Chronic cardiomyopathy and weakness or acute coma in children with a defect in carnitine uptake (original) (raw)

Carnitine deficiency presenting as familial cardiomyopathy: A treatable defect in carnitine transport

Catherine Neill

The Journal of Pediatrics, 1982

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Impaired Skin Fibroblast Carnitine Uptake in Primary Systemic Carnitine Deficiency Manifested by Childhood Carnitine-Responsive Cardiomyopathy

Enrico Bertini

Pediatric Research, 1990

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Infantile primary carnitine deficiency: A severe cardiac presentation unresponsive to carnitine supplementation

Richard Emmanuel

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The Syndrome of Carnitine Deficiency: Morphological and Metabolic Correlations in Two Cases

Cesare Cerri

Canadian Journal of Neurological Sciences / Journal Canadien des Sciences Neurologiques, 1978

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A patient with lethal cardiomyopathy and a carnitine ? acylcarnitine translocase deficiency

Hugo Heymans

Journal of Inherited Metabolic Disease, 1995

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Primary carnitine deficiency is a life‐long disease

Tobias Bruning

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Carnitine Membrane Transporter Deficiency: A Rare Treatable Cause of Cardiomyopathy and Anemia

Aline Cano, C. Vianey-saban

Pediatric Cardiology, 2008

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Exclusive cardiac dysfunction in familial primary carnitine deficiency cases: a genotype-phenotype correlation

Georges Nemer

Clinical Genetics, 2007

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Carnitine deficiency with cardiomyopathy presenting as neonatal hydrops: Successful response to carnitine therapy

Gnat Daniella, Philippe Steenhout, Esther Vamos

Journal of Inherited Metabolic Disease, 1990

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Primary carnitine deficiency: novel mutations and insights into the cardiac phenotype

Mariam Arabi, Georges Nemer

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Carnitine deficiency-induced cardiomyopathy

Dennis Paulson

Molecular and cellular biochemistry, 1998

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Metabolic Studies of Carnitine in a Child with Propionic Acidemia

Charles Hoppel

Pediatric Research, 1989

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Primary carnitine deficiency dilated cardiomyopathy: 28years follow-up

Lee Bitton, Nicola Carano, Bertrand Tchana

International Journal of Cardiology, 2013

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Identification of Mutations and Evaluation of Cardiomyopathy in Turkish Patients with Primary Carnitine Deficiency

A. Tokatlı

JIMD Reports, 2011

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Maternal systemic primary carnitine deficiency uncovered by newborn screening: Clinical, biochemical, and molecular aspects

Fernando Scaglia

Genetics in Medicine, 2010

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Primary Carnitine Deficiency – A Rare Treatable Cause of Cardiomyopathy and Massive Hepatomegaly

Sunita Bijarnia

Indian Journal of Pediatrics, 2016

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Renal Handling of Carnitine in Secondary Carnitine Deficiency Disorders

William Treem

Pediatric Research, 1993

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The role of L-carnitine in nutritional status and echocardiographic parameters in idiopathic dilated cardiomyopathy in children

Marco Parana Parana

Jornal de Pediatria, 2005

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Carnitine-acylcarnitine carrier deficiency: identification of the molecular defect in a patient

Ferdinando Palmieri

Journal of inherited metabolic disease, 1998

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Diabetic Cardiomyopathy and Carnitine Deficiency

Douglas Schocken

Journal of Diabetes and its Complications, 1999

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Dietary-dependent carnitine deficiency as a causeof nonketotic hypoglycemia in an infant

Peggy Borum

The Journal of Pediatrics, 1981

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Carnitine-acylcarnitine translocase deficiency: case report and review of the literature

María Bueno, Isidro Vitoria, Jaime Dalmau

Acta Paediatrica, 2007

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Effect of carnitine supplementation on cardiac function in hemodialyzed children

Alpay Celiker

Pediatrics International, 1998

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Carnitine supplementation for treating people with inborn errors of metabolism

Zbys Fedorowicz

Protocols, 1996

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Familial carnitine transporter defect: A treatable cause of cardiomyopathy in children

Galen Breningstall

American Heart Journal, 2000

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Infantile lipid storage myopathy with nocturnal hypoventilation shows abnormal low-affinity muscle carnitine uptake in vitro

Corrado Angelini

Neuromuscular Disorders, 1999

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