Double Aortic Arch Mimics the Clinical Characteristics of Severe Reactive Airway Disease in a Pediatric Patient (original) (raw)

Congenital airway anomaly of double aortic arch in a 2-day-old infant

Ear, nose, & throat journal

Double aortic vascular ring is a complete vascular ring that is formed when the distal portion of the right dorsal aorta fails to regress and the ascending aorta bifurcates to surround and compress both trachea and esophagus and rejoins to form the descending aorta.

Double aortic arch: a rare cause of wheezing and respiratory distress in infants: a case report

International Journal of Contemporary Pediatrics

Double aortic arch is a rare congenital disorder. Symptoms arises due to compression of trachea or esophagus. Its presentation varies from asymptomatic cases to life threatening respiratory distress. Clinical diagnosis is often difficult due to presence of wide verities of symptoms. We described a three-month-old child presented with wheezing and severe respiratory distress and found to have double aortic arch.

Three Cases of a Rare Association: Double Aortic Arch

International Journal of Pediatrics, 2016

Background Vascular ring is less than 1% of congenital heart disease. Double aortic arch (DAA) is the most common form of it. Its detecting is important because of the effects of pressure on the esophagus and trachea. Case Report In this study, three children suffering from double aortic arch with symptoms of dysphagia and recurrent aspiration, which in two cases had led to cardiac arrest, were introduced. In all of these studies, computed tomography angiography and chest X-ray were used to diagnose the compression effect of double aortic arch on the esophagus and the surgery provided for treatment of the children. After the surgery, all three patients were monitored in the intensive care unit (ICU) for five days without showing any symptoms. Conclusion Totally, we found that three computed tomography angiography, as a non invasive, high quality method, would be suitable for the diagnosis of this abnormality.

Double Aortic Arch in Adolescence

2015

Introduction: Double aortic arch (DAA) is the most frequently encountered vascular ring malfor-mation characterized by a complete encirclement of the trachea and esophagus by the aortic arch with a wide clinical spectrum. Objective: The aim of this study is to describe a case of DAA in ado-lesecents. Case Presentation: An 11-year-old boy was admitted for chronic productive cough which initially was diagnosed with pulmonary arterial hypertension. The final diagnosis was DAA which

Double Aortic Arch - a Case Report

Pakistan Armed Forces Medical Journal, 2021

Double Aortic Arch is a rare congenital cardiovascular anomaly. Its first successful surgery was performed by Robert Gross in 1945 at Children Hospital Boston, USA. It accounts for 0.4 to 1% of all congenital cardiac defects. Patients having a Double Aortic Arch mostly present with symptoms in the 1st week of life but depending upon the severity of symptoms can present at any age in childhood. We present a case report of two month old baby with noisy breathing, intermittent cough, gross jugular notch retraction and sub costal recession. His Cardiac CT was subsequently done which showed a Double Aortic Arch of left dominant variety encircling the trachea. Surgery was done and the encircling artery compressing the trachea was recognized, dissected and interrupted. Marked relief of tracheal and/or esophageal compression was evident from operation day. Post operative recovery was speedy. Patient’s follow up of was done at 1, 4 and 24 weeks. His recovery was unremarkable. Currently he wa...

Double Aortic Arch in Adolescence: A Case Report

Open Journal of Pediatrics, 2015

Introduction: Double aortic arch (DAA) is the most frequently encountered vascular ring malformation characterized by a complete encirclement of the trachea and esophagus by the aortic arch with a wide clinical spectrum. Objective: The aim of this study is to describe a case of DAA in adolesecents. Case Presentation: An 11-year-old boy was admitted for chronic productive cough which initially was diagnosed with pulmonary arterial hypertension. The final diagnosis was DAA which was established after chest computed tomography (CT) scan. Conclusion: Establishing a diagnosis of DAA in adolescents requires thorough understanding and clinical skills in performing diagnostic steps. The management of heart failure symptoms and other comorbidities is essential while preparing for its definite therapy.

Double aortic arch diagnosed in a 44-year-old woman with recurring respiratory infections

Respiratory medicine case reports, 2017

Complete vascular rings are originated because of the persistence of the fourth aortic arches, which surround the trachea and esophagus partially or completely, compressing them. The most common type of complete vascular ring is the double aortic arch. Symptoms usually appear in the first months of life, and are provoked by esophageal and tracheal compression. The diagnosis is usually made through the chest X-ray and the esophagogram in patients with dysphagia. We present a case in which the diagnosis of a double aortic arch was made in adulthood, suspected through a spirometry test and a chest X-ray.

Bifurcation-of-Aorta-A-Diagnostic-Challenge-and-Associated-Infectious-and-Congenital-Anomalies.pdf

Scholarena Journal of Case Reports, 2018

Double aortic arch is a rare cardiovascular anomaly. It represents about 61% of vascular rings, found in both gender equally, and results from persistence of the embryonic fourth arch. It is usually discovered at postmortem or at autopsy in the dissecting room. Most of the recorded cases had symptoms of constriction of the esophagus and tracheas, resulting in death from broncho-pneumonia at an early age, but sometimes patients with this condition have survived till adulthood. It must be considered if an infant presents with noisy breathing, persistent respiratory symptoms of infection, emesis, choking, and dysphagia or acute apneic spells. Here, we document a rare case, a 6-month-old male patient with a history of repeated admissions and referrals since birth. The characteristic complaints included attacks of respiratory distress, lower respiratory tract infections, stridor, feeding problems, vomiting, and sepsis. With a persistent right aortic arch that constricts esophagus and trachea, repeated infections, hypocalcemia, and umbilical hernia supporting 22q11 deletions disorder is being presented for the first time in Pakistan pediatric population.

Double vascular ring: a case report of double aortic arch and concurrent pulmonary artery sling

European Heart Journal - Case Reports, 2019

Background Double aortic arch (DAA) and pulmonary artery sling (PAS) are vascular ring formations that present in neonates and infants with symptoms of respiratory stenosis. Case summary The patient was a girl with suspected ventricular septal defect (VSD), right aortic arch (AA), left patent ductus arteriosus, and bilateral superior vena cava (SVC) on foetal echography in the first day of life. The girl was delivered at 40 weeks and 4 days of gestation. Ventricular septal defect, DAA, coarctation of the left AA, and bilateral SVC were diagnosed. Contrast-enhanced computed tomography at Day 16 revealed PAS with concurrent anomalous tracheal branching in addition to DAA. The right A2 segmental artery, which supplies the right upper pulmonary artery, showed abnormal branching from the left pulmonary artery (LPA). At 3 months of age, VSD patching, left AA resection distal to the root of the left subclavian artery, arterial ligament dissection, and LPA replacement were performed. Discus...

Double aortic arch presenting as severe bronchiolitis in a 2-week-old infant

Journal of Paediatrics and Child Health, 2005

A 2-week-old female infant was transferred from a regional hospital for mechanical ventilation after developing severe respiratory distress. Stridor had been present since the age of 1 week and was complicated by coryzal illness. Mechanical ventilation was difficult with marked inspiratory and expiratory flow obstruction recorded by the ventilator. Echocardiogram showed a normal heart. Flexible bronchoscopy revealed mid-tracheal extrinsic compression (unchanged with positive endexpiratory pressure) and advancement of the endotracheal tube by 2 cm completely corrected the flow obstruction. Repeat echocardiogram showed a double aortic arch. This case report emphasizes the importance of clinical history, examination findings and interpretation of the ventilator waveforms in the differential diagnosis of a difficult-to-ventilate infant with bronchiolitis.