Deletion ΔF508 and clinical expression of cystic fibrosis-related liver disease (original) (raw)

Genotype analysis for ΔF508, G551D and R553X mutations in children and young adults with cystic fibrosis with and without chronic liver disease

John Warner

Hepatology, 1992

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Cystic fibrosis: The ΔF508 mutation does not lead to an exceptionally severe phenotype. A cohort study

G. Mastella

European Journal of Pediatrics, 1993

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Genetic Modifiers of Liver Disease in Cystic Fibrosis

Claire Wainwright

JAMA, 2009

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Liver expression in cystic fibrosis could be modulated by genetic factors different from the cystic fibrosis transmembrane regulator genotype

Donatello Salvatore, Teresa Santostasi

American Journal of Medical Genetics, 2001

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Frequency of delta F508 in a Mexican sample of cystic fibrosis patients

Maggi Moreno Chavez

Journal of Medical Genetics, 1993

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Genotype-phenotype relationship in Iranian patients with cystic fibrosis

alireza moraveji

The Turkish Journal of Gastroenterology, 2015

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Analysis of the DF508 mutation in a Brazilian cystic fibrosis population: comparison of pulmonary status of homozygotes with other patients

Paulo Marostica

Brazilian Journal of Medical and Biological Research, 1998

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Detection of mutation delta F508 in the cystic fibrosis gene using allele-specific PCR primers and time-resolved fluorometry

Pertti Hurskainen

Genome Research, 1992

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Delta F508 in cystic fibrosis: willing but not able

Kevin Southern

Archives of Disease in Childhood, 1997

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Phenotypic expression of genotype-phenotype correlation in cystic fibrosis patients carrying the 852del22 mutation

Teresa Santostasi, Luigi Mappa

American Journal of Medical Genetics Part A, 2005

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Screening for F508del as a first step in the molecular diagnosis of cystic fibrosis

Jose Dirceu Ribeiro

Jornal brasileiro de pneumologia : publicaça̋o oficial da Sociedade Brasileira de Pneumologia e Tisilogia

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High morbidity and mortality in cystic fibrosis patients compound heterozygous for 3905insT and ΔF508

Sabina Gallati

European Respiratory Journal, 2001

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Frequency of the deltaF508 mutation in 108 cystic fibrosis patients in São Paulo: comparison with reported Brazilian data

Thelma Okay

Clinics, 2005

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Phenotypic discordance in three siblings affected by atypical cystic fibrosis with the F508del/D614G genotype

Rossella Tomaiuolo

Journal of Cystic Fibrosis, 2006

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Prevalence of ∆F508 cystic fibrosis carriers in a Romanian population group

Constantin Ionuț Coroamă

Revista Romana de Medicina de Laborator, 2021

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An MBL2 haplotype and ABCB4 variants modulate the risk of liver disease in cystic fibrosis patients: A multicentre study

Dario Degiorgio

Digestive and Liver Disease, 2009

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Nutrional status and dietary factors in cystic fibrosis patients with delta F508 mutation

Thais Steemburgo

Revista de Nutrição, 2015

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p.F508del in a heterogeneous cystic fibrosis population from Minas Gerais, Brazil

Geraldo Filho

Brazilian Journal of Medical and Biological Research, 2008

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Liver involvement in cystic fibrosis

Andrea Crosignani

Journal of Hepatology, 1999

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Identification of the commonest cystic fibrosis transmembrane regulator gene ΔF508 mutation: evaluation of PCR–single-strand conformational polymorphism and polyacrylamide gel electrophoresis

Ioannis Kanakis

Biomedical Chromatography, 2006

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Cystic fibrosis liver disease - from diagnosis to risk factors

Liviu Tamas

Romanian journal of morphology and embryology = Revue roumaine de morphologie et embryologie, 2014

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Frequency of the ∆ ∆∆ ∆∆F508 Mutation in 108 Cystic Fibrosis Patients in São Paulo: Comparison with Reported Brazilian Data

Thelma Okay

Clinics, 2005

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Uniparental inheritance of microsatellite alleles of the cystic fibrosis gene ( CFTR ): identification of a 50 kilobase deletion

N. Cobos

Human Molecular Genetics, 1993

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Genotype-phenotype correlation in cystic fibrosis: The role of modifier genes

Olga Scudiero

American Journal of Medical Genetics, 2002

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Clinical expression of cystic fibrosis in a large cohort of Italian siblings

Arianna Bisogno

2018

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Association between Haplotypes and Specific Mutations in Swiss Cystic Fibrosis Families

Michael Morris

Pediatric Research, 1991

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