Laboratory and genetic evaluation of Gaucher disease Labordiagnostik bei Morbus Gaucher (original) (raw)

Diagnosis of Lysosomal Storage Disorders: Gaucher Disease

Angela Dajnoki

Current Protocols in Human Genetics, 2001

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Pathogenesis of lysosomal storage disorders as illustrated by Gaucher disease

Sonja Van Weely

Journal of Inherited Metabolic Disease, 1993

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Identification and use of biomarkers in Gaucher disease and other lysosomal storage diseases

M. Maas

Acta Paediatrica, 2007

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Correlation among Genotype, Phenotype, and Biochemical Markers in Gaucher Disease: Implications for the Prediction of Disease Severity

Michael Fietz

Molecular Genetics and Metabolism, 2002

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First pilot newborn screening for four lysosomal storage diseases in an Italian region: identification and analysis of a putative causative mutation in the GBA gene

Camillo Rosano

Clinica chimica acta; international journal of clinical chemistry, 2012

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Clinico-hematological profile of lysosomal storage disorders — a report of three cases

Aparna Harbhajanka

Indian Journal of Hematology and Blood Transfusion, 2008

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Twenty- five years of biochemical diagnosis of Gaucher disease: the Egyptian experience

Dr. Zeinab Abdallah

Heliyon, 2019

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Biochemical properties of β-glucosidase in leukocytes from patients and obligated heterozygotes for Gaucher disease carriers

Roberto Giugliani

Clinica Chimica Acta, 2005

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Characterization of glucocerebrosidase in Greek Gaucher disease patients: mutation analysis and biochemical studies

Helen Michelakakis

Journal of Inherited Metabolic Disease, 1995

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Gaucher's disease: the changing paradigm of a lysosomal disorder

Atul Mehta

Medicina Clínica, 2011

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Gaucher’s disease is a common storage disorder but rare entity: Two case report

Kartavya Kumar Verma

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Genotype/phenotype relationship in Gaucher disease patients. Novel mutation in glucocerebrosidase gene

Paula Arévalo

Clinical Chemistry and Laboratory Medicine (CCLM), 2020

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Inherited Metabolic Disorders: Efficacy of Enzyme Assays on Dried Blood Spots for the Diagnosis of Lysosomal Storage Disorders

Jyotsna Verma

JIMD Reports, 2016

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Analysis of the glucocerebrosidase gene and mutation profile in 144 Italian gaucher patients

Mirella Filocamo, Stefano Regis, Fiorina Giona

Human Mutation, 2002

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Lysosomal storage disorders: Molecular basis and laboratory testing

Mirella Filocamo

Human Genomics, 2011

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Glucosidase acid beta gene mutations in Egyptian children with Gaucher disease and relation to disease phenotypes

Othman Soliman

World Journal of Pediatrics, 2011

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High Prevalence of the 55-bp Deletion (c.1263del55) in Exon 9 of the Glucocerebrosidase Gene Causing Misdiagnosis (for Homozygous N370S (c.1226A > G) Mutation) in Spanish Gaucher Disease Patients

Pilar Alfonso

Blood Cells, Molecules, and Diseases, 2002

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Decreased glucocerebrosidase activity in Gaucher disease parallels quantitative enzyme loss due to abnormal interaction with TCP1 and c-Cbl

Richard Hodes

Proceedings of the National Academy of Sciences, 2010

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Novel mutations in the glucocerebrosidase gene of Indian patients with Gaucher disease

Frenny Sheth

Journal of Human Genetics, 2014

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Novel Mutations in the Glucocerebrosidase Gene of Brazilian Patients with Gaucher Disease

MariaLuiza Saraiva-Pereira

JIMD Reports, 2012

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Genetic and clinical characteristics of Filipino patients with Gaucher disease

Mary Chiong

Molecular Genetics and Metabolism Reports, 2018

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Spectrum of lysosomal storage disorders at a medical genetics center in Northern India

Prajnya Ranganath

Indian Pediatrics, 2012

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Enzymic diagnosis in 27 cases with Gaucher's disease

Klaus Harzer

Clinica Chimica Acta, 1980

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Gaucher disease

Rafiu Ariganjoye

Neurosciences, 2015

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Clinical phenotype of Gaucher disease in relation to properties of mutant glucocerebrosidase in cultured fibroblasts

Ineke Jansen

Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease, 1991

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Neurological manifestations in Pakistani lysosomal storage disorders patients and molecular characterization of Gaucher disease

Sabika Firasat

Genetika, 2021

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