Tendon Extracellular Matrix Remodeling and Defective Cell Polarization in the Presence of Collagen VI Mutations (original) (raw)

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[Collagen VI related myopathies. When to suspect, how to identify. The contribution of muscle magnetic resonance]

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Changes in Muscle Cell Metabolism and Mechanotransduction Are Associated with Myopathic Phenotype in a Mouse Model of Collagen VI Deficiency

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Collagen VI Status and Clinical Severity in Ullrich Congenital Muscular Dystrophy: Phenotype Analysis of 11 Families Linked to the COL6 Loci

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Collagen VI deficiency induces early onset myopathy in the mouse: an animal model for Bethlem myopathy

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