the left lung (original) (raw)
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A Case of Congenital Bronchial Pulmonary Arterial Malformation Successfully Treated by Embolization
Journal of Clinical Interventional Radiology ISVIR
Idiopathic bronchial pulmonary arterial malformation (BPAM) is a very rare condition. The authors present a case of BPAM in which a right bronchial artery communicates with a main upper lobe branch of the right pulmonary artery. It was successfully treated by embolization in one setting. The patient remained asymptomatic and well during the follow-up period. The authors therefore conclude that if the embolic material/device is carefully chosen, it is a safe and effective means of treating BPAM.
The Turkish journal of pediatrics, 2016
Congenital pulmonary vascular abnormalities arise from several etiologies. These anomalies are difficult to categorize and sorted into distinct classifications. Major pulmonary vascular abnormalities can be ranked as interruption of the main pulmonary artery or its absence, emergence of the left pulmonary artery in the right pulmonary artery, pulmonary venous drainage abnormalities, and pulmonary arteriovenous malformations (PAVMs). Some of the cases are asymptomatic and diagnosed by coincidence, whereas a few of them are diagnosed by typical findings in the newborn and infancy period, symptoms, and radiological appearances. Early diagnosis is important, since death may occur as a result of pulmonary and cardiac pathologies developed in patients with pulmonary vascular anomalies. In this case presentation, the clinical and radiological findings of patients that presented with different complaints and were diagnosed with pulmonary vascular anomalies were introduced.
Thorax, 1987
Congenital malformations of the bronchopulmonary airway and related arterial blood supply are a complex group of lesions in which abnormalities of venous drainage and lung parenchyma may coexist. Twenty five cases have been analysed, by a method whereby each anatomical component is separately considered. All 25 patients had abnormalities of the tracheobronchial tree, with no connection to the abnormal segment in nine cases. The aberrant arterial blood supply was single in 16 cases and multiple in nine cases, one patient from the latter group having a mixed pulmonary and systemic arterial supply to a part of the abnormal segment. Seventeen patients had anomalous venous drainage. In nine of these the vein or veins (they were multiple in four cases) drained the major part or the whole of the lung, whereas the aberrant arterial supply was limited to the right lower zone-that is, mismatched anomalous venous drainage. Abnormalities of lung parenchyma included changes within the lesion (for example, cysts, foregut inclusions) and associated abnormalities of surrounding lung (for example, hypoplasia, abnormal lobation). This information, together with the clinical features and haemodynamic data, was found to be essential for decisions on appropriate management. Patients presenting in infancy with haemodynamic disturbance continue to present major management problems (50% mortality), particularly if there are associated congenital heart defects. The role of aberrant systemic artery occlusion or ligation as a first stage procedure is well established in patients with haemodynamic abnormalities. There may be a place for this procedure in selected patients who have no haemodynamic disturbance at presentation.
Excluded right pulmonary artery in a neonate
European Journal of Pediatrics, 2004
A case of ''absent'' right pulmonary artery in a 3-dayold newborn is presented. Initial treatment consisted of stenting the arterial duct with subsequent surgical correction. Congenital unilateral ''absence'' of a pulmonary artery is a rare malformation. ''Absent'' right pulmonary artery is mostly found as an isolated lesion whereas an ''absent'' left pulmonary artery is commonly associated with tetralogy of Fallot, in particular with pulmonary atresia and duct-dependent pulmonary circulation. Patients with isolated unilateral ''absence'' of a pulmonary artery are mostly asymptomatic, this being an incidental finding, e.g. on a chest X-ray film [1, 6, 7, 8,9]. Some patients develop recurrent respiratory infections, dyspnoea, exercise intolerance, haemoptysis and pulmonary hypertension in the contra lateral pulmonary artery. The affected pulmonary artery is not actually absent and the distal portion and the intrapulmonary vessels are always present but may be occluded. Perfusion of these distal vessels was occasionally described by an arterial duct originating from the aorta or from the ipsilateral brachiocephalic artery [1, 5,7]. Thus, only the central portion of the affected pulmonary artery is absent causing discontinuity between the intrapulmonary artery and the pulmonary trunk. The search for the patency of this occult intrapulmonary artery is of great importance in order to try to restore blood flow to the affected side. This stimulates further normal vessel and lung growth thus preventing pulmonary hypertension in the contralateral lung. We report a case in which an excluded right pulmonary artery was detected in the neonatal period. Sponsored in part by the Belgian Foundation for Research in Paediatric Cardiology. L.M. is clinical researcher for the Foundation for Scientific Research (FWO).
Therapeutic Strategies in Children with an Isolated Unilaterally Absent Proximal Pulmonary Artery
Pediatric Cardiology, 2010
Therapeutic strategies for isolated unilateral absence of a proximal pulmonary artery remain unclear. The natural history of the disease, or thrombosis of primary surgical anastomosis, leads to exclusion of the affected lung with increased risk of intrapulmonary bleeding, impaired quality of life, and shortened life expectancy. We herein describe our two-stage approach in a small series of patients starting with interventional catheterization followed by surgical anastomosis. Other medical interventions, such as anticoagulation and pulmonary vasodilatation, are key factors to successfully restore pulmonary circulation in this rare defect.
Echocardiography, 2008
We report an interest and mystifying cardiovascular imaging in a 22q11 deletion neonate with rare congenital heart defects, including anomalous origin of the left pulmonary artery arising from the right pulmonary artery and in front of the trachea, called pseudo-pulmonary artery sling, combined with isolated left subclavian artery confirmed by multidetector row computed tomography. (ECHOCARDIOGRAPHY, Volume 25, September 2008) 22q11 deletion, isolated subclavian artery, pulmonary artery sling Anomalous origin of the left pulmonary artery (LPA) arising from the right pulmonary artery (RPA), pulmonary artery sling, is a rare but serious congenital anomaly. Affected infants generally present with respiratory distress and feeding problems during the early infancy. This anomaly can be associated with other cardiac defects, including tetralogy of Fallot (TOF), and echocardiography can provide an accurate diagnosis. 1,2 Right aortic arch with isolation of branchiocephalic vessels is also relatively uncommon. This anomaly includes isolated left subclavian artery (LSCA), the left common carotid artery or the left innominate artery. Herein we present a case of a 1-week-old male neonate with TOF, right aortic arch, and 22q11 deletion syndrome. Typical imaging of anomalous origin of the LPA from the RPA and coursing posteriorly and leftward in the parasternal short-axis plane was detected by transthoracic echocardiography. The main pulmonary artery (MPA) did not bifurcate in the usual location . Although there were no vascular slingrelated symptoms, such as respiratory distress or feeding problems in this patient, multidetec-
Archivos de cardiología de México
Objective: The aim of this report is to describe a clinical case of an anomalous origin of the left pulmonary artery branch from the ascending aorta, and to present a current literature review of this rare disease. Clinical case: A 2 year-old infant was referred to our institution for surgical correction of sub aortic obstruction. The non invasive investigation disclosed a right aortic arch anatomy with left ventricle outflow tract obstruction due to sub aortic membrane associated but failed to show the anomalous origin of the left pulmonary artery branch from the ascending aorta. The diagnosis was made intraoperatively and the patient underwent a total surgical correction of the defects, including simultaneous anastomosis of the left pulmonary artery to the pulmonary trunk. Results of the surgical repair of this case were successful. Conclusions. Although anomalous origin of the left pulmonary artery from the ascending aorta is a rare disease which was not diagnosed appropriately, ...