Primary unresectable locally invasive biatrial paraganglioma presenting with chest pain (original) (raw)
2018, Human Pathology: Case Reports
AI-generated Abstract
Primary cardiac paragangliomas are rare tumors that can present with ischemic symptoms. A case of a 43-year-old female with an unresectable paraganglioma located above the right atrium is reported, demonstrating intense peripheral enhancement on imaging. Histopathology confirmed the diagnosis with a characteristic 'Zellballen' pattern, while immunohistochemical studies indicated an SDHB gene mutation. The absence of adrenergic symptoms complicated the diagnosis, underscoring the importance of considering paragangliomas in the differential diagnosis of cardiac neoplasms.
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