The first deletion mutation in the TSP1-6 repeat domain of ADAMTS13 in a family with inherited thrombotic thrombocytopenic purpura (original) (raw)

ADAMTS13 mutations and polymorphisms in congenital thrombotic thrombocytopenic purpura

Roberta Palla

Human Mutation, 2010

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Immune and Hereditary Thrombotic Thrombocytopenic Purpura: Can ADAMTS13 Deficiency Alone Explain the Different Clinical Phenotypes?

Raimondo De Cristofaro

Journal of Clinical Medicine

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Deficiency of ADAMTS13 and thrombotic thrombocytopenic purpura

HAN-MOU TSAI

Blood, 2002

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Novel ADAMTS-13 mutations in an adult with delayed onset thrombotic thrombocytopenic purpura

Lawrence Rice

Journal of Thrombosis and Haemostasis, 2006

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Mutations in a member of the ADAMTS gene family cause thrombotic thrombocytopenic purpura

Ravindra Sarode

Nature, 2001

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Two novel ADAMTS13 gene mutations in thrombotic thrombocytopenic purpura/hemolytic-uremic syndrome (TTP/HUS)

Thorsten Simon

Kidney International, 2004

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Congenital thrombotic thrombocytopenic purpura in association with a mutation in the second CUB domain of ADAMTS13

Louis Wadsworth

Blood, 2004

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A novel homozygous missense ADAMTS13 mutation Y658C in a patient with recurrent thrombotic thrombocytopenic purpura

/간호학과 이선희

Annals of clinical and laboratory science, 2011

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Thrombotic Thrombocytopenic Purpura: A Thrombotic Disorder Caused by ADAMTS13 Deficiency

P. Ormos

Hematology/Oncology Clinics of North America, 2007

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A novel homozygous frameshift mutation in Exon 7 of the ADAMTS13 gene in a patient with congenital thrombotic thrombocytopenic purpura from India: a case report

Bipin Kulkarni

Transfusion, 2017

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ADAMTS13 gene; a novel splicing site mutation in a case with thrombotic thrombocytopenic purpura

Behzad Zaker

Journal of Nephropharmacology

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Role of ADAMTS13 in the pathogenesis, diagnosis, and treatment of thrombotic thrombocytopenic purpura

Bernhard Lämmle

Hematology-American Society Hematology Education Program, 2012

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Complete deficiency in ADAMTS13 is prothrombotic, but it alone is not sufficient to cause thrombotic thrombocytopenic purpura

Toshiyuki Miyata

Blood, 2006

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Deficiency of ADAMTS13 causes thrombotic thrombocytopenic purpura. Editorial

HAN-MOU TSAI

Arteriosclerosis Thrombosis and Vascular Biology, 2003

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Prevalence of the ADAMTS-13 missense mutation R1060W in late onset adult thrombotic thrombocytopenic purpura

Richard Starke

Journal of Thrombosis and Haemostasis, 2008

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Deficiency of ADAMTS13 Causes Thrombotic Thrombocytopenic Purpura

HAN-MOU TSAI

2010

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Congenital Thrombotic Thrombocytopenic Purpura With a Novel ADAMTS13 Gene Mutation

Priscilla B Caguioa

Cureus

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ADAMTS13 phenotype in plasma from normal individuals and patients with thrombotic thrombocytopenic purpura

HAN-MOU TSAI

European Journal of Pediatrics, 2006

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A first case of congenital TTP on the African continent due to a new homozygous mutation in the catalytic domain of ADAMTS13

Johanna Kremer

Annals of Hematology, 2008

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ADAMTS13 Secretion and Residual Activity among Patients with Congenital Thrombotic Thrombocytopenic Purpura with and without Renal Impairment

Marina Noris

Clinical journal of the American Society of Nephrology : CJASN, 2015

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Diagnostic relevance of ADAMTS13 activity: Evaluation of 28 patients with thrombotic thrombocytopenic purpura - hemolytic uremic syndrome clinical diagnosis

Dragica Vucelić, Dragana Jevtic

Srpski arhiv za celokupno lekarstvo, 2013

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Gain-of-function ADAMTS13 variants that are resistant to autoantibodies against ADAMTS13 in patients with acquired thrombotic thrombocytopenic purpura

Long Zheng

Blood, 2012

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Fatal congenital thrombotic thrombocytopenic purpura with apparent ADAMTS13 inhibitor: in vitro inhibition of ADAMTS13 activity by hemoglobin

Bernhard Lämmle

Blood, 2005

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ADAMTS-13 assays in thrombotic thrombocytopenic purpura

Roberta Palla, I. Mackie

Journal of Thrombosis and Haemostasis, 2010

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Thrombotic thrombocytopenic purpura related to severe ADAMTS13 deficiency in children

C. Desconclois

Pediatric Nephrology, 2009

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Epitope mapping of ADAMTS13 autoantibodies in acquired thrombotic thrombocytopenic purpura

Bernhard Lämmle

Blood, 2004

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Unique case of autoantibody mediated inactivation of ADAMTS13 in an Indian TTP patient

Renu Saxena

Blood Cells Molecules and Diseases, 2019

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Children and adults with thrombotic thrombocytopenic purpura associated with severe, acquired Adamts13 deficiency: Comparison of incidence, demographic and clinical features

Johanna Kremer

Pediatric Blood & Cancer, 2013

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The International Hereditary Thrombotic Thrombocytopenic Purpura Registry: key findings at enrollment until 2017

Toshiyuki Miyata

Haematologica, 2019

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The novel ADAMTS13-p.D187H mutation impairs ADAMTS13 activity and secretion and contributes to thrombotic thrombocytopenic purpura in mice

hans deckmyn

Journal of thrombosis and haemostasis : JTH, 2014

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