A rare epidermal naevus: naevus comedonicus case repot (original) (raw)

International Journal of Research in Dermatology

Naevus comedonicus (NC) is a rare epidermal naevus characterized by a honeycomb-like dilated follicular opening filled with black or brown keratinous plug. Diagnosis is based mainly on clinical examination and histopathology. It is also a part of NC syndrome (a neurocutaneous syndrome) with ophthalmological (congenital cataract), skeletal (scoliosis, fused vertebra, spina bifida, absence of the fifth finger, polysyndactyly, clinodactyly, rudimentary toe, bone hypertrophy, bone cyst, kyphosis and vitamin D resistant rickets), neurological (mental retardation, corpus callosum dysgenesis, seizures, paresis, electrocochleographic abnormalities). The physician should be aware of the extracutaneous manifestations involving the skeletal system, ophthalmological, neurological, and other skin manifestations. Several topical creams and energy-based devices treat with an unsatisfactory or moderate response. Surgical excision offers good aesthetic results.