Herniation Of The Left Atrial Appendage Due To Partial Congenital Absence Of The Left Pericardium (original) (raw)

Congenital Partial Pericardial Defect and Herniated Right Atrial Appendage: A Rare Anomaly

Echocardiography, 2006

A congenital partial defect of the right-sided pericardium is a rare cardiac anomaly and it represents defective formation of the pleuropericardial membrane. Patients can be asymptomatic, but they may experience chest pain, myocardial ischemia, emboli, arrhythmia, and sudden death. In this report, we present an 8-month-old boy with pericardial defect and right atrial appendage herniation. It was diagnosed by echocardiography and cardiac magnetic resonance imaging.

Congenital partial absence of the pericardium in a young man with atypical chest pain

World journal of cardiology, 2013

Pericardial defects are infrequent congenital anomalies due to agenesis caused by premature atrophy of the common cardinal vein or Cuvier duct during the 5(th) or 6(th) week of embryonic life. These congenital defects are rare, typically observed as an incidental finding and usually remain asymptomatic. Nevertheless, the more widespread use of modern imaging techniques has contributed to an increase of its incidence in recent years. There is currently no consensus regarding therapeutic options, all of which are based on small retrospective studies that evaluate the risk of developing a life-threatening complication such as herniation and incarceration of the myocardium. We report on a 22-year-old male who presented with sudden onset of sharp chest pain and dyspnea. Computed tomography and cardiac magnetic resonance scan revealed a pericardial defect adjacent to the lateral free wall of the left atrium with associated herniation of the left atrial appendage. The patient was managed c...

Congenital absence of left atrial appendage: A case report and literature review

Journal of the Saudi Heart Association, 2015

Congenital absence of left atrial appendage (LAA) is an extremely rare entity. A 50-year-old man with no past cardiac history was admitted with symptomatic atrial fibrillation (AF). Before subjecting him to direct current (DC) cardioversion, the patient underwent a transesophageal echocardiography (TEE) examination, but neither LAA nor a cardiac thrombus could be detected. Absence of both was confirmed by cardiac computer tomography (CT) and a cardiac magnetic resonance imaging (MRI) scan. The patient reverted to sinus rhythm with an uneventful synchronized biphasic DC shock of 100 joules.

Congenital left atrial appendage aneurysm with intact pericardium: Diagnosis by transesophageal echocardiography

American Heart Journal, 1990

Isolated congenital intrapericardial left atrial appendage aneurysm is an unusual anomaly.' Patients are often asymptomatic and are diagnosed incidentally,' but may present with embolization or supraventricular arrhythmia^.^-^ We report a case of left atrial appendage aneurysm with thrombus formation diagnosed by transesophageal echocardiography and confirmed at surgery. CASE REPORT A 66-year-old Chinese woman had suffered from paroxysmal palpitation off and on for more than 10 years, and exertional dyspnea for 4 years. She was referred for cardiac evaluation due to the unusual cardiac silhouette in a chest radiograph. The patient denied any past or present medical problems other than the above symptoms. Moreover, there were no specific past symptoms suggesting a thromboembolic phenomenon. After admission, the initial blood pressure was 140/90 mm Hg, and the pulse was 7Olmin and regular. The appearance of the patient was healthy. Physical examination was entirely normal, including the first and second heart sounds, jugular and carotid pulsations, lung fields, and neurological examinations. The 24-hour Holter electrocardiography showed paroxysmal atrial fibrillation. The chest roentgenogram was noted to have an abnormal bulging-out opacity in the left atrial region.

Complete Congenital Absence of the Left Pericardium in Elderly Patient: A Case Report

International medical case reports journal, 2024

Congenital pericardial absence is an uncommon heart condition that is usually undiagnosed due to a lack of symptoms and awareness. In this case study, we present a 72-year-old patient who initially presented for medical evaluation due to unexplained weight loss, a displaced cardiac apex, and poor echocardiographic windows. An extracardiac tumor was suspected at first, but it was later determined that the patient had a congenital complete absence of the left pericardium. This case illustrates the possibility for benign pathology to present abnormally and details the clinical features, imaging findings, and management of congenital absence of the pericardium.

Partial Congenital Absence of The Pericardium: A Case Report

Brazilian Journal of Cardiovascular Surgery

The complete or the partial absence of pericardium is a rare congenital malformation for which the patients are commonly asymptomatic and the diagnosis is incidental. The absence of the left side of the pericardium is the most common anomaly that is reported in the literature while the complete absence of pericardium or the absence of the right side of the pericardium are uncommon and their criteria are still unrecognized given their rare occurrence in clinical practice. This paper aims to report a case of 19-year-old male with the congenital partial absence of both sides of the pericardium and to highlight the symptoms and the different cardiac imaging modalities used to confirm the diagnosis of this defect.

Congenital complete and partial absence of the left pericardium

Wiener Medizinische Wochenschrift, 2013

Kongenitale komplete und partielle Absenz des Perikardiums Zusammenfassung Das kongenitale Fehlen des Perikards ist eine seltene Fehlbildung. Wir zeigen diese Diagnose anhand der Kasuistiken zweier junger Männer. Bei der posteroanterioren Röntgendarstellung der Brust wurde eine Verschiebung der linken Herzgrenze in den linken Hemitorax festgestellt. Ungewöhnliche akustische Fenster und abnormale Herz-und septale Bewegungen während der Echokardiographie wiesen auf die Diagnose der kongenitalen Absenz des Perikardiums hin. Die Magnetresonanzuntersuchungen bestätigten endgültig die Diagnose.