Harun Peru - Academia.edu (original) (raw)

Papers by Harun Peru

Research paper thumbnail of Development and validation of juvenile autoinflammatory disease multidimensional assessment report (JAIMAR)

Pediatric Rheumatology, 2014

Research paper thumbnail of Successful management of antiGBM disease in a 5½-year-old girl

Research paper thumbnail of Cardiac troponin-I in the serum of infants of diabetic mothers

Cardiology in the young, 2003

A transient form of hypertrophic cardiomyopathy has been previously described in infants of diabe... more A transient form of hypertrophic cardiomyopathy has been previously described in infants of diabetic mothers. When it occurs, it is generally benign. The purpose of our study was to establish the extent of injury to the cardiomyocytes in symptomatic and asymptomatic patients with and without hypertrophic cardiomyopathy. Thus, we compared 35 consecutive patients to 20 healthy controls, establishing the significance, if any, of differences in cardiac troponin-I and creatine kinase, including its MB-fraction, and seeking to establish the value of these parameters in the diagnosis of cardiac injury. We also determined to levels of glucose and insulin in the serum, and took note of electrocardiographic and echocardiographic investigations. Values were determined at the 1st and 7th days after admission in the patients, while parameters were measured in the control group only on the first day. We found that the levels of cardiac troponin-I in the serum, known to be a marker for cardiac inj...

Research paper thumbnail of HLA class 1 associations in Henoch Schonlein purpura: increased and decreased frequencies

Research paper thumbnail of An Unusual Association between Familial Mediterranean Fever and IgM Nephropathy

Medical Principles and Practice, 2008

To report a case with the diagnosis of IgM nephropathy and familial Mediterranean fever (FMF). A ... more To report a case with the diagnosis of IgM nephropathy and familial Mediterranean fever (FMF). A 9-year-old boy was admitted to our hospital with recurrent abdominal pain since the age of 4 years. Laboratory investigations revealed a sedimentation rate of 88 mm/h, C-reactive protein: 83.2 mg/l (0-10 mg/l), white blood cell count: 12,700/mm(3), fibrinogen: 622 mg/dl (200-400 mg/dl) and serum amyloid A: 186 mg/l (0-5.8 mg/l). Urinalysis revealed +2 proteinuria. A 24-hour urinary protein excretion was 12 mg/m(2)/h. M694V homozygous mutation was identified in exon 10. Percutaneous renal biopsy showed mesangial cell proliferation and increased mesangial matrix in the glomeruli, without amyloid accumulation. Immunofluorescence study showed IgM (+1) and C1q (+1) deposits. Treatment with 1 mg/day colchicine was started. Six weeks later, proteinuria had disappeared and the patient was asymptomatic. This case illustrates the unusual association of FMF with non-amyloid glomerulopathy. Glomerular diseases such as IgM nephropathy may be seen as a manifestation of FMF.

Research paper thumbnail of Henoch-Schönlein Nephritis: A Nationwide Study

Nephron Clinical Practice, 2009

The aim of this retrospective study was to evaluate the presentation, clinical and pathological m... more The aim of this retrospective study was to evaluate the presentation, clinical and pathological manifestations and outcome of the Henoch-Schönlein purpura (HSP) nephritis in children. Clinical and laboratory data of 443 children with HSP nephritis aged between 3 and 16 years from 16 pediatric nephrology reference centers were analyzed retrospectively. The biopsy findings were graded according to the classification developed by the International Study of Kidney Disease in Children (ISKDC). Renal biopsy was performed in 179 of the patients with HSP nephritis. The most common presenting clinical finding in patients who were biopsied was nephrotic range proteinuria (25%) which was followed by nephritic-nephrotic syndrome (23.5%). The biopsy findings according to the ISKDC were as follows: class I: 8.3%; II: 44.1%; III: 36.3%; IV: 6.7%; V: 3.3%; VI: 1.1%. All of the patients who developed end-stage renal disease had nephritic-nephrotic syndrome at presentation. Of 443 patients, 87.2% had a favorable outcome and 12.8% had an unfavorable outcome. The overall percentage of children who developed end-stage renal disease at follow-up was 1.1%. Logistic regression analysis did not show any association of initial symptoms and histology with outcome. In the presented cohort, the presence of crescents in the first biopsy or presenting clinical findings did not seem to predict the outcome of HSP nephritis in children. We conclude that children with HSP nephritis even with isolated microscopic hematuria and/or mild proteinuria should be followed closely.

Research paper thumbnail of Adiponectin levels and arteriosclerotic risk factors in pediatric renal transplant recipients

Pediatric Transplantation, 2006

Research paper thumbnail of Clinical and demographic characteristics of children with familial mediterranean fever in Central Anatolia

Pediatric Rheumatology, 2011

Research paper thumbnail of Familial hypomagnesemia with hypercalciuria and nephrocalcinosis: report of three Turkish siblings

Pediatric Nephrology, 2008

Research paper thumbnail of Etiology and outcome of acute kidney injury in children

Pediatric Nephrology, 2010

The aim of this prospective, multicenter study was to define the etiology and clinical features o... more The aim of this prospective, multicenter study was to define the etiology and clinical features of acute kidney injury (AKI) in a pediatric patient cohort and to determine prognostic factors. Pediatric-modified RIFLE (pRIFLE) criteria were used to classify AKI. The patient cohort comprised 472 pediatric patients (264 males, 208 females), of whom 32.6% were newborns (median age 3 days, range 1-24 days), and 67.4% were children aged >1 month (median 2.99 years, range 1 month-18 years). The most common medical conditions were prematurity (42.2%) and congenital heart disease (CHD, 11.7%) in newborns, and malignancy (12.9%) and CHD (12.3%) in children aged >1 month. Hypoxic/ischemic injury and sepsis were the leading causes of AKI in both age groups. Dialysis was performed in 30.3% of newborns and 33.6% of children aged >1 month. Mortality was higher in the newborns (42.6 vs. 27.9%; p < 0.005). Stepwise multiple regression analysis revealed the major independent risk factors to be mechanical ventilation [relative risk (RR) 17.31, 95% confidence interval (95% CI) 4.88-61.42], hypervolemia (RR 12.90, 95% CI 1.97-84.37), CHD (RR 9.85, 95% CI 2.08-46.60), and metabolic acidosis (RR 7.64, 95% CI 2.90-20.15) in newborns and mechanical ventilation (RR 8.73, 95% CI 3.95-19.29), hypoxia (RR 5.35, 95% CI 2.26-12.67), and intrinsic AKI (RR 4.91, 95% CI 2.04-11.78) in children aged >1 month.

Research paper thumbnail of CTLA-4 +49 A/G genotype and HLA-DRB1 polymorphisms in Turkish patients with Henoch–Schönlein purpura

Pediatric Nephrology, 2008

Research paper thumbnail of Chronic kidney disease in children in Turkey

Pediatric Nephrology, 2009

Research paper thumbnail of High serum adiponectin levels during steroid-responsive nephrotic syndrome relapse

Pediatric Nephrology, 2005

Research paper thumbnail of Leptin and resistin levels and their relationships with glucose metabolism in children with chronic renal insufficiency and undergoing dialysis

Research paper thumbnail of Ureteroscopic Stone Treatment in Preschool Children

Journal of Pediatric Urology, 2010

Research paper thumbnail of The relationship between urinary tract infections and vesicoureteral reflux in Turkish children

International Urology and Nephrology, 2009

Research paper thumbnail of Sulphasalazine treatment in protracted familial Mediterranean fever arthritis

European Journal of Pediatrics, 2009

Familial Mediterranean fever (FMF) is an autosomal recessive disease characterized by self-limite... more Familial Mediterranean fever (FMF) is an autosomal recessive disease characterized by self-limited attacks of fever and polyserositis. Articular involvement in early-onset FMF is a common finding characterized by non-erosive, generally asymmetric monoarthritis in large joints. Protracted FMF arthritis was reported in 2.6% of Turkish patients. An 8-year-old female who has a history of FMF for 5 years applied to our hospital with complaints of persistent swelling and pain of her left knee for 8 months. The patient had been tried to be managed with non-steroidal anti-inflammatory drugs as well as intra-articulary steroids and colchicine. However, arthritis and acute phase response persisted. With sulphasalazine, complete recovery was achieved. It is our belief that sulphasalazine can be a choice of medical treatment in protracted FMF arthritis.

Research paper thumbnail of Henoch Schonlein purpura in childhood: clinical analysis of 254 cases over a 3-year period

Clinical Rheumatology, 2008

We aimed to evaluate the patients who were diagnosed as Henoch Schonlein purpura (HSP) for diseas... more We aimed to evaluate the patients who were diagnosed as Henoch Schonlein purpura (HSP) for disease characteristics and prognosis of those with joint, gastrointestinal (GI), and renal involvement. Two hundred and fifty-four children who were followed up with the diagnosis of HSP in the Pediatric Nephrology Clinics of Meram Medical Faculty of Selcuk University and Medical Faculty of Gazi University between January 2003 and June 2006 were retrospectively evaluated. The clinical follow-up and treatment regimens of patients in whom renal biopsy was performed were evaluated in detail. The study group consisted of 254 children, 147 boys (57.8%) and 107 girls (42.2%), and the ratio of boys to girls was 1.37. The percentages of skin, joint, GI, and renal manifestations were 100%, 66%, 56%, and 30%, respectively. Eight patients had intussusception. Five of them recovered with steroid treatment only while three patients were operated on. Sixty-four patients (44%) with GI involvement had severe disease and were successfully treated with steroids. Renal biopsy was performed in 26 patients. Among those 26 patients, two of them recovered spontaneously within 3 and 4 weeks. Ten patients improved with only steroid treatment while 12 patients recovered with steroid and cyclophosphamide treatment. Two patients were resistant to steroid and cyclophosphamide treatment and were treated with cyclosporine A. We believe that steroid therapy given to the HSP patients with GI manifestations might be helpful to prevent probable complications such as GI bleeding and intussusception. In addition, combined therapy with steroid and cyclophosphamide can usually be an appropriate treatment for patients with nephrotic proteinuria.

Research paper thumbnail of HLA class 1 associations in Henoch Schonlein purpura: increased and decreased frequencies

Clinical Rheumatology, 2007

Research paper thumbnail of The evaluation of carotid intima-media thickness in children with familial Mediterranean fever

Clinical Rheumatology, 2008

Research paper thumbnail of Development and validation of juvenile autoinflammatory disease multidimensional assessment report (JAIMAR)

Pediatric Rheumatology, 2014

Research paper thumbnail of Successful management of antiGBM disease in a 5½-year-old girl

Research paper thumbnail of Cardiac troponin-I in the serum of infants of diabetic mothers

Cardiology in the young, 2003

A transient form of hypertrophic cardiomyopathy has been previously described in infants of diabe... more A transient form of hypertrophic cardiomyopathy has been previously described in infants of diabetic mothers. When it occurs, it is generally benign. The purpose of our study was to establish the extent of injury to the cardiomyocytes in symptomatic and asymptomatic patients with and without hypertrophic cardiomyopathy. Thus, we compared 35 consecutive patients to 20 healthy controls, establishing the significance, if any, of differences in cardiac troponin-I and creatine kinase, including its MB-fraction, and seeking to establish the value of these parameters in the diagnosis of cardiac injury. We also determined to levels of glucose and insulin in the serum, and took note of electrocardiographic and echocardiographic investigations. Values were determined at the 1st and 7th days after admission in the patients, while parameters were measured in the control group only on the first day. We found that the levels of cardiac troponin-I in the serum, known to be a marker for cardiac inj...

Research paper thumbnail of HLA class 1 associations in Henoch Schonlein purpura: increased and decreased frequencies

Research paper thumbnail of An Unusual Association between Familial Mediterranean Fever and IgM Nephropathy

Medical Principles and Practice, 2008

To report a case with the diagnosis of IgM nephropathy and familial Mediterranean fever (FMF). A ... more To report a case with the diagnosis of IgM nephropathy and familial Mediterranean fever (FMF). A 9-year-old boy was admitted to our hospital with recurrent abdominal pain since the age of 4 years. Laboratory investigations revealed a sedimentation rate of 88 mm/h, C-reactive protein: 83.2 mg/l (0-10 mg/l), white blood cell count: 12,700/mm(3), fibrinogen: 622 mg/dl (200-400 mg/dl) and serum amyloid A: 186 mg/l (0-5.8 mg/l). Urinalysis revealed +2 proteinuria. A 24-hour urinary protein excretion was 12 mg/m(2)/h. M694V homozygous mutation was identified in exon 10. Percutaneous renal biopsy showed mesangial cell proliferation and increased mesangial matrix in the glomeruli, without amyloid accumulation. Immunofluorescence study showed IgM (+1) and C1q (+1) deposits. Treatment with 1 mg/day colchicine was started. Six weeks later, proteinuria had disappeared and the patient was asymptomatic. This case illustrates the unusual association of FMF with non-amyloid glomerulopathy. Glomerular diseases such as IgM nephropathy may be seen as a manifestation of FMF.

Research paper thumbnail of Henoch-Schönlein Nephritis: A Nationwide Study

Nephron Clinical Practice, 2009

The aim of this retrospective study was to evaluate the presentation, clinical and pathological m... more The aim of this retrospective study was to evaluate the presentation, clinical and pathological manifestations and outcome of the Henoch-Schönlein purpura (HSP) nephritis in children. Clinical and laboratory data of 443 children with HSP nephritis aged between 3 and 16 years from 16 pediatric nephrology reference centers were analyzed retrospectively. The biopsy findings were graded according to the classification developed by the International Study of Kidney Disease in Children (ISKDC). Renal biopsy was performed in 179 of the patients with HSP nephritis. The most common presenting clinical finding in patients who were biopsied was nephrotic range proteinuria (25%) which was followed by nephritic-nephrotic syndrome (23.5%). The biopsy findings according to the ISKDC were as follows: class I: 8.3%; II: 44.1%; III: 36.3%; IV: 6.7%; V: 3.3%; VI: 1.1%. All of the patients who developed end-stage renal disease had nephritic-nephrotic syndrome at presentation. Of 443 patients, 87.2% had a favorable outcome and 12.8% had an unfavorable outcome. The overall percentage of children who developed end-stage renal disease at follow-up was 1.1%. Logistic regression analysis did not show any association of initial symptoms and histology with outcome. In the presented cohort, the presence of crescents in the first biopsy or presenting clinical findings did not seem to predict the outcome of HSP nephritis in children. We conclude that children with HSP nephritis even with isolated microscopic hematuria and/or mild proteinuria should be followed closely.

Research paper thumbnail of Adiponectin levels and arteriosclerotic risk factors in pediatric renal transplant recipients

Pediatric Transplantation, 2006

Research paper thumbnail of Clinical and demographic characteristics of children with familial mediterranean fever in Central Anatolia

Pediatric Rheumatology, 2011

Research paper thumbnail of Familial hypomagnesemia with hypercalciuria and nephrocalcinosis: report of three Turkish siblings

Pediatric Nephrology, 2008

Research paper thumbnail of Etiology and outcome of acute kidney injury in children

Pediatric Nephrology, 2010

The aim of this prospective, multicenter study was to define the etiology and clinical features o... more The aim of this prospective, multicenter study was to define the etiology and clinical features of acute kidney injury (AKI) in a pediatric patient cohort and to determine prognostic factors. Pediatric-modified RIFLE (pRIFLE) criteria were used to classify AKI. The patient cohort comprised 472 pediatric patients (264 males, 208 females), of whom 32.6% were newborns (median age 3 days, range 1-24 days), and 67.4% were children aged >1 month (median 2.99 years, range 1 month-18 years). The most common medical conditions were prematurity (42.2%) and congenital heart disease (CHD, 11.7%) in newborns, and malignancy (12.9%) and CHD (12.3%) in children aged >1 month. Hypoxic/ischemic injury and sepsis were the leading causes of AKI in both age groups. Dialysis was performed in 30.3% of newborns and 33.6% of children aged >1 month. Mortality was higher in the newborns (42.6 vs. 27.9%; p < 0.005). Stepwise multiple regression analysis revealed the major independent risk factors to be mechanical ventilation [relative risk (RR) 17.31, 95% confidence interval (95% CI) 4.88-61.42], hypervolemia (RR 12.90, 95% CI 1.97-84.37), CHD (RR 9.85, 95% CI 2.08-46.60), and metabolic acidosis (RR 7.64, 95% CI 2.90-20.15) in newborns and mechanical ventilation (RR 8.73, 95% CI 3.95-19.29), hypoxia (RR 5.35, 95% CI 2.26-12.67), and intrinsic AKI (RR 4.91, 95% CI 2.04-11.78) in children aged >1 month.

Research paper thumbnail of CTLA-4 +49 A/G genotype and HLA-DRB1 polymorphisms in Turkish patients with Henoch–Schönlein purpura

Pediatric Nephrology, 2008

Research paper thumbnail of Chronic kidney disease in children in Turkey

Pediatric Nephrology, 2009

Research paper thumbnail of High serum adiponectin levels during steroid-responsive nephrotic syndrome relapse

Pediatric Nephrology, 2005

Research paper thumbnail of Leptin and resistin levels and their relationships with glucose metabolism in children with chronic renal insufficiency and undergoing dialysis

Research paper thumbnail of Ureteroscopic Stone Treatment in Preschool Children

Journal of Pediatric Urology, 2010

Research paper thumbnail of The relationship between urinary tract infections and vesicoureteral reflux in Turkish children

International Urology and Nephrology, 2009

Research paper thumbnail of Sulphasalazine treatment in protracted familial Mediterranean fever arthritis

European Journal of Pediatrics, 2009

Familial Mediterranean fever (FMF) is an autosomal recessive disease characterized by self-limite... more Familial Mediterranean fever (FMF) is an autosomal recessive disease characterized by self-limited attacks of fever and polyserositis. Articular involvement in early-onset FMF is a common finding characterized by non-erosive, generally asymmetric monoarthritis in large joints. Protracted FMF arthritis was reported in 2.6% of Turkish patients. An 8-year-old female who has a history of FMF for 5 years applied to our hospital with complaints of persistent swelling and pain of her left knee for 8 months. The patient had been tried to be managed with non-steroidal anti-inflammatory drugs as well as intra-articulary steroids and colchicine. However, arthritis and acute phase response persisted. With sulphasalazine, complete recovery was achieved. It is our belief that sulphasalazine can be a choice of medical treatment in protracted FMF arthritis.

Research paper thumbnail of Henoch Schonlein purpura in childhood: clinical analysis of 254 cases over a 3-year period

Clinical Rheumatology, 2008

We aimed to evaluate the patients who were diagnosed as Henoch Schonlein purpura (HSP) for diseas... more We aimed to evaluate the patients who were diagnosed as Henoch Schonlein purpura (HSP) for disease characteristics and prognosis of those with joint, gastrointestinal (GI), and renal involvement. Two hundred and fifty-four children who were followed up with the diagnosis of HSP in the Pediatric Nephrology Clinics of Meram Medical Faculty of Selcuk University and Medical Faculty of Gazi University between January 2003 and June 2006 were retrospectively evaluated. The clinical follow-up and treatment regimens of patients in whom renal biopsy was performed were evaluated in detail. The study group consisted of 254 children, 147 boys (57.8%) and 107 girls (42.2%), and the ratio of boys to girls was 1.37. The percentages of skin, joint, GI, and renal manifestations were 100%, 66%, 56%, and 30%, respectively. Eight patients had intussusception. Five of them recovered with steroid treatment only while three patients were operated on. Sixty-four patients (44%) with GI involvement had severe disease and were successfully treated with steroids. Renal biopsy was performed in 26 patients. Among those 26 patients, two of them recovered spontaneously within 3 and 4 weeks. Ten patients improved with only steroid treatment while 12 patients recovered with steroid and cyclophosphamide treatment. Two patients were resistant to steroid and cyclophosphamide treatment and were treated with cyclosporine A. We believe that steroid therapy given to the HSP patients with GI manifestations might be helpful to prevent probable complications such as GI bleeding and intussusception. In addition, combined therapy with steroid and cyclophosphamide can usually be an appropriate treatment for patients with nephrotic proteinuria.

Research paper thumbnail of HLA class 1 associations in Henoch Schonlein purpura: increased and decreased frequencies

Clinical Rheumatology, 2007

Research paper thumbnail of The evaluation of carotid intima-media thickness in children with familial Mediterranean fever

Clinical Rheumatology, 2008