Idiopathic orbital inflammatory disease (original) (raw)
Idiopathic orbital inflammatory (IOI) disease refers to a marginated mass-like enhancing soft tissue involving any area of the orbit. It is the most common painful orbital mass in the adult population, and is associated with proptosis, cranial nerve palsy (Tolosa–Hunt syndrome), uveitis, and retinal detachment. Idiopathic orbital inflammatory syndrome, also known as orbital pseudotumor, was first described by Gleason in 1903 and by Busse and Hochheim. It was then characterized as a distinct entity in 1905 by Birch-Hirschfeld. It is a benign, nongranulomatous orbital inflammatory process characterized by extraocular orbital and adnexal inflammation with no known local or systemic cause. Its diagnosis is of exclusion once neoplasm, primary infection and systemic disorders have been ruled out
.jpg?width=300)
| Property | Value |
|---|---|
| dbo:abstract | Idiopathic orbital inflammatory (IOI) disease refers to a marginated mass-like enhancing soft tissue involving any area of the orbit. It is the most common painful orbital mass in the adult population, and is associated with proptosis, cranial nerve palsy (Tolosa–Hunt syndrome), uveitis, and retinal detachment. Idiopathic orbital inflammatory syndrome, also known as orbital pseudotumor, was first described by Gleason in 1903 and by Busse and Hochheim. It was then characterized as a distinct entity in 1905 by Birch-Hirschfeld. It is a benign, nongranulomatous orbital inflammatory process characterized by extraocular orbital and adnexal inflammation with no known local or systemic cause. Its diagnosis is of exclusion once neoplasm, primary infection and systemic disorders have been ruled out. Once diagnosed, it is characterized by its chronicity, anatomic location or histologic subtype. Idiopathic orbital inflammation has a varied clinical presentation depending on the involved tissue. It can range from a diffuse inflammatory process to a more localized inflammation of muscle, lacrimal gland or orbital fat. Its former name, orbital pseudotumor, is derived due to resemblance to a neoplasm. However, histologically it is characterized by inflammation. Although a benign condition, it may present with an aggressive clinical course with severe vision loss and oculomotor dysfunction. (en) La enfermedad inflamatoria orbital idiopática se refiere a un tejido blando reforzado similar a una masa marginada que involucra cualquier área de la órbita. Es la masa orbital dolorosa más común en la población adulta y está asociada con proptosis, parálisis del nervio craneal (síndrome de Tolosa-Hunt), uveítis y desprendimiento de retina. El síndrome inflamatorio orbital idiopático, también conocido como pseudotumor orbital, fue descrito por primera vez por Gleason en 1903 y por Busse y Hochhmein. Luego se caracterizó como una entidad distinta en 1905 por Birch-Hirschfeld. Es un proceso inflamatorio orbital no granulomatoso benigno que se caracteriza por una inflamación extraocular orbital y anexial sin causa local o sistémica conocida. Su diagnóstico es de exclusión una vez que se han descartado neoplasias, y trastornos . Una vez diagnosticado, se caracteriza por su cronicidad, ubicación anatómica o subtipo histológico. La inflamación orbitaria idiopática tiene una presentación clínica variada según el tejido afectado. Puede ir desde un proceso inflamatorio difuso hasta una inflamación más localizada del músculo, la glándula lagrimal o la . Su nombre anterior, pseudotumor orbital, se deriva debido a su parecido con una neoplasia. Sin embargo, se caracteriza por inflamación. Aunque es una afección benigna, puede presentar un curso clínico agresivo con pérdida severa de la visión y disfunción oculomotora. (es) |
| dbo:synonym | Orbital pseudotumor |
| dbo:thumbnail | wiki-commons:Special:FilePath/Inflammatory_pseudotu...a_Case_176_(5601449638).jpg?width=300 |
| dbo:wikiPageID | 27738398 (xsd:integer) |
| dbo:wikiPageLength | 13636 (xsd:nonNegativeInteger) |
| dbo:wikiPageRevisionID | 1090718544 (xsd:integer) |
| dbo:wikiPageWikiLink | dbr:Carotid-cavernous_fistula dbr:Sarcoidosis dbr:Uveitis dbr:Cranial_nerve dbr:Graves'_ophthalmopathy dbr:Orbital_cellulitis dbr:IgG4-related_ophthalmic_disease dbc:IgG4-related_disease dbr:Granulomatosis_with_polyangiitis dbr:Retinal_detachment dbr:Proptosis dbc:Eye_diseases dbr:Tolosa–Hunt_syndrome dbr:Extraocular_muscles dbr:Wikt:palsy |
| dbp:caption | In this area there is a predominance of large histiocytes admixed with plasma cells. (en) |
| dbp:imageSize | 250 (xsd:integer) |
| dbp:synonym | Orbital pseudotumor (en) |
| dbp:wikiPageUsesTemplate | dbt:Citation_needed dbt:Infobox_medical_condition_(new) dbt:Reflist |
| dct:subject | dbc:IgG4-related_disease dbc:Eye_diseases |
| rdf:type | owl:Thing wikidata:Q12136 dbo:Disease |
| rdfs:comment | Idiopathic orbital inflammatory (IOI) disease refers to a marginated mass-like enhancing soft tissue involving any area of the orbit. It is the most common painful orbital mass in the adult population, and is associated with proptosis, cranial nerve palsy (Tolosa–Hunt syndrome), uveitis, and retinal detachment. Idiopathic orbital inflammatory syndrome, also known as orbital pseudotumor, was first described by Gleason in 1903 and by Busse and Hochheim. It was then characterized as a distinct entity in 1905 by Birch-Hirschfeld. It is a benign, nongranulomatous orbital inflammatory process characterized by extraocular orbital and adnexal inflammation with no known local or systemic cause. Its diagnosis is of exclusion once neoplasm, primary infection and systemic disorders have been ruled out (en) La enfermedad inflamatoria orbital idiopática se refiere a un tejido blando reforzado similar a una masa marginada que involucra cualquier área de la órbita. Es la masa orbital dolorosa más común en la población adulta y está asociada con proptosis, parálisis del nervio craneal (síndrome de Tolosa-Hunt), uveítis y desprendimiento de retina. El síndrome inflamatorio orbital idiopático, también conocido como pseudotumor orbital, fue descrito por primera vez por Gleason en 1903 y por Busse y Hochhmein. Luego se caracterizó como una entidad distinta en 1905 por Birch-Hirschfeld. Es un proceso inflamatorio orbital no granulomatoso benigno que se caracteriza por una inflamación extraocular orbital y anexial sin causa local o sistémica conocida. Su diagnóstico es de exclusión una vez que se han d (es) |
| rdfs:label | Inflamación orbital idiopática (es) Idiopathic orbital inflammatory disease (en) |
| owl:sameAs | freebase:Idiopathic orbital inflammatory disease wikidata:Idiopathic orbital inflammatory disease dbpedia-es:Idiopathic orbital inflammatory disease http://tt.dbpedia.org/resource/Орбитаның_идиопатияле_ялкынсынуы https://global.dbpedia.org/id/4nevc |
| prov:wasDerivedFrom | wikipedia-en:Idiopathic_orbital_inflammatory_disease?oldid=1090718544&ns=0 |
| foaf:depiction | wiki-commons:Special:FilePath/Inflammatory_pseudotu...l_granuloma_Case_176_(5601449638).jpg |
| foaf:isPrimaryTopicOf | wikipedia-en:Idiopathic_orbital_inflammatory_disease |
| is dbo:wikiPageDisambiguates of | dbr:IOI |
| is dbo:wikiPageRedirects of | dbr:Idiopathic_Orbital_Inflammatory_Disease dbr:Orbital_pseudotumor |
| is dbo:wikiPageWikiLink of | dbr:Orbital_cellulitis dbr:IgG4-related_disease dbr:IgG4-related_ophthalmic_disease dbr:POEMS_syndrome dbr:Idiopathic_Orbital_Inflammatory_Disease dbr:IOI dbr:Exophthalmos dbr:Exposure_keratopathy dbr:Orbital_pseudotumor |
| is foaf:primaryTopic of | wikipedia-en:Idiopathic_orbital_inflammatory_disease |
