Inhibitory effect of 3-hydroxyacyl-CoAs and other long-chain fatty acidβ-oxidation intermediates on mitochondrial oxidative phosphorylation
Jos Ruiter
Journal of Inherited Metabolic Disease, 1996
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A new, simple assay for long-chain acyl-CoA dehydrogenase in cultured skin fibroblasts using stable isotopes and GC-MS
Hugo Heymans
Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease, 1992
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Metabolic and Phenotypic Characterization of Human Skin Fibroblasts After Forcing Oxidative Capacity
Cláudia Deus
Toxicological sciences : an official journal of the Society of Toxicology, 2018
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Evaluation of metabolic pathway activity in cultured skin fibroblasts and blood leukocytes
Rima Rozen
Clinica Chimica Acta, 1977
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Acyl-CoA: dihydroxyacetone phosphate acyltransferase in human skin fibroblasts: study of its properties using a new assay method
rob ofman
Biochimica Et Biophysica Acta (bba) - Lipids and Lipid Metabolism, 1986
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The Oxidation of Fatty Acids by Rabbit Reticulocytes and Their Isolated Mitochondria
Frank Gellerich
European Journal of Biochemistry, 1972
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Effects of odd-numbered medium-chain fatty acids on the accumulation of long-chain 3-hydroxy-fatty acids in long-chain L-3-hydroxyacyl CoA dehydrogenase and mitochondrial trifunctional protein deficient skin fibroblasts
Yasmeen Butt
Molecular Genetics and Metabolism, 2004
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Mitochondrial and metabolic remodeling in human skin fibroblasts in response to glucose availability
Cláudia Deus
2021
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Metabolism of saturated and polyunsaturated very-long-chain fatty acids in fibroblasts from patients with defects in peroxisomal β-oxidation
Jackie Street
Biochemical Journal, 1990
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Accumulation of 3-Hydroxy-Fatty Acids in the Culture Medium of Long-Chain l-3-Hydroxyacyl CoA Dehydrogenase (LCHAD) and Mitochondrial Trifunctional Protein-Deficient Skin Fibroblasts: Implications for Medium Chain Triglyceride Dietary Treatment of LCHAD Deficiency
Yasmeen Butt
Pediatric Research, 2003
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Medium-chain fatty acids undergo elongation before �-oxidation in fibroblasts
Yasmeen Butt
Biochem Biophys Res Commun, 2006
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Peroxisomal fatty acid beta-oxidation in relation to the accumulation of very long chain fatty acids in cultured skin fibroblasts from patients with Zellweger syndrome and other peroxisomal disorders
Carlo van Roermund
Journal of Clinical Investigation, 1987
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Very long chain fatty acids activate NADPH oxidase in human dermal fibroblasts
Milad Bitar
Cell Biochemistry and Function, 2004
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Regulation of the mitochondrial ATP-synthase in human fibroblasts
Anibh Das
Clinica Chimica Acta, 1994
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Measurement of peroxisomal fatty acid β-oxidation in cultured human skin fibroblasts
C. Roermund
Journal of Inherited Metabolic Disease, 1995
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Metabolism of saturated and polyunsaturated fatty acids by normal and Zellweger syndrome skin fibroblasts
Jackie Street
Biochemical Journal, 1989
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Medium-chain fatty acids undergo elongation before β-oxidation in fibroblasts
Yasmeen Butt
Biochemical and Biophysical Research Communications, 2006
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Analysis of fatty acid oxidation intermediates in cultured fibroblasts to detect mitochondrial oxidation disorders
morteza pourfarzam
Clinical Chemistry
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Polyunsaturated fatty acid accumulation in the lipids of cultured fibroblasts and smooth muscle cells
Victor Gavino
Journal of lipid …, 1981
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Measurement of short-chain acyl-CoA dehydrogenase (SCAD) in cultured skin fibroblasts with hexanoyl-CoA as a competitive inhibitor to eliminate the contribution of medium-chain acyl-CoA dehydrogenase
Hugo Heymans
Clinica Chimica Acta, 1994
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Inhibition of oxidative phosphorylation by palmitoyl-CoA in digitonin permeabilized fibroblasts: implications for long-chain fatty acid β-oxidation disorders
Jos Ruiter
Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease, 1995
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Identification of fatty acid oxidation disorder patients with lowered acyl-CoA thioesterase activity in human skin fibroblasts
rob ofman
European Journal of Clinical Investigation, 2005
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Raising plasma fatty acid concentration induces increased biogenesis of mitochondria in skeletal muscle
Pablo M Garcia-Roves
Proceedings of the National Academy of Sciences, 2007
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Effect of injected glucagon or fatty acids on mitochondrial ATPase
Belen Garrido
Archives of Biochemistry and Biophysics, 1984
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Correction of Fatty Acid Oxidation in Carnitine Palmitoyl Transferase 2–Deficient Cultured Skin Fibroblasts by Bezafibrate
Jean Bastin
Pediatric Research, 2003
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Analysis of organic acids after incubation with (16- 2 H 3 )palmitic acid in fibroblasts from patients with mitochondrial β-oxidation defects
Jose Henry Osorio
Journal of Inherited Metabolic Disease, 2000
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Metabolic fate of extracellular NAD in human skin fibroblasts
Giuseppe Pompucci
Journal of Cellular Biochemistry, 2001
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Impaired Mitochondrial Fatty Acid Oxidative Flux in Fibroblasts from a Patient with Malonyl-CoA Decarboxylase Deficiency
Michael Bennett
Molecular Genetics and Metabolism, 2001
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Peroxisomal Fatty Acid β-Oxidation in Relation to Adrenoleukodystrophy
C. Roermund
Developmental Neuroscience, 1991
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Fatty acid oxidation in peripheral blood cells: characterization and use for the diagnosis of defects of fatty acid oxidation
morteza pourfarzam
Pediatric …, 1995
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Effect of Ascorbic and Dehydroascorbic Acids on Lipid Composition of C 3 H/10T1/2 Cells
Victoria L. Ibric
Annals of the New York Academy of Sciences, 1987
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Genetic Deficiency of Medium-Chain Acyl Coenzyme A Dehydrogenase: Studies in Cultured Skin Fibroblasts and Peripheral Mononuclear Leukocytes
Barbara Corkey
Pediatric Research, 1985
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Metabolism of branched chain fatty acids in peroxisomal disorders
harinder singh
Journal of Inherited Metabolic Disease, 1990
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